A rare trigger for photosensitive seizure: fireworks

[No Abstract Available

The effectiveness of the ketogenic diet in drug-resistant childhood epilepsy

2nd International Behcet Uz Children's Congress -- MAR 04-07, 2020 -- Izmir, TURKEYBackground. We aimed to investigate the effectiveness of ketogenic diet (KD) in children with various types of refractory epilepsy. Methods. A total of 91 children (49 females) aged 3 to 193 months (median, 52 months) with drug resistant epilepsy who received KD treatment for at least 12 months were enrolled in the study. Seizure frequency, adherence to diet, reason for discontinuation of KD, and adverse effects were recorded. Response was defined as >= 50% improvement in seizure frequency compared to baseline. We also searched for influences of different variables on the outcome. Results. Intent-to-treat analysis revealed an improvement in seizure frequency for >= 50% in 73.6%, 80.2%, 75.8%, 73.6%, and 70.3% of patients at month-1,-3,-6,-9, and month-12, respectively. Overall, 32 (35.2%) patients remained seizure-free at month-12. There was no significant differences between responders and non responders in terms of age at onset of epilepsy, age at onset of KD, gender, or etiology. Mild hyperlipidemia was associated with a higher response rate. At the last follow-up (median: 20 months), 38 (41.8%) patients were still maintained on KD. While 15.4% of patients completed the diet with a success in seizure control, remainder discontinued KD due to lack of efficacy (23.1%), non-adharence to diet (11%), intercurrent infection (4.4%), adverse effects (3.3%), and death (1.1%). Conclusion. Ketogenic diet treatment appears to be effective in about two-thirds of children with various types of drug-resistant epilepsy, including one-third remaining seizure free. Mild hyperlipidemia seems to be associated with a higher response rate. Discontinuation of KD is mostly due to lack of efficacy or nonadherence, and rarely side effects

Evaluation of immunization status in patients with cerebral palsy: a multicenter CP-VACC study

Children with chronic neurological diseases, including cerebral palsy (CP), are especially susceptible to vaccine-preventable infections and face an increased risk of severe respiratory infections and decompensation of their disease. This study aims to examine age-appropriate immunization status and related factors in the CP population of our country. This cross-sectional prospective multicentered survey study included 18 pediatric neurology clinics around Turkey, wherein outpatient children with CP were included in the study. Data on patient and CP characteristics, concomitant disorders, vaccination status included in the National Immunization Program (NIP), administration, and influenza vaccine recommendation were collected at a single visit. A total of 1194 patients were enrolled. Regarding immunization records, the most frequently administrated and schedule completed vaccines were BCG (90.8%), hepatitis B (88.9%), and oral poliovirus vaccine (88.5%). MMR was administered to 77.3%, and DTaP-IPV-HiB was administered to 60.5% of patients. For the pneumococcal vaccines, 54.1% of children received PCV in the scope of the NIP, and 15.2% of children were not fully vaccinated for their age. The influenza vaccine was administered only to 3.4% of the patients at any time and was never recommended to 1122 parents (93.9%). In the patients with severe (grades 4 and 5) motor dysfunction, the frequency of incomplete/none vaccination of hepatitis B, BCG, DTaP-IPV-HiB, OPV, and MMR was statistically more common than mild to moderate (grades 1-3) motor dysfunction (p = 0.003, p < 0.001, p < 0.001, p < 0.00, and p < 0.001, respectively). Physicians' influenza vaccine recommendation was higher in the severe motor dysfunction group, and the difference was statistically significant (p = 0.029). Conclusion: Children with CP had lower immunization rates and incomplete immunization programs. Clinicians must ensure children with CP receive the same preventative health measures as healthy children, including vaccines

What is the role of primary hip hemiarthroplasty over 70 years of age?

AMAÇ: Yetmiş yaş üzeri anstabil intertrokanterik femur kırıklarda (IFK) hemiartroplasti uyguladığımız olguları morbidite açısından değerlendirdik. Günümüzdeki hemiartroplastinin yerini tartışmayı amaçladık. GEREÇ veYÖNTEMLER: Kliniğimizde 1995-2006 yılları arasında hemiartroplasti yöntemi ile tedevi edilen intertrokanterik femur kırıklı hastaların 75'i çalışmaya dahil edildi. Ortalama takip süreleri 44 (20-82) ay idi. Hastaların 43'ü kadın,32'si erkekti. 45 hastanın sağ, 30 hastanın sol kalçası etkilenmişti. Olguların hepsi Harris kalça skorlamasına göre değerlendirildi. BULGULAR: Harris kalça skorlama sistemine göre dört hastada mükemmel sonuç, 54 hastada iyi sonuç, dokuz hastada orta, sekiz hastada kötü sonuç saptandı.Yetmiş yaş üzeri anstabil IFK'larında uygulanan hemiartroplasti olgularının %78'inde iyi-mükemmel sonuca ulaşılmış olduğu saptandı SONUÇ: Ameliyat süresinin çok kısa olması, skopi gibi teknik donanıma sahip olma şartının olmaması ve erken tam yük verebilme gibi avantajları olan hemiartroplasti yönteminin yaşlı IFK olgularında halen geçerliliğini ve etkinliğini koruyan bir yöntem olduğu sonucuna vardık.OBJECTIVE: We assessed importance of primary hip hemiarthroplasty in treatment algorithm. And we have evaluated patients treated with primary hip hemiarthroplasty for unstable intertrochanteric hip fractures according to morbidity rates. MATERIAL and METHODS: In our clinic between 1995 and 2006; we selected 75 patients treated with primary hip hemiarthroplasty for intertrochanteric femur fracture (IFF). Mean follow-up was 44 months (20-82). Genders of patients were female 43% and male 32%. Numbers of affected hips were 45 right and 30 left. Patients were evaluated with Harris Hip Score. RESULTS: Harris Hip Score of patients; Excellent 4, Good 54, Fair 9 and Poor 8 results were obtained. Seventyeight percent excellent to good results obtained primary hip hemiarthroplasty for unstable intertrochanteric femur fracture patients over 70 years of age. CONCLUSION: There are advantages of primary hip hemiarthroplasty over osteosynthesis for patient's population over 70 years of age such as; short surgery time, no radiation exposure and immediate weight bearing. Primary hip hemiarthroplasty can be an alternative treatment for unstable intertrochanteric fractures in elderly patients so as to achieve earlier mobilization. It is also current and effective treatment option for most elderly

Hot water epilepsy under 3 years of age: A short term follow-up study

Aim: Hot water epilepsy (HWE) is a type of reflex epilepsy that occurs as a result of immersing or pouring hot water over the head. Clinical and laboratory findings and short-term neurodevelopmental outcomes of patients were discussed in this report. Materials and Methods: Eight patients under the age of three and followed-up with a diagnosis of HWE between 2017 and 2020 were enrolled in the study. Patient files were evaluated retrospectively. Results: All our patients except one were boys. The patients’ mean age at admission was 16.6 months (min: 10, max: 36), and the mean follow-up period was 13.5 months (min: 6, max: 25). Two patients also experienced non-reflex motor seizures not related to bathing, and these received daily oral antiepileptic therapy. Six patients had focal onset secondary generalized seizures, while one had focal seizures and one has hypomotor seizures accompanied by loss of consciousness. neurodevelopmental milestones were compatible with the patient’s age in all followed-up cases. Clobazam administration before bathing is currently an effective and easily applicable method for this condition. Conclusion: Hot water epilepsy is mostly benign. Clobazam before bathing is an effective option. Daily oral antiepileptic therapy should be administered to patients with seizures accompanying HWE

Osteometric examination of skeletal remains of sheep uncovered in excavations performed in ancient city of Kibyra

Çalışmada Burdur'un Gölhisar ilçesinde bulunan Kibyra Antik Kentindeki arkeolojik kazılardan ortaya çıkarılan koyun iskeleti kalıntılarının osteometrik olarak incelenmesi amaçlanmıştır. Çalışmada Kibyra Antik Kenti'nin Bouleuterion-Odeion, Stadion, Agora ve Dış Cephe arkeolojik kazılarında ortaya çıkarılan ölçü alınabilir nitelikte toplam 370 adet kemik kalıntısı kullanıldı. Bu kemiklerden osteometrik ölçüler alındı. Ayrıca elde edilen veriler kullanılarak koyunların cidago yüksekliği ve ebatları ile ilgili tahminde bulunuldu. Buna göre Kibyra koyunlarının ortalama cidago yüksekliği 59.8 cm olarak tespit edildi. Sonuç olarak çalışmada elde edilen sayısal verilerin Ülkemizde sınırlı sayıdaki zooarkeolojik çalışmalara katkı sağlayacağı düşünülmektedir.The aim of the study was to investigate the osteometric investigation of the remains of sheep skeleton from archaeological excavations in Kibyra Antique City located in Golhisar district of Burdur. In the study, the remains of the totally measurable 370 bones revealed in the archaeological excavations of Bouleuterion-Odeion, Stadion, Agora and Facade of the ancient city of Kibyra were used. The osteometric measuraments were obtained from these bones. Moreover, the shoulder height and dimensions were estimated by using obtained data. According to this, the average of shoulder height of Kibyra sheep was determined as 59.8 cm. As a result, it was thought that the numerical data obtained in the study will contribute to the limited number zooarcaeological researches in our country

An unexpected clinical presentation in periodontal Ehler-Danlos syndrome: preterm birth, profound intellectual disability and self-injurious behavior

[Abstract Not Available