VENTRİKÜLER SEPTAL DEFEKTLİ BİR APERT SENDROMU OLGUSU

Apert syndrome is a congenital malformation syndrome which is associated withcraniosynostosis, craniofacial anomalies, syndactyly and congenital heart defects.Several cardiovascular abnormalities including atrial septal defect, ventricular septaldefect or patent ductus arteriosus were reported in 10% of the patients with Apertsyndrome. Herein, we report a case of Apert syndrome with ventricular septal defectdiagnosed at 2-month-old age and aim to emphasize the clinical and laboratoryfeatures of Apert syndrome in the light of this case. We also aim to attract the attentionof the pediatricians to the careful cardiologic examination in every newly diagnosedcase of Apert syndrome for early detection of possible heart defects.Apert sendromu, kraniyosinostoz, kraniyofasyal anomaliler, sindaktili ve konjenital kalpdefektleri ile giden bir konjenital malformasyon sendromudur. Apert sendromluhastaların %10'unda atriyal septal defekt, ventriküler septal defekt veya patent duktusarteriozus gibi çeşitli kardiyovasküler anormallikler bildirilmiştir. Bu yazıda 2 aylıkkentanı alan ventriküler septal defektli bir olgu sunuyor ve bu olgunun ışığında Apertsendromunun klinik ve laboratuar özelliklerini vurgulamayı amaçlıyoruz. Ayrıca yenitanı alan her Apert semdromlu olguda, olası kardiyak defektlerin erken teşhisi içindikkatlı bir kardiyak muayene yapılmasının gerekliliğine çocuk hekimlerinin dikkatiniçekmeyi amaçlıyoruz

Effectiveness of music during cardiac catheterization on children\u27s pain, fear, anxiety and vital signs: A randomized, blind controlled trial

PURPOSE: This study aims to examine the effectiveness of music during pediatric cardiac catheterization procedure on children\u27s pain, fear, anxiety and vital signs. DESIGN AND METHODS: This randomized, blind controlled study was conducted with the guidelines of Consolidated Standards of Reporting Trials (CONSORT). The sample of children was allocated to the Control Group, the Classic Music Group, and the Self-Selected Group. Pain, fear, and anxiety levels were measured before and after the pediatric cardiac catheterization procedure. Vital signs were measured before, during, and after the pediatric cardiac catheterization procedure. RESULTS: There was no significant difference between the groups in terms of demographic status, pain, fear, or anxiety levels and vital signs before the procedure. In post pediatric cardiac catheterization measurement in the recovery phase, pain, fear levels, anxiety levels, heart rate, systolic and diastolic blood pressure of children in the musical intervention groups were lower than the control group. No statistical difference was found in terms of pain, fear and anxiety levels of the children in groups Classic and Self-Selected. CONCLUSION AND PRACTICE IMPLICATIONS: The result of this research reveals that musical intervention applied during the pediatric cardiac catheterization procedure in children affects the reduction of pain, fear and anxiety levels and stabilization of vital signs. This intervention could be an effective nonpharmacological method to improve outcomes.Nurses can improve children\u27s comfort by using musical interventions. CLINICAL REGISTRATION: This study was registered at the U.S. National Library of Medicine Clinical Trials (code: NCT04316754)