ISOLATED TORSION OF THE ACCESSORY FALLOPIAN-TUBE IN 2 PREMENARCHAL GIRLS

Two 12-year-old, premenarchal girls presenting with acute abdominal pain due to torsion of their unilateral accessory Fallopian tubes are presented. These two patients are the first reported cases of isolated torsion of the accessory tubes in the world literature. Diagnostic difficulties and operative management of this rare condition are discussed

Jeune's asphyxiating thoracic dystrophy of the newborn

A 13-month-old patient with Jeune's thoracic asphyxiating dystrophy, was surgically treated using a methyl-methacrylate (acrylic) prosthesis. Although postoperative recovery was fast, the patient died of respiratory distress two months following surgery. Limitations of currently available surgical techniques and the need for long-term results will be discussed

PROPHYLACTIC ESOPHAGEAL CALIBRATION IN ESOPHAGEAL ATRESIA SURGERY

Anastomotic stricture is the most common complication following surgery for oesophageal atresia. The management of this problem provides a continuing challenge to paediatric surgeons. In an effort to reduce the rate as well as the morbidity and mortality associated with oesophageal stricture formation, a regime of routine post-operative prophylactic oesophageal calibration has been undertaken in Princess Margaret Hospital for Children over the last 12 years. Retrospective review of the results of this treatment modality shows low stricture (1.8%) and morbidity rates associated with the procedure

GIANT UMBILICAL-CORD ASSOCIATED WITH CORD HEMANGIOMA

A 6-h-old girl was transferred to the Pediatric Surgery Department of Sisli Children's Hospital due to a giant umbilical cord. Radiologic and laboratory studies were within normal limits. The umbilical mass was excised through an intraumbilical incision and the umbilicus reconstructed. Pathologic investigation demonstrated an umbilical cord hemangioma located near the umbilical end, compressing the cord structures externally. The remaining cord consisted of loose, edematous stroma similar to Wharton's jelly. The patient was discharged from the hospital on the 5th postoperative day and remains healthy 1 year later. Umbilical cord hemangioma should be considered in the etiology of a giant umbilical cord

LID - 10.1016/j.jpedsurg.2020.12.008 [doi]

AIM: Preservation of the azygos vein (AV) maintains normal venous drainage of the mediastinum and decreases postoperative congestion. The modification of esophageal atresia (EA) repair by preserving AV may prevent postoperative complications and may lead to better outcomes. The data from the Turkish Esophageal Atresia Registry (TEAR) were evaluated to define the effect of AV preservation on postoperative complications of patients with EA. METHODS: Data from TEAR for a period of five years were evaluated. Patients were enrolled into two groups according to the preservation of AV. Patients with divided (DAV) and preserved AV (PAV) were evaluated for demographic and operative features and postoperative complications for the first year of life. The DAV and PAV groups were compared according to the postoperative complications, such as fistula recanalization, symptomatic strictures, anastomotic leaks, total number of esophageal dilatations, and anti-reflux surgery. In addition, respiratory problems, which required treatment, were compared between groups. RESULTS: Among 502 registered patients; the data from 315 patients with the information of AV ligation were included. The male female ratio of DAV (n = 271) and PAV (n = 44) groups were 150:121 and 21:23, respectively (p > 0.05). The mean body weight, height, gestational age, and associated anomalies were similar in both groups (p > 0.05). The esophageal repair with thoracotomy was significantly higher in DAV group, when compared to the PAV group (p  0.05). There was no difference between DAV and PAV groups for anastomotic leaks, symptomatic anastomotic strictures, fistula recanalization, and the requirement for anti-reflux surgery (p > 0.05). The rate of respiratory problems, which required treatment, was significantly higher in the DAV group (p < 0.05) CONCLUSION: The data in the TEAR demonstrated that preserving the AV during EA repair led to no significant advantage on postoperative complications, with exception of respiratory problems. AV should be preserved as much as possible to maintain a normal mediastinal anatomy and to avoid respiratory complications