487 research outputs found
Lateral Trunk Motion and Knee Pain in Osteoarthritis of the Knee: a cross-sectional study
- Author
- A Cappozzo
- A Mündermann
- A Mündermann
- A Mündermann
- CA McGibbon
- DE Hurwitz
- DG Kleinbaum
- Dirk L Knol
- GH Maassen
- J Harlaar
- JA Zeni Jr
- Jaap Harlaar
- JC Buckland-Wright
- JH Kellgren
- Joost Dekker
- Josien C van den Noort
- K Tanaka
- K Tanaka
- KL Bennell
- L Roorda
- M Esch van der
- M Van der Esch
- M Van der Esch
- M Van der Esch
- MA Hunt
- Martijn PM Steultjens
- Martin van der Esch
- MPM Steultjens
- N Doriot
- RD Altman
- RD Altman
- SD Lark
- SP Messier
- Publication venue
- BioMed Central
- Publication date
- 01/01/2011
- Field of study
<p>Abstract</p> <p>Background</p> <p>Patients with osteoarthritis of the knee may change their gait in an attempt to reduce loading of the affected knee, thereby reducing pain. Especially changes in lateral trunk motion may be potentially effective, since these will affect the position of the centre of mass relative to the knee, enabling minimization of the load on the knee and thereby knee pain. The aim of the study was to test the hypothesis that a higher level of knee pain is associated with higher lateral trunk motion in patients with knee OA.</p> <p>Methods</p> <p>Fifty-two patients with OA of the knee were tested. Lateral trunk motion was measured during the stance phase of walking with an optoelectronic motion analysis system and a force plate. Knee pain was measured with the VAS and the WOMAC pain questionnaire. Regression analyses were performed to assess the relationship between lateral trunk motion and knee pain.</p> <p>Results</p> <p>It was shown that in bivariate analyses knee pain was not associated with lateral trunk motion. In regression analyses, pain was associated with more lateral trunk motion. In addition, more lateral trunk motion was associated with younger age, being female, higher self-reported knee stiffness and higher maximum walking speed.</p> <p>Conclusion</p> <p>Pain is associated with lateral trunk motion. This association is weak and is influenced by age, gender, self-reported stiffness and maximum walking speed.</p
Prorenin anno 2008
- Author
- A Ichihara
- A Ichihara
- A. H. Jan Danser
- AHJ Danser
- AHJ Danser
- AHJ Danser
- AR Stankovic
- B Peters
- CA Burcklé
- CAM Kesteren van
- E Villard
- FHM Derkx
- G Nguyen
- G Prescott
- J Ménard
- JA Luetscher
- JH Schefe
- JHM Esch van
- JJ Saris
- JJ Saris
- JJ Saris
- Joep H. M. van Esch
- M Krop
- M Véniant
- Manne Krop
- MMED Eijnden van den
- T Lenz
- Wendy W. Batenburg
- WW Batenburg
- Y Huang
- Y Kaneshiro
- Y Kaneshiro
- Publication venue
- Springer-Verlag
- Publication date
- 01/01/2008
- Field of study
For many years, prorenin has been considered to be nothing more than the inactive precursor of renin. Yet, its elevated levels in diabetic subjects with microvascular complications and its extrarenal production at various sites in the body suggest otherwise. This review discusses the origin, regulation, and enzymatic activity of prorenin, its role during renin inhibition, and the angiotensin-dependent and angiotensin-independent consequences of its binding to the recently discovered (pro)renin receptor. The review ends with the concept that prorenin rather than renin determines tissue angiotensin generation
In Vivo Analysis of the Role of O-Glycosylations of Von Willebrand Factor
- Author
- A Kauskot
- A Varki
- A Varki
- B Obert
- B Plaimauer
- B Samor
- C Martin
- Caterina Casari
- Cecile V. Denis
- CJ van Schooten
- DD Wagner
- H Ulrichts
- HJ Weiss
- I Marx
- I Marx
- Idinath Badirou
- J Auwerx
- J Rayes
- JA Carew
- JA Davies
- Julie Rayes
- K Canis
- K Julenius
- K Titani
- KL Mohlke
- KS Sakariassen
- L Yang
- MA Cruz
- Marijke Bryckaert
- Mohamad Kurdi
- MS Chitta
- Olivier D. Christophe
- Paulette Legendre
- Peter J. Lenting
- PJ Lenting
- PL Turecek
- RD Palmiter
- Schulte am Esch J 2nd
- Stoddart JH Jr
- TA McKinnon
- TA McKinnon
- Toshiyuki Miyata
- TW Rademacher
- ZM Ruggeri
- Publication venue
- Public Library of Science
- Publication date
- 17/05/2012
- Field of study
The objective of this project was to study the function of O-glycosylations in von Willebrand factor (VWF) life cycle. In total, 14 different murine Vwf cDNAs mutated on one or several O-glycosylations sites were generated: 9 individual mutants, 2 doublets, 2 clusters and 1 mutant with all 9 murine glycosylation sites mutated (Del-O-Gly). We expressed each mutated cDNA in VWF deficient-mice by hydrodynamic injection. An immunosorbent assay with Peanut Agglutinin (PNA) was used to verify the O-glycosylation status. Wild-type (WT) VWF expressed by hepatocytes after hydrodynamic injection was able to bind PNA with slightly higher affinity than endothelial-derived VWF. In contrast, the Del-O-Gly VWF mutant did not bind PNA, demonstrating removal of O-linked glycans. All mutants displayed a normal multimeric pattern. Two mutants, Del-O-Gly and T1255A/T1256A, led to expression levels 50% lower than those induced by WT VWF and their half-life in vivo was significantly reduced. When testing the capacity of each mutant to correct the bleeding time of VWF-deficient mice, we found that S1486A, T1255A, T1256A and the doublet T1255A/T1256A were unable to do so. In conclusion we have shown that O-glycosylations are dispensable for normal VWF multimerization and biosynthesis. It also appears that some O-glycosylation sites, particularly the T1255 and T1256 residues, are involved in the maintenance of VWF plasma levels and are essential for normal haemostasis. As for the S1486 residue, it seems to be important for platelet binding as demonstrated in vitro using perfusion experiments
Observation of associated near-side and away-side long-range correlations in √sNN=5.02 TeV proton-lead collisions with the ATLAS detector
- Author
- Aad G
- Abajyan T
- Abbott B
- Abdallah J
- Abdel Khalek S
- Abdelalim AA
- Abdinov O
- Aben R
- Abi B
- Abolins M
- Abouzeid OS
- Abramowicz H
- Abreu H
- Acharya BS
- Adamczyk L
- Adams DL
- Addy TN
- Adelman J
- Adomeit S
- Adragna P
- Adye T
- Aefsky S
- Aguilar-Saavedra JA
- Agustoni M
- Ahlen SP
- Ahles F
- Ahmad A
- Ahsan M
- Aielli G
- Akesson TP
- Akimoto G
- Akimov AV
- Alam MA
- Albert J
- Albrand S
- Aleksa M
- Aleksandrov IN
- Alessandria F
- Alexa C
- Alexander G
- Alexandre G
- Alexopoulos T
- Alhroob M
- Aliev M
- Alimonti G
- Alison J
- Allbrooke BM
- Allison LJ
- Allport PP
- Allwood-Spiers SE
- Almond J
- Aloisio A
- Alon R
- Alonso A
- Alonso F
- Altheimer A
- Alvarez Gonzalez B
- Alviggi MG
- Amako K
- Amelung C
- Ammosov VV
- Amor Dos Santos SP
- Amorim A
- Amoroso S
- Amram N
- Anastopoulos C
- Ancu LS
- Andari N
- Andeen T
- Anders CF
- Anders G
- Anderson KJ
- Andreazza A
- Andrei V
- Anduaga XS
- Angelidakis S
- Anger P
- Angerami A
- Anghinolfi F
- Anisenkov A
- Anjos N
- Annovi A
- Antonaki A
- Antonelli M
- Antonov A
- Antos J
- Anulli F
- Aoki M
- Aperio Bella L
- Apolle R
- Arabidze G
- Aracena I
- Arai Y
- Arce AT
- Arfaoui S
- Arguin JF
- Argyropoulos S
- Arik E
- Arik M
- Armbruster AJ
- Arnaez O
- Arnal V
- Artamonov A
- Artoni G
- Arutinov D
- Asai S
- Ask S
- Asman B
- Asquith L
- Assamagan K
- Astalos R
- Astbury A
- Atkinson M
- ATLAS Collaboration The
- Auerbach B
- Auge E
- Augsten K
- Aurousseau M
- Avolio G
- Axen D
- Azuelos G
- Azuma Y
- Baak MA
- Baccaglioni G
- Bacci C
- Bach AM
- Bachacou H
- Bachas K
- Backes M
- Backhaus M
- Backus Mayes J
- Badescu E
- Bagnaia P
- Bai Y
- Bailey DC
- Bain T
- Baines JT
- Baker OK
- Baker S
- Balek P
- Balli F
- Banas E
- Banerjee P
- Banerjee S
- Banfi D
- Bangert A
- Bansal V
- Bansil HS
- Barak L
- Baranov SP
- Barber T
- Barberio EL
- Barberis D
- Barbero M
- Bardin DY
- Barillari T
- Barisonzi M
- Barklow T
- Barlow N
- Barnett BM
- Barnett RM
- Baroncelli A
- Barone G
- Barr AJ
- Barreiro Guimarães da Costa J
- Barreiro F
- Bartoldus R
- Barton AE
- Bartsch V
- Basye A
- Bates RL
- Batkova L
- Batley JR
- Battaglia A
- Battistin M
- Bauer F
- Bawa HS
- Beale S
- Beau T
- Beauchemin PH
- Beccherle R
- Bechtle P
- Beck HP
- Becker K
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- Beckingham M
- Becks KH
- Beddall A
- Beddall AJ
- Bedikian S
- Bednyakov VA
- Bee CP
- Beemster LJ
- Beermann TA
- Begel M
- Behar Harpaz S
- Belanger-Champagne C
- Bell PJ
- Bell WH
- Bella G
- Bellagamba L
- Bellomo M
- Belloni A
- Beloborodova O
- Belotskiy K
- Beltramello O
- Benary O
- Benchekroun D
- Bendtz K
- Benekos N
- Benhammou Y
- Benhar Noccioli E
- Benitez Garcia JA
- Benjamin DP
- Benoit M
- Bensinger JR
- Benslama K
- Bentvelsen S
- Berge D
- Bergeaas Kuutmann E
- Berger N
- Berghaus F
- Berglund E
- Beringer J
- Bernat P
- Bernhard R
- Bernius C
- Bernlochner FU
- Berry T
- Bertella C
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- Besana MI
- Besjes GJ
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- Blair RE
- Blanchard JB
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- Bloch I
- Blocker C
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- Blumenschein U
- Bobbink GJ
- Bobrovnikov VS
- Bocchetta SS
- Bocci A
- Boddy CR
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- Boldea V
- Bolnet NM
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- Borer C
- Borisov A
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- Borjanovic I
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- Buttar CM
- Butterworth JM
- Buttinger W
- Byszewski M
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- Cabrera Urbán S
- Caforio D
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- Calafiura P
- Calderini G
- Calfayan P
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- Caloba LP
- Caloi R
- Calvet D
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- Camacho Toro R
- Camarri P
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- Caminada LM
- Caminal Armadans R
- Campana S
- Campanelli M
- Canale V
- Canelli F
- Canepa A
- Cantero J
- Cantrill R
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- Capeans Garrido MD
- Caprini I
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- Castro NF
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- Chalupkova I
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- Chapman JD
- Chapman JW
- Charlton DG
- Chavda V
- Chavez Barajas CA
- Cheatham S
- Chekanov S
- Chekulaev SV
- Chelkov GA
- Chelstowska MA
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- Chernyatin V
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- Corriveau F
- Cortes-Gonzalez A
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- Cuthbert C
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- Czirr H
- Czodrowski P
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- Dearnaley WJ
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- Delemontex T
- Deliyergiyev M
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- Della Volpe D
- Delmastro M
- Delsart PA
- Deluca C
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- Demirkoz B
- Denisov SP
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- Derkaoui JE
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- Federic P
- Fedin OL
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- Fehling-Kaschek M
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- Ferreira de Lima DE
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- Ferretto Parodi A
- Fiascaris M
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- Filipčič A
- Filthaut F
- Fincke-Keeler M
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- Fitzgerald EA
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- Flowerdew MJ
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- Gagnon P
- Galea C
- Galhardo B
- Gallas EJ
- Gallo V
- Gallop BJ
- Gallus P
- Gan KK
- Gandrajula RP
- Gao YS
- Gaponenko A
- Garay Walls FM
- Garberson F
- Garcia-Sciveres M
- García Navarro JE
- García C
- Gardner RW
- Garelli N
- Garonne V
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- Gavrilenko IL
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- Gaycken G
- Gazis EN
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- Gemme C
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- Genest MH
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- Gershon A
- Geweniger C
- Ghazlane H
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- Giangiobbe V
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- Gillam TP
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- Gillman AR
- Gingrich DM
- Ginzburg J
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- Giordani MP
- Giordano R
- Giorgi FM
- Giovannini P
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- Gladilin LK
- Glasman C
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- Goddard JR
- Godfrey J
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- Goebel M
- Goeringer C
- Goldfarb S
- Golling T
- Golubkov D
- Gomes A
- Gomez Fajardo LS
- Goncalves Pinto Firmino Da Costa J
- Gonella L
- Gonzalez Parra G
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- Gonzalez-Sevilla S
- González de la Hoz S
- Gonçalo R
- Goodson JJ
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- Gorelov I
- Gorfine G
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- Goshaw AT
- Gostkin MI
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- Zevi Della Porta G
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- Publication venue
- American Physical Society
- Publication date
- 01/01/2012
- Field of study
Two-particle correlations in relative azimuthal angle (Δϕ) and pseudorapidity (Δη) are measured in √sNN=5.02 TeV p+Pb collisions using the ATLAS detector at the LHC. The measurements are performed using approximately 1 μb-1 of data as a function of transverse momentum (pT) and the transverse energy (ΣETPb) summed over 3.1<η<4.9 in the direction of the Pb beam. The correlation function, constructed from charged particles, exhibits a long-range (2<|Δη|<5) “near-side” (Δϕ∼0) correlation that grows rapidly with increasing ΣETPb. A long-range “away-side” (Δϕ∼π) correlation, obtained by subtracting the expected contributions from recoiling dijets and other sources estimated using events with small ΣETPb, is found to match the near-side correlation in magnitude, shape (in Δη and Δϕ) and ΣETPb dependence. The resultant Δϕ correlation is approximately symmetric about π/2, and is consistent with a dominant cos2Δϕ modulation for all ΣETPb ranges and particle pT
Measurement of the cross-section of high transverse momentum vector bosons reconstructed as single jets and studies of jet substructure in pp collisions at √s = 7 TeV with the ATLAS detector
- Author
- Aad G
- Abajyan T
- Abbott B
- Abdallah J
- Abdinov O
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- Publication venue
- 'IOP Publishing'
- Publication date
- 01/01/2014
- Field of study
This paper presents a measurement of the cross-section for high transverse momentum W and Z bosons produced in pp collisions and decaying to all-hadronic final states. The data used in the analysis were recorded by the ATLAS detector at the CERN Large Hadron Collider at a centre-of-mass energy of √s = 7 TeV;{\rm Te}{\rm V}andcorrespondtoanintegratedluminosityof4.6\;{\rm f}{{{\rm b}}^{-1}}.ThemeasurementisperformedbyreconstructingtheboostedWorZbosonsinsinglejets.ThereconstructedjetmassisusedtoidentifytheWandZbosons,andajetsubstructuremethodbasedonenergyclusterinformationinthejetcentre−of−massframeisusedtosuppressthelargemulti−jetbackground.Thecross−sectionforeventswithahadronicallydecayingWorZboson,withtransversemomentum{{p}_{{\rm T}}}\gt 320\;{\rm Ge}{\rm V}andpseudorapidity|\eta |\lt 1.9,ismeasuredtobe{{\sigma }_{W+Z}}=8.5\pm 1.7$ pb and is compared to next-to-leading-order calculations. The selected events are further used to study jet grooming techniques
Search for pair-produced long-lived neutral particles decaying to jets in the ATLAS hadronic calorimeter in ppcollisions at √s=8TeV
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- Sundermann JE
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- Swiatlowski M
- Sykora I
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- Takeshita T
- Takubo Y
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- Talyshev AA
- Tam JYC
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- Tannenwald BB
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- Teuscher RJ
- Therhaag J
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- Thomas JP
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- Thompson EN
- Thompson PD
- Thompson PD
- Thompson RJ
- Thomsen LA
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- Tibbetts MJ
- Tikhomirov VO
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- Trzebinski M
- Trzupek A
- Tsarouchas C
- Tseng JC-L
- Tsiareshka PV
- Tsionou D
- Tsipolitis G
- Tsirintanis N
- Tsiskaridze S
- Tsiskaridze V
- Tskhadadze EG
- Tsukerman I
- Tsulaia V
- Tsuno S
- Tsybychev D
- Tudorache A
- Tudorache V
- Tuna AN
- Tupputi SA
- Turchikhin S
- Turecek D
- Turra R
- Tuts PM
- Tykhonov A
- Tylmad M
- Tyndel M
- Uchida K
- Ueda I
- Ueno R
- Ughetto M
- Ugland M
- Uhlenbrock M
- Ukegawa F
- Unal G
- Undrus A
- Unel G
- Ungaro FC
- Unno Y
- Unverdorben C
- Urbaniec D
- Urquijo P
- Usai G
- Usanova A
- Vacavant L
- Vacek V
- Vachon B
- Valencic N
- Valentinetti S
- Valero A
- Valery L
- Valkar S
- Vallecorsa S
- Van Den Wollenberg W
- Van Der Deijl PC
- van der Geer R
- van der Graaf H
- Van Der Leeuw R
- van der Ster D
- Van Eldik N
- Van Gemmeren P
- van Huysduynen LH
- Van Nieuwkoop J
- van Vulpen I
- Van Woerden MC
- Vanadia M
- Vandelli W
- Vanguri R
- Vaniachine A
- Vankov P
- Vannucci F
- Vaque FV
- Vardanyan G
- Vari R
- Varnes EW
- Varol T
- Varouchas D
- Vartapetian A
- Varvell KE
- Vazeille F
- Vazquez JGP
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- Veloso F
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- Veneziano S
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- Venturi N
- Venturini A
- Vercesi V
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- Vermeulen JC
- Verzini MJA
- Vest A
- Vetterli MC
- Viazlo O
- Vichou I
- Vickey T
- Viehhauser GHA
- Viel S
- Vigne R
- Villa M
- Vilucchi E
- Vincter MG
- Vinogradov VB
- Virzi J
- Vivarelli I
- Vlachos S
- Vladoiu D
- Vlasak M
- Vogel A
- Vokac P
- Volpi G
- Volpi M
- von der Schmitt H
- von Radziewski H
- von Toerne E
- Vorobel V
- Vorobev K
- Vos M
- Voss R
- Vossebeld JH
- Vranjes N
- Vrba V
- Vreeswijk M
- Vuanh T
- Vuillermet R
- Vukotic I
- Vykydal Z
- Wagner P
- Wagner W
- Wahlberg H
- Wahrmund S
- Wakabayashi J
- Walder J
- Walker R
- Walkowiak W
- Wall R
- Waller P
- Walls FMG
- Walsh B
- Wang C
- Wang C
- Wang F
- Wang H
- Wang H
- Wang J
- Wang J
- Wang K
- Wang R
- Wang SM
- Wang T
- Wang X
- Wanotayaroj C
- Warburton A
- Ward CP
- Wardrope DR
- Warsinsky M
- Washbrook A
- Wasicki C
- Watkins PM
- Watson AT
- Watson IJ
- Watson MF
- Watts G
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- Waugh BM
- Webb S
- Weber MS
- Weber SW
- Webster JS
- Weidberg AR
- Weigell P
- Weinert B
- Weingarten J
- Weiser C
- Weits H
- Wells PS
- Wemans ADV
- Wenaus T
- Wendland D
- Weng Z
- Wengler T
- Wenig S
- Wermes N
- Werner M
- Werner P
- Wessels M
- Wetter J
- Whalen K
- White A
- White MJ
- White R
- White S
- Whiteson D
- Wicke D
- Wickens FJ
- Wiedenmann W
- Wielers M
- Wienemann P
- Wiglesworth C
- Wiik-Fuchs LAM
- Wijeratne PA
- Wildauer A
- Wildt MA
- Wilkens HG
- Will JZ
- Williams HH
- Williams S
- Willis C
- Willocq S
- Wilson A
- Wilson JA
- Wingerter-Seez I
- Winklmeier F
- Winter BT
- Wittgen M
- Wittig T
- Wittkowski J
- Wollstadt SJ
- Wolter MW
- Wolters H
- Wong KHY
- Wosiek BK
- Wotschack J
- Woudstra MJ
- Wozniak KW
- Wright M
- Wu M
- Wu SL
- Wu X
- Wu Y
- Wulf E
- Wyatt TR
- Wynne BM
- Xella S
- Xiao M
- Xu D
- Xu L
- Yabsley B
- Yacoob S
- Yakabe R
- Yamada M
- Yamaguchi H
- Yamaguchi Y
- Yamamoto A
- Yamamoto K
- Yamamoto S
- Yamamura T
- Yamanaka T
- Yamauchi K
- Yamazaki Y
- Yan Z
- Yang H
- Yang H
- Yang UK
- Yang Y
- Yanush S
- Yao L
- Yao W-M
- Yasu Y
- Yatsenko E
- Ye J
- Ye S
- Yeletskikh I
- Yen AL
- Yildirim E
- Yildiz HD
- Yilmaz M
- Yoosoofmiya R
- Yorita K
- Yoshida R
- Yoshihara K
- Young C
- Young CJS
- Youssef S
- Yu DR
- Yu J
- Yu J
- Yu JM
- Yuan L
- Yurkewicz A
- Yusuff I
- Zabinski B
- Zaidan R
- Zaitsev AM
- Zaman A
- Zambito S
- Zanello L
- Zanzi D
- Zeitnitz C
- Zeman M
- Zemla A
- Zengel K
- Zenin O
- Zenis T
- Zerwas D
- Zhang D
- Zhang F
- Zhang H
- Zhang J
- Zhang L
- Zhang X
- Zhang Z
- Zhao Z
- Zhemchugov A
- Zhong J
- Zhou B
- Zhou L
- Zhou N
- Zhu CG
- Zhu H
- Zhu J
- Zhu Y
- Zhuang X
- Zhukov K
- Zibell A
- Zieminska D
- Zimine NI
- Zimmermann C
- Zimmermann R
- Zimmermann S
- Zimmermann S
- Zinonos Z
- Ziolkowski M
- Zobernig G
- Zoccoli A
- zur Nedden M
- Zurzolo G
- Zutshi V
- Zwalinski L
- Publication venue
- 'Elsevier BV'
- Publication date
- 01/01/2014
- Field of study
The ATLAS detector at the Large Hadron Collider at CERN is used to search for the decay of a scalar boson to a pair of long-lived particles, neutral under the Standard Model gauge group, in 20.3fb−1of data collected in proton–proton collisions at √s=8TeV. This search is sensitive to long-lived particles that decay to Standard Model particles producing jets at the outer edge of the ATLAS electromagnetic calorimeter or inside the hadronic calorimeter. No significant excess of events is observed. Limits are reported on the product of the scalar boson production cross section times branching ratio into long-lived neutral particles as a function of the proper lifetime of the particles. Limits are reported for boson masses from 100 GeVto 900 GeV, and a long-lived neutral particle mass from 10 GeVto 150 GeV
De novo CCND2 mutations leading to stabilization of cyclin D2 cause megalencephaly-polymicrogyria-polydactyly-hydrocephalus syndrome
- Author
- A Kida
- A McKenna
- A Poduri
- A Pontious
- Andrew E Fry
- C Englund
- CA Schneider
- Carissa Adams
- Clare V Logan
- Colin A Johnson
- Dagmar Wieczorek
- Daniela T Pilz
- David A Parry
- David T Bonthron
- Eamonn G Sheridan
- Elizabeth Sweeney
- Ghayda M Mirzaa
- Grazia M S Mancini
- H Li
- H Li
- Hilde van Esch
- I Bystron
- Jacek Majewski
- JB Rivière
- Jean-Baptiste Rivière
- Jeremy Schwartzentruber
- JH Lee
- JM Huard
- Judith St-Onge
- K Wang
- Karen W Gripp
- Kees P J Braun
- Ki Pang
- Kristin A Giamanco
- Kym M Boycott
- L Baala
- Laurence Faivre
- M Elizabeth Ross
- M Nonaka-Kinoshita
- MA DePristo
- Megan Vanstone
- Michelle Steinraths
- MJ Lindhurst
- Nicola Roberts
- Nienke Verbeek
- P Cohen
- Rebecca D Hodge
- RF Hevner
- Robert F Hevner
- S Tokuda
- SB Glickstein
- SB Glickstein
- SB Glickstein
- Shawn Singh
- Stanislav S Kholmanskikh
- V Martínez-Cerdeño
- William B Dobyns
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- 01/01/2014
- Field of study
Activating mutations in genes encoding phosphatidylinositol 3-kinase (PI3K)-AKT pathway components cause megalencephaly-polymicrogyria-polydactyly-hydrocephalus syndrome (MPPH, OMIM 603387). Here we report that individuals with MPPH lacking upstream PI3K-AKT pathway mutations carry de novo mutations in CCND2 (encoding cyclin D2) that are clustered around a residue that can be phosphorylated by glycogen synthase kinase 3β (GSK-3β). Mutant CCND2 was resistant to proteasomal degradation in vitro compared to wild-type CCND2. The PI3K-AKT pathway modulates GSK-3β activity, and cells from individuals with PIK3CA, PIK3R2 or AKT3 mutations showed similar CCND2 accumulation. CCND2 was expressed at higher levels in brains of mouse embryos expressing activated AKT3. In utero electroporation of mutant CCND2 into embryonic mouse brains produced more proliferating transfected progenitors and a smaller fraction of progenitors exiting the cell cycle compared to cells electroporated with wild-type CCND2. These observations suggest that cyclin D2 stabilization, caused by CCND2 mutation or PI3K-AKT activation, is a unifying mechanism in PI3K-AKT–related megalencephaly syndromes
Is the relationship between increased knee muscle strength and improved physical function following exercise dependent on baseline physical function status?
- Author
- A Ruhdorfer
- AK Lange
- Ben R. Metcalf
- BT Maurer
- DC Sanchez-Ramirez
- EM Roos
- F Tubach
- Fiona Dobson
- GL Cheing
- J Knoop
- J Marszalet
- J Runhaar
- JE Broderick
- Jessica Kasza
- JH Kellgren
- JR Moreland
- Kim L. Bennell
- KL Bennell
- KL Bennell
- KR Baker
- L Fernandes
- M Rooij de
- Marike van der Leeden
- Martin van der Esch
- MH Jan
- Michelle Hall
- MJ Berger
- N Bellamy
- N Bellamy
- NE Foster
- Rana S. Hinman
- RD Altman
- RM Palmieri-Smith
- SP Messier
- ST Skou
- T Liikavainio
- TE McAlindon
- Tim V. Wrigley
- VB Kraus
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Development of a microfluidic confocal fluorescence detection system for the hyphenation of nano-LC to on-line biochemical assays
- Author
- A Fonseca
- AB Smit
- AG Hadd
- AJ Oosterkamp
- AR Boer de
- August B. Smit
- BJ Burke
- BM Johnson
- DA Annis
- DA Tatosian
- Dick van Iperen
- Ferry Heus
- G Hempel
- GE Kloe de
- Gerdien E. de Kloe
- Henk Lingeman
- Hubertus Irth
- Iwan J. P. de Esch
- J Kong
- J Kool
- J Kool
- J Kool
- Jeroen Kool
- JH Sung
- Joost Buijs
- KV Niessen
- L Yu
- M Eggink
- Martin Giera
- NH Schebb
- PA Auroux
- PH Celie
- RC Hogg
- RC Hogg
- S Dutertre
- S Gotz
- Tariq T. Nahar
- TD Laing
- V Kolivoska
- WB Du
- Wilfried M. A. Niessen
- Y Sun
- Publication venue
- Publication date
- 01/01/2010
- Field of study
One way to profile complex mixtures for receptor affinity is to couple liquid chromatography (LC) on-line to biochemical detection (BCD). A drawback of this hyphenated screening approach is the relatively high consumption of sample, receptor protein and (fluorescently labeled) tracer ligand. Here, we worked toward minimization of sample and reagent consumption, by coupling nano-LC on-line to a light-emitting diode (LED) based capillary confocal fluorescence detection system capable of on-line BCD with low-flow rates. In this fluorescence detection system, a capillary with an extended light path (bubble cell) was used as a detection cell in order to enhance sensitivity. The technology was applied to a fluorescent enhancement bioassay for the acetylcholine binding protein, a structural analog of the extracellular ligand-binding domain of neuronal nicotinic acetylcholine receptors. In the miniaturized setup, the sensitive and low void volume LED-induced confocal fluorescence detection system operated in flow injection analysis mode allowing the measurement of IC(50) values, which were comparable with those measured by a conventional plate reader bioassay. The current setup uses 50 nL as injection volume with a carrier flow rate of 400 nL/min. Finally, coupling of the detection system to gradient reversed-phase nano-LC allowed analysis of mixtures in order to identify the bioactive compounds present by injecting 10 nL of each mixture
Measurement of the transverse polarization of Λ and Λ¯ hyperons produced in proton-proton collisions at √s=7 TeV using the ATLAS detector
- Author
- Aad G
- Abbott B
- Abdallah J
- Abdinov O
- Aben R
- Abi B
- Abolins M
- AbouZeid OS
- Abramowicz H
- Abreu H
- Abreu R
- Abulaiti Y
- Acharya BS
- Adam ER
- Adamczyk L
- Adams DL
- Adelman J
- Adomeit S
- Adye T
- Agatonovic-Jovin T
- Aguilar-Saavedra JA
- Agustoni M
- Ahlen SP
- Ahmadov F
- Aielli G
- Akerstedt H
- Akesson TPA
- Akimoto G
- Akimov AV
- Alberghi GL
- Albert J
- Albrand S
- Aleksa M
- Aleksandrov IN
- Alexa C
- Alexander G
- Alexandre G
- Alexopoulos T
- Alhroob M
- Alimonti G
- Alio L
- Alison J
- Allbrooke BMM
- Allison LJ
- Allport PP
- Aloisio A
- Alonso A
- Alonso F
- Alpigiani C
- Altheimer A
- Alviggi MG
- Amako K
- Amaral Coutinho Y
- Amelung C
- Amidei D
- Amor Dos Santos SP
- Amorim A
- Amoroso S
- Amram N
- Amundsen G
- Anastopoulos C
- Ancu LS
- Andari N
- Andeen T
- Anders CF
- Anders G
- Anderson KJ
- Andreazza A
- Andrei V
- Anduaga XS
- Angelidakis S
- Angelozzi I
- Anger P
- Angerami A
- Anghinolfi F
- Anh TV
- Anisenkov AV
- Anjos N
- Annovi A
- Antonelli M
- Antonov A
- Antos J
- Anulli F
- Aoki M
- Arabidze G
- Arai Y
- Aranda CP
- Araque JP
- Arce ATH
- Arduh FA
- Arguin J-F
- Argyropoulos S
- Arik M
- Armbruster AJ
- Arnaez O
- Arnal V
- Arnold H
- Arratia M
- Arslan O
- Artamonov A
- Artoni G
- Asai S
- Asbah N
- Ashkenazi A
- Asman B
- Asquith L
- Assamagan K
- Astalos R
- Atkinson M
- Atlay NB
- Auerbach B
- Augsten K
- Aurousseau M
- Avolio G
- Axen B
- Azuelos G
- Azuma Y
- Baak MA
- Baas AE
- Bacci C
- Bachacou H
- Bachas K
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- Tsulaia V
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- Tsybychev D
- Tudorache A
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- Tuna AN
- Tupputi SA
- Turchikhin S
- Turecek D
- Turra R
- Turvey AJ
- Tuts PM
- Tykhonov A
- Tylmad M
- Tyndel M
- Ueda I
- Ueno R
- Ughetto M
- Ugland M
- Uhlenbrock M
- Ukegawa F
- Unal G
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- Urban J
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- Urquijo P
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- Usanova A
- Vacavant L
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- Vachon B
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- Van den Wollenberg W
- Van der Deijl PC
- Van der Geer R
- Van der Graaf H
- Van der Leeuw R
- Van der Ster D
- Van Eldik N
- Van Gemmeren P
- Van Huysduynen LH
- Van Nieuwkoop J
- Van Vulpen I
- Van Woerden MC
- Vanadia M
- Vandelli W
- Vanguri R
- Vaniachine A
- Vankov P
- Vannucci F
- Vaque FV
- Vardanyan G
- Vari R
- Varnes EW
- Varol T
- Varouchas D
- Vartapetian A
- Varvell KE
- Vazeille F
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- Veatch J
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- Vermeulen JC
- Verzini MJA
- Vest A
- Vetterli MC
- Viazlo O
- Vichou I
- Vickey T
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- Viel S
- Vigne R
- Villa M
- Vilucchi E
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- Vogel A
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- Von Toerne E
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- Vukotic I
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- Wagner P
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- Yao W-M
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- Yeletskikh I
- Yen AL
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- Yusuff I
- Zabinski B
- Zaidan R
- Zaitsev AM
- Zaman A
- Zambito S
- Zanello L
- Zanzi D
- Zeitnitz C
- Zeman M
- Zemla A
- Zengel K
- Zenin O
- Zenis T
- Zerwas D
- Zhang D
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- Zhemchugov A
- Zhong J
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- Zhuang X
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- Zibell A
- Zieminska D
- Zimine NI
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- Zurzolo G
- Zwalinski L
- Publication venue
- 'American Physical Society (APS)'
- Publication date
- 01/12/2014
- Field of study
The transverse polarization of Λ and Λ¯ hyperons produced in proton-proton collisions at a center-of-mass energy of 7 TeV is measured. The analysis uses 760 μb−1 of minimum bias data collected by the ATLAS detector at the LHC in the year 2010. The measured transverse polarization averaged over Feynman xF from 5×10−5 to 0.01 and transverse momentum pT from 0.8 to 15 GeV is −0.010±0.005(stat)±0.004(syst) for Λ and 0.002±0.006(stat)±0.004(syst) for Λ¯. It is also measured as a function of xF and pT, but no significant dependence on these variables is observed. Prior to this measurement, the polarization was measured at fixed-target experiments with center-of-mass energies up to about 40 GeV. The ATLAS results are compatible with the extrapolation of a fit from previous measurements to the xF range covered by this measurement
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