Желудочковая экстрасистолия у детей

The article presents updated data on the problem of premature ventricular contractions in children based on the clinical guidelines of the Russian Society of Cardiology and the Union of Pediatricians of Russia for the diagnosis, treatment and management of pediatric patients with premature ventricular contraction. The issues of diagnosis and treatment based on the principles of evidence-based medicine as well as important aspects of prevention of exacerbations and follow-up have been clarified in detail. The criteria for assessing the quality of care for patients with premature ventricular contractions have been presented.CONFLICT OF INTEREST. Not declared.В статье изложены обновленные данные о проблеме желудочковых экстрасистолий у детей, основанные на клинических рекомендациях Ассоциации детских кардиологов России и Союза педиатров России по диагностике, лечению и ведению пациентов детского возраста с желудочковой экстрасистолией. Подробно освещены вопросы диагностики, лечения, основанные на принципах доказательной медицины, а также важные аспекты профилактики обострений болезни и диспансерного наблюдения. Отображены критерии оценки качества медицинской помощи пациентам с желудочковыми экстрасистолиями.Публикация является обновленным вариантом клинических рекомендаций Ассоциации детских кардиологов России и Союза педиатров России по диагностике, лечению и ведению пациентов детского возраста с желудочковой экстрасистолией, опубликованных на сайте https://medi.ru/klinicheskie-rekomendatsii/zheludochkovaya-ekstrasistoliya-u-detej_14366/Авторы подтверждают отсутствие конфликта интересов, который необходимо обнародовать

Ventricular arrhythmias. Ventricular tachycardias and sudden cardiac death. 2020 Clinical guidelines

Russian Society of Cardiology (RSC).With the participation of Russian Scientific Society of Clinical Electrophysiology, Arrhythmology and Cardiac Pacing, Russian Association of Pediatric Cardiologists, Society for Holter Monitoring and Noninvasive Electrocardiology.Approved by the Scientific and Practical Council of the Russian Ministry of Health

GENETICALLY DETERMINED CARDIAC ARRHYTHMIAS

Genetic factors play an important role in pathogenesis of many diseases. It has been shown that potential-dependent Na, K, and Ca channels have common characteristics in their molecular structure, which should be taken into account when assessing physiological functioning of these channels. Hereditary diseases due to channel pathology are called channelopathies, or primary electrical heart disorders (long QT interval syndrome, short QT interval syndrome, Brugada syndrome, catecholamine-dependent ventricular tachycardia, idiopathic ventricular fibrillation, Lenegre disease, hereditary Wolf-Parkinson-White syndrome, hereditary atrial fibrillation). The second leading cause of sudden cardiac death (SCD), after coronary heart disease, is secondary hereditary electrical disorders (hypertrophic cardiomyopathy, dilated cardiomyopathy, right ventricular arrhythmogenic dysplasia, isolated left ventricular non-compaction). Genetically determined cardiac arrhythmias (CA), with or without structural heart pathology, manifest in young age (with an exception of Brugada syndrome) and have specific phenotypic and genotypic characteristics. Timely diagnostics of these diseases should be based on ECG screening (ideally performed before 3 years of age) and EchoCG. In addition, examination of families with high SCD risk has an important diagnostic value. High total SCD risk in treated patients with genetically determined CA is an indication for cardioverter-defibrillator implantation. Optimal strategy of SCD prevention in patients with genetically determined CA includes baseline risk assessment and ongoing monitoring, according to the individual risk profile. This review describes clinical and molecular features of genetically determined CA, SCD risk criteria, and modern views on diagnostics and treatment of these patients

Premature Ventricular Contraction in Children

The article presents updated data on the problem of premature ventricular contractions in children based on the clinical guidelines of the Russian Society of Cardiology and the Union of Pediatricians of Russia for the diagnosis, treatment and management of pediatric patients with premature ventricular contraction. The issues of diagnosis and treatment based on the principles of evidence-based medicine as well as important aspects of prevention of exacerbations and follow-up have been clarified in detail. The criteria for assessing the quality of care for patients with premature ventricular contractions have been presented.CONFLICT OF INTEREST. Not declared