Anästhesie und Ahornsirupkrankheit: Fallbericht und perioperatives anästhesiologisches Management

Zusammenfassung: Die Ahornsirupkrankheit ist eine seltene autosomal-rezessive Stoffwechselerkrankung, der eine Störung der Decarboxylierung von verzweigtkettigen Aminosäuren zugrunde liegt. Erste Symptome zeigen sich bereits in der Neonatalperiode. Unbehandelt führt die Erkrankung zu rasch progredienter neurologischer Symptomatik. Während stressvoller Situationen wie Infektionen und Operationen können bei Patienten mit Ahornsirupkrankheit schwere ketoacidotische Zustände mit rapider neurologischer Verschlechterung und Hypoglykämien auftreten. Im vorliegenden Beitrag wird über das perioperative Management bei einem 26-jährigen Mann mit Ahornsirupkrankheit berichtet, ein Überblick über die Erkrankung gegeben, und die anästhesiologischen Implikationen werden diskutier

Using Custom NER Models to Extract DOD Specific Entities from Contracts

The Air Force Sustainment Center collected 3.7 million contracts onto the Air Force Research Laboratory’s high power computers. They are in the format of a .pdf or scanned document, making them unstructured data. The Data Analytics Resource Team extracted the documents into a textual format for use in further analysis. This thesis looks to extract four DOD specific entities (NSN, Part Number, CAGE Code, and Supplier Name) from the contracts using custom NER models. This newly extracted information will allow the Air Force to identify what parts are supplied by which vendors. This information along with historical CLIN pricing for the vendor specific part number can give decision makers the ability to negotiate pricing based on historical data and competitor pricing. In addition to just pricing, part numbers can be aligned with maintenance data to make informed decisions on which vendor to go with by analyzing life cycle costs of a part

Anästhesie und Ahornsirupkrankheit : Fallbericht und perioperatives anästhesiologisches Management

Maple syrup urine disease is a rare autosomal-recessive metabolic disorder caused by a deficit of oxidative decarboxylation of branched-chain amino acids. First symptoms appear in the neonatal period. Without treatment the disease is characterized by rapid progression of neurological symptoms. During stressful situations, such as infection or surgery, patients may experience severe ketoacidosis, rapid neurological deterioration and hypoglycemia. The perioperative management of a 26-year-old man with maple syrup urine disease is described, a review of the disease is given and anaesthesia-related implications are discussed

Observations of ramped current operation in ZT-40M

A new mode of reversed-field pinch (RFP) startup has been tested in the RFP experiment ZT-40M. Instead of increasing the toroidal current almost sinusoidally to its maximum, as is normally done, the current is initially raised to approx. 70 kA in 0.8 ms and subsequently slowly ramped up to approx. 170 kA in 14 ms. The behaviors of toroidal flux, particle density, temperature, and radiated power for the ramped discharges are compared with fast current rise, flat-topped operation. The successful demonstration of ramped toroidal discharges has an important impact on future large RFP experiments since the voltage necessary to drive the toroidal current for slow (approx. 10 to approx. 20 ms) startup is reduced

Design of the ZT-1 toroidal pinch experiment

Electrical design details are given for a toroidal Z-pinch device named ZT-1 that uses field programming to achieve a stable, reversed field pinch. The plasma is formed in a 4-mm-thick, 10.3-cm-i.d., high alumina, segmented ceramic vacuum chamber. Voltages as high as 70 kV are routinely attained by interrupting with a fuse 800 kA in an inductive store. The current is diverted from the fuse to the primary of a single-turn transformer divided into quadrants. A total of 280 kV at 200 kA can then be applied to the plasma, which forms the secondary circuit of the transformer. This system produces dB/sub theta//dt's of up to 8 T/ $mu$s; with modifications to the electrical system, dB/sub theta//dt's as low as 0.1 T/$mu$s are obtained. The B/sub z/ bias field of up to 0.25 T can be reversed at a rate of up to 0.2 T/$mu$s. Both B/sub theta/ and B/sub z/ magnetic field errors are minimized. The design of the fuses and magnetic core and the development of a low inductance and resistance metal-to-metal crowbar are described. (auth

La marche vers le 230/400 V a EDF La planification integree des reseaux BT

SIGLEAvailable at INIST (FR), Document Supply Service, under shelf-number : 26165 B, issue : a.1996 n.33 / INIST-CNRS - Institut de l'Information Scientifique et TechniqueFRFranc