Megacolon és ízületi gyulladás = Megacolon and arthritis

A szerzők jelen munkában négy juvenilis betegük esetét mutatják be, akiknél a krónikus ízületi gyulladást kísérő megacolont észleltek. A két betegség lefolyását és egymással való (feltehetőleg patogenetikai) kapcsolatát ismertetik, felhívva a figyelmet arra, hogy nem véletlen társulásról lehet szó. A mozgásszervi klinikai kép alapján mind a négy eset a szeronegatív spondylarthritisek csoportjába sorolható. A hasi statust illetően fizikális vizsgálattal minden alkalommal a bal oldali iliacalis régióban masszív rezisztenciát, nagy mennyiségű scibalakkal telített megacolont észleltek. A megacolon egy esetben bizonyult valódi Hirschprung-betegségnek, műtéti megoldására egy esetben került sor, amely egyúttal az arthritis remisszióját is eredményezte. A többi betegnél a krónikus obstipáció, megacolon továbbra is megoldásra vár. | In present reports authors describes four cases with megacolon and arthritis. The etiology of these unique associations is known in only one case. The musculoskeletal pictures belong to the group of seronegative spondyloarthritis. A huge resistance with great scibalas was detected in the left iliac region by physical examination in all cases. Operative maneuver of bowel resulted complete remission of arthritis in one case, thus, chronic obstipation with intermittent relapse of arthritis remained at the other cases

Tha Hungarian version of the Juvenile Arthritis Multidimensional Assessment Report (JAMAR)

The Juvenile Arthritis Multidimensional Assessment Report (JAMAR) is a new parent/patient-reported outcome measure that enables a thorough assessment of the disease status in children with juvenile idiopathic arthritis (JIA). We report the results of the cross-cultural adaptation and validation of the parent and patient versions of the JAMAR in the Hungarian language. The reading comprehension of the questionnaire was tested in 10 JIA parents and patients. Each participating centre was asked to collect demographic, clinical data and the JAMAR in 100 consecutive JIA patients or all consecutive patients seen in a 6-month period and to administer the JAMAR to 100 healthy children and their parents. The statistical validation phase explored descriptive statistics and the psychometric issues of the JAMAR: the three Likert assumptions, floor/ceiling effects, internal consistency, Cronbach\u2019s alpha, interscale correlations, test\u2013retest reliability, and construct validity (convergent and discriminant validity). A total of 206 JIA patients (3.9% systemic, 41.3% oligoarticular, 28.2% RF-negative polyarthritis, 26.6% other categories) and 90 healthy children, were enrolled in two centres. The JAMAR components discriminated healthy subjects from JIA patients. All JAMAR components revealed good psychometric performances. In conclusion, the Hungarian version of the JAMAR is a valid tool for the assessment of children with JIA and is suitable for use both in routine clinical practice and clinical research

Proceedings Of The 23Rd Paediatric Rheumatology European Society Congress: Part Two

PubMe