Current Trends in the Development of Creative Industries. Musical Minimalism in Modern Cinema

В статье рассматривается понятие «творческие/креативные индустрии» и те направления, которые к ним относятся. Описывается механизм существования креативных индустрий в наше время и их значение в социокультурной практике. Среди направлений креативных индустрий важное место занимает кинематограф. В качестве примера актуальных киноработ автор уделяет внимание творчеству композитора Филипа Гласса и его музыке к трилогии «Каци». Рассматривается роль музыкального минимализма в кинематографе, а также различные композиторские техники, применимые к данному направлениюThe article discusses the concept of “creative/creative industries” and the areas that relate to them. The mechanism of the existence of creative industries in our time and their importance in socio-cultural practice is described. Cinema occupies an important place among the directions of creative industries. As an example of actual film works, the author pays attention to the work of composer Philip Glass and his music for the Katsi trilogy. The role of musical minimalism in cinema is considered, as well as various compositional techniques applicable to this directio

Design of an Universal Source for Semi-automatic Ac Welding and Induction Heating

This paper proposes a circuit solution and a power source control algorithm for semi-automatic AC welding with improved energy and weight-size characteristics. A distinctive feature of the designed source is the absence of an input rectifier: welding is carried out with a high-frequency alternating current. That has made it possible to significantly reduce power losses in the source, as well as provide the possibility of implementing induction heating by connecting an inductor to the source output. Another distinctive feature of the designed source is an increased power factor and a reduced level of higher harmonics of the current consumed. The power factor of the described source reaches 0.94 against 0.5÷0.7 for sources equipped with a conventional rectifier with capacitive smoothing. The designed source's composition includes a power supply system for the wire feed drive with speed stabilization due to positive feedback on the motor current. That has made it possible to ensure the stable operation of the drive in a wide range of speeds. A model has also been developed of a flux wire welding torch containing a feed drive and a coil with a wire (up to 100 mm in diameter), placed, in order to reduce the size, in the handle of the torch. In addition to the welding function, the source makes it possible to solve the tasks related to induction heating and/or hardening of small parts; to that end, a compact inductor is connected to its output. Tests of the source showed the feasibility of the proposed ideas and circuit solutions. The dimensions of the source are 190×107×65 mm; weight, 1.4 kg; output current, up to 120 A. The proposed technical solution enables the construction of small-sized, lightweight, universal, easy-to-use power supplies for semi-automatic welding with the option of induction heatin

Клинические рекомендации по ведению детей с дефицитом лизосомной кислой липазы

Lysosomal acid lipase deficiency is s a rare hereditary enzymopathy. The article presents epidemiological data and features of etiopathogenesis of two phenotypic forms of lysosomal acid lipase deficiency — Wolman disease and cholesterol ester storage disease. Special attention has been given to the key issues of differential diagnostic search, clinical guidelines based on the principles of evidence-based medicine have been given.Дефицит лизосомной кислой липазы — редкая наследственная ферментопатия. В статье представлены эпидемиологические данные и особенности этиопатогенеза двух фенотипических форм дефицита лизосомной кислой липазы — болезни Вольмана и болезни накопления эфиров холестерина. Подробно описаны клинические характеристики быстропрогрессирующей формы и медленно развивающейся болезни накопления эфиров холестерина. Особое внимание уделено ключевым вопросам дифференциально-диагностического поиска, приведены рекомендации по лечению, основанные на принципах доказательной медицины