Etiopathogenesis of sirenomelia on the framework of a case report

Kaudal regresyon sendromu grubu içinde değerlendirilen si- renomeli nadir görülen bir anomalidir. Birçok organda ciddi malformasyonla beraberlik gösterir. Bu yazıda daha önce tıbbi yazında bildirilmemiş olan sirenomeli ile 13 kaburga ve torakal vertebranın birlikteliği sunuldu. Olgumuzu, etiyopatogenezle ilgili yeni yorumlara ışık tutabileceği düşüncesiyle sunduk.Sirenomelia is a rare anomaly evaluated in the group of caudal regression syndrome. It is associated with serious malforma- tion in many organs. In this article, we present a sirenomelia case with coexistence in 13 ribs and thoracic vertebrae. We re- ported our case to shed light on new comments with etio- pathogenesis

Turkish Neonatal and Turkish Ophthalmology Societies consensus guideline on the retinopathy of prematurity.

Retinopathy of prematurity is a pathophysiological condition that occurs in relation to abnormal proliferation in the retinal vessels in premature babies. Its exact pathogenesis is not known. In Turkey, the increased chance of survival in premature babies with much younger gestational age and much lower birth weight in parallel with the developments in neonatal care causes retinopathy of prematurity, which has led to vision problems and blindness to emerge as a more frequent problem. Early diagnosis and timely and appropriate treatment of retinopathy of prematurity contributes to the developmental process and increases the quality of life by preventing vision loss. It should be kept in mind that retinopathy of prematurity may also lead to serious medicolegal problems

Nadir komplikasyonlarla giden dört yenidoğan kompleks over kisti olguları

With the wide common use of ultrasound, ovarian cysts of the fetus and neonate are more often detected. A case series of four infant with uncommon complications of antenatal ovarian cysts were presented. In the first case; autoamputated ovarian tissue was determined and disappeared during the follow up. The second and third case went under surgery. Histopathological results were reported as a torsional autoamputated hemorrhagic necrotic tuba-ovarian cyst. Abdominal ascites was determined postnatally due to rupture of neonatal ovarian cyst in the fourth case. The treatment approaches for ovarian cysts poses a therapeutic dilemma for the pediatrician and the pediatric surgeon. It has to be decided which patient should be referred for surgical therapy and which might be treated conservatively.Ultrasonun sık kullanımıyla fetal ve neonatal dönemde yenidoğan over kistleri daha sık saptanmaktadır. Bu yazıda; nadir komplikasyonlarla giden antenatal tanılı over kisti olguları sunulmuştur. Birinci olguda, otoampute over kisti saptanmış ve takibinde spontan kaybomuştur. İkinci ve üçüncü olguya cerrahi tedavi uygulanmıştır. Histopatolojik sonucu otoampute hemorajik nekrotik torsiyone tuba ovaryan kist olarak raporlanmıştır. Dördüncü olguda da, postnatal dönemde antenatal over kisti rüptürüne bağlı abdominal asit saptanmıştır. Pediatrist ve çocuk cerrahları için yenidoğan over kistlerinin tedavi yaklaşımı halen tartışmalıdır. Hangi hastada cerrahi, hangi hastada konservatif tedavi yaklaşımı yapılacağı belirlenmelidir

Bedside Diode Laser Photocoagulation Under Remifentanil Analgesia for Retinopathy of Prematurity: Early Structural Outcomes

Objectives: To evaluate one-year structural outcomes of bedside diode laser photocoagulation with remifentanil analgesia for retinopathy of prematurity (ROP) and discuss clinical and demographic characteristics of infants and other possible risk factors that may affect the outcome. Materials and Methods: The medical records of premature infants who were treated with bedside transpupillary diode laser photocoagulation under remifentanil analgesia for ROP were evaluated for clinical and demographic characteristics, accompanying systemic risk factors, laser parameters, complications of treatment, retreatment rate and one-year structural outcomes. Results: One-hundred and ninety-five eyes of 99 infants (59 males, 40 females) were recruited for the study. The mean gestational age and birth weight were 27.4±2.3 weeks (23-34) and 1003.3±297.8 g (570-2250), respectively. Laser therapy was performed for high-risk prethreshold ROP in 66.2% of eyes, aggressive posterior ROP (APROP) in 15.4% and threshold ROP in 18.4%. The mean number of laser spots was 1510.4±842.1 per laser session. No adverse effects of laser photocoagulation were observed except small lens opacities in two eyes and corneal opacity in one eye. Retreatment was needed in only three eyes, and vitreoretinal surgery was needed in six eyes of six patients despite laser treatment. Anatomic outcome was favorable in 189 eyes (96.9%) at the end of a 1-year follow-up. Presence of dilated and tortuous iris vessels (p=0.002) and tunica vasculosa lentis (p=0.009) along with type of ROP (APROP and stage 4a ROP at initial presentation) (p=0.001) were associated with poor anatomical outcome. Conclusion: Accurate and timely bedside transpupillary diode-laser photocoagulation under remifentanil analgesia is an effective and safe treatment modality for ROP, and may prevent vision-threatening retinal detachment and reduce the need for vitreoretinal surgery.PubMedScopu

The Turkish Neonatal Society proposal for the management of COVID-19 in the neonatal intensive care unit

Due to immaturity of immune function and the possibility of motherfetal vertical and aerosol transmissions, neonates are particularly susceptible to the new coronavirus (SARS-CoV-2). Perinatal-neonatal departments should cooperate closely and take integrated approaches, and neonatal intensive care units (NICU) should prepare emergency plans for the coronavirus disease 2019 (COVID-19) as far as possible, so as to ensure the optimal management and treatment of potential victims. During the epidemic of COVID-19, the emergency response plan for the NICU should be based on the actual situation, including diagnosis, isolation, and treatment, as well as available equipment and staffing, and take into account the psychosocial needs of the families and neonatal care staff. In this context of the COVID-19 pandemic, the Turkish Neonatal Society has proposed a protocol with the evidence available at the time of preparation to handle neonates with SARS-CoV-2 infections and outbreaks in NICUs. We hope that this proposal can provide valuable information so medical workers do not have to enter the battlefield alone. At this moment, sharing resources, experiences and lessons, regardless of who you are, is our only chance to win