10 research outputs found
Early-onset idiopathic pyoderma gangrenosum
Neutrophilic dermatoses are autoinflammatory disorders characterized by sterile cutaneous inflammatory neutrophilic infiltrates. This group of diseases is rare in infants and children, where sepsis is the diagnosis of exclusion. This report focuses on the clinical presentation, investigation, and management of infants with idiopathic pyoderma gangrenosum. It should allow for a better appreciation of the disease and a more patient focused approach to its diagnosis and management