A case of Incontinentia Pigmenti associated with congenital absence of portal vein system and nodular regenerative hyperplasia

Congenital absence of portal vein system (CAPVS) is a rare condition in which portal perfusion is bypassed by portosystemic shunt leading to the development of portal hypertension (PH) or porto‐systemic encephalopathy (PSE). Visceral anomalies and liver cancer can be associated with CAPVS1.Thanks to the advances in imaging, the number of CAPVS cases detected has increased. Incontinentia Pigmenti (IP) (OMIM #308300) also represents a rare condition, characterized by skin, teeth, hair, nails, eyes and central nervous system alterations, due to mutations of NEMO/IKBKG gene. We report on the first case of IP associated with CAPVS and nodular regenerative hyperplasia (NRH) of the liver, in a patient with facial dysmorphisms and speech delay. Although rare, this finding may support the role of NEMO in liver homeostasis

Broad-band properties of flat-spectrum radio-loud narrow-line Seyfert 1 galaxies

We report about recent updates of broad-band properties of radio-loud narrow-line Seyfert 1 galaxies.Comment: 5 pages, no figures. Proceedings 28th Texas Symposium on Relativistic Astrophysics, Geneva (Switzerland), 13-18 December 201

Jet quenching in the neutron star low-mass X-ray binary 1RXS J180408.9-342058

We present quasi-simultaneous radio (VLA) and X-ray (Swift) observations of the neutron star low-mass X-ray binary (NS-LMXB) 1RXS J180408.9-342058 (J1804) during its 2015 outburst. We found that the radio jet of J1804 was bright (232 ± 4 µJy at 10 GHz) during the initial hard X-ray state, before being quenched by more than an order of magnitude during the soft X-ray state (19 ± 4 µJy). The source then was undetected in radio ( < 13 µJy) as it faded to quiescence. In NS-LMXBs, possible jet quenching has been observed in only three sources and the J1804 jet quenching we show here is the deepest and clearest example to date. Radio observations when the source was fading towards quiescence (L X = 10 34-35 erg s -1 ) show that J1804 must follow a steep track in the radio/X-ray luminosity plane with ß > 0.7 (where L R a L X ß ). Few other sources have been studied in this faint regime, but a steep track is inconsistent with the suggested behaviour for the recently identified class of transitional millisecond pulsars. J1804 also shows fainter radio emission at L X < 10 35 erg s -1 than what is typically observed for accreting millisecond pulsars. This suggests that J1804 is likely not an accreting X-ray or transitional millisecond pulsar. © 2017 The Authors. Published by Oxford University Press on behalf of the Royal Astronomical Society

Properties of flat-spectrum radio-loud narrow-line Seyfert 1 galaxies

We have conducted a multiwavelength survey of 42 radio loud narrow-1ine Seyfert 1 galaxies (RLNLS1s), selected by searching among all the known sources of this type and omitting those with steep radio spectra. We analyse data from radio frequencies to X-rays, and supplement these with information available from online catalogues and the literature in order to cover the full electromagnetic spectrum. This is the largest known multiwavelength survey for this type of source. We detected 90% of the sources in X-rays and found 17% at gamma rays. Extreme variability at high energies was also found, down to timescales as short as hours. In some sources, dramatic spectral and flux changes suggest interplay between a relativistic jet and the accretion disk. The estimated masses of the central black holes are in the range ~10^6-8 Msun, lower than those of blazars, while the accretion luminosities span a range from ~0.01 to ~0.49 times the Eddington limit, with an outlier at 0.003, similar to those of quasars. The distribution of the calculated jet power spans a range from ~10^42.6 to ~10^45.6 erg/s, generally lower than quasars and BL Lac objects, but partially overlapping with the latter. Once normalised by the mass of the central black holes, the jet power of the three types of active galactic nuclei are consistent with each other, indicating that the jets are similar and the observational differences are due to scaling factors. Despite the observational differences, the central engine of RLNLS1s is apparently quite similar to that of blazars. The historical difficulties in finding radio-loud narrow-line Seyfert 1 galaxies might be due to their low power and to intermittent jet activity

Single hadron response measurement and calorimeter jet energy scale uncertainty with the ATLAS detector at the LHC

The uncertainty on the calorimeter energy response to jets of particles is derived for the ATLAS experiment at the Large Hadron Collider (LHC). First, the calorimeter response to single isolated charged hadrons is measured and compared to the Monte Carlo simulation using proton-proton collisions at centre-of-mass energies of sqrt(s) = 900 GeV and 7 TeV collected during 2009 and 2010. Then, using the decay of K_s and Lambda particles, the calorimeter response to specific types of particles (positively and negatively charged pions, protons, and anti-protons) is measured and compared to the Monte Carlo predictions. Finally, the jet energy scale uncertainty is determined by propagating the response uncertainty for single charged and neutral particles to jets. The response uncertainty is 2-5% for central isolated hadrons and 1-3% for the final calorimeter jet energy scale.Comment: 24 pages plus author list (36 pages total), 23 figures, 1 table, submitted to European Physical Journal

Search for the standard model Higgs boson in the H to ZZ to 2l 2nu channel in pp collisions at sqrt(s) = 7 TeV

A search for the standard model Higgs boson in the H to ZZ to 2l 2nu decay channel, where l = e or mu, in pp collisions at a center-of-mass energy of 7 TeV is presented. The data were collected at the LHC, with the CMS detector, and correspond to an integrated luminosity of 4.6 inverse femtobarns. No significant excess is observed above the background expectation, and upper limits are set on the Higgs boson production cross section. The presence of the standard model Higgs boson with a mass in the 270-440 GeV range is excluded at 95% confidence level.Comment: Submitted to JHE

Standalone vertex finding in the ATLAS muon spectrometer

A dedicated reconstruction algorithm to find decay vertices in the ATLAS muon spectrometer is presented. The algorithm searches the region just upstream of or inside the muon spectrometer volume for multi-particle vertices that originate from the decay of particles with long decay paths. The performance of the algorithm is evaluated using both a sample of simulated Higgs boson events, in which the Higgs boson decays to long-lived neutral particles that in turn decay to bbar b final states, and pp collision data at √s = 7 TeV collected with the ATLAS detector at the LHC during 2011