LINEAR IGA DERMATOSIS – SCROTAL CLUSTER OF GRAPES PRESENTATION

A dermatose IgA linear infantil, ou dermatose bolhosa crónica da infância, é uma doença imuno-bolhosa, subepidérmica e adquirida. Este caso ilustra uma forma de apresentação peculiar de uma doença incomum da infância e pretende salientar a importância da dapsona no seu tratamento, numa altura em que este fármaco é cada vez mais de acesso limitado.PALAVRAS-CHAVE – Criança; Dermatose IgA linear; Dermatose bolhosa crónica; Dapsona.Linear IgA dermatosis, or chronic bullous disease of childhood, is an acquired subepidermic immunobullous disease. This case illustrates a peculiar form of presentation of an uncommon pathology of childhood and emphasizes the importance of dapsone in its treatment, especially in at a time when availability of this drug is limited.KEYWORDS – Immunoglobulin A; Autoimmune Diseases; Skin Diseases, Vesiculobullous; Child; Dapsone

Adult blaschkolinear acquired inflammatory skin eruption (BLAISE) with simultaneous features of lichen striatus and blaschkitis

Blaschkitis and lichen striatus are generally distinguished in the literature by the age of onset, lesion distribution, and histopathology. However, there is currently no clear consensus among authors about whether to consider blaschkitis and lichen striatus different clinical entities or a spectrum ofthe same disease. We present a case of adult BLAISE with features of both lichen striatus and blaschkitis, which seems to support the theory that these clinical entities may in fact represent a spectrum of the same pathological process