28 research outputs found
Influence of temperature condition on the process of СNM generation
Role of surface in processes of carbon nanomaterials generation in plasma-liquid system was analyzed. Qualitative
analysis of samples was supplied by spectrophotometrical methods, X-rays microanalysis and scanning microscope.
Influence of substrate temperature on carbon deposited nanostructures was shown. Possibility of obtaining carbon
nanostructures with metal inclusions in plasma-liquid systems from ethanol was presented.Досліджено роль поверхні в процесах генерації вуглецевих наноматеріалів (ВНМ) у плазмово-рідинній
системі на базі вторинного розряду. Якісний аналіз зразків проводився за допомогою спектрофотометричної
методики, рентгенівського мікроаналізу та скануючої мікроскопії. Показано вплив температури підкладки на
вихідні ВНМ. Продемонстровано можливість отримання вуглецевих наноструктур з включенням значної
кількості металів.Исследована роль поверхности в процессах генерации углеродных наноматериаллов (УНМ) в плазменно-
жидкостной системе с вторичным разрядом. Качественный анализ образцов проводился с помощью
спектрофотометрической методики, рентгеновского микроанализа и сканирующей микроскопии. Показано
влияние температуры подложки на полученные УНМ. Продемонстрирована возможность получения
углеродных наноструктур с включением значительного количества металлов
Hadronic B Decays to Charmed Baryons
We study exclusive B decays to final states containing a charmed baryon
within the pole model framework. Since the strong coupling for is larger than that for , the two-body charmful decay
has a rate larger than
as the former proceeds via the pole while the latter via the
pole. By the same token, the three-body decay receives less baryon-pole contribution than
. However, because the important charmed-meson
pole diagrams contribute constructively to the former and destructively to the
latter, has a rate slightly larger than
. It is found that one quarter of the rate comes from the resonant contributions. We discuss
the decays and
and stress that they are not color suppressed even though they can only proceed
via an internal W emission.Comment: 25 pages, 6 figure
Variational self-consistent theory for trapped Bose gases at finite temperature
We apply the time-dependent variational principle of Balian-V\'en\'eroni to a
system of self-interacting trapped bosons at finite temperature. The method
leads to a set of coupled non-linear time dependent equations for the
condensate density, the thermal cloud and the anomalous density. We solve
numerically these equations in the static case for a harmonic trap. We analyze
the various densities as functions of the radial distance and the temperature.
We find an overall good qualitative agreement with recent experiments as well
as with the results of many theoretical groups. We also discuss the behavior of
the anomalous density at low temperatures owing to its importance to account
for many-body effects.Comment: 8 pages, 8 figure
Next-to-next-to-leading order prediction for the photon-to-pion transition form factor
We evaluate the next-to-next-to-leading order corrections to the
hard-scattering amplitude of the photon-to-pion transition form factor. Our
approach is based on the predictive power of the conformal operator product
expansion, which is valid for a vanishing -function in the so-called
conformal scheme. The Wilson--coefficients appearing in the non-forward
kinematics are then entirely determined from those of the polarized
deep-inelastic scattering known to next-to-next-to-leading accuracy. We propose
different schemes to include explicitly also the conformal symmetry breaking
term proportional to the -function, and discuss numerical predictions
calculated in different kinematical regions. It is demonstrated that the
photon-to-pion transition form factor can provide a fundamental testing ground
for our QCD understanding of exclusive reactions.Comment: 62 pages LaTeX, 2 figures, 9 tables; typos corrected, some references
added, to appear in Phys. Rev.
Performance of novel VUV-sensitive Silicon Photo-Multipliers for nEXO
Liquid xenon time projection chambers are promising detectors to search for
neutrinoless double beta decay (0), due to their response
uniformity, monolithic sensitive volume, scalability to large target masses,
and suitability for extremely low background operations. The nEXO collaboration
has designed a tonne-scale time projection chamber that aims to search for
0 of \ce{^{136}Xe} with projected half-life sensitivity of
~yr. To reach this sensitivity, the design goal for nEXO is
1\% energy resolution at the decay -value (~keV).
Reaching this resolution requires the efficient collection of both the
ionization and scintillation produced in the detector. The nEXO design employs
Silicon Photo-Multipliers (SiPMs) to detect the vacuum ultra-violet, 175 nm
scintillation light of liquid xenon. This paper reports on the characterization
of the newest vacuum ultra-violet sensitive Fondazione Bruno Kessler VUVHD3
SiPMs specifically designed for nEXO, as well as new measurements on new test
samples of previously characterised Hamamatsu VUV4 Multi Pixel Photon Counters
(MPPCs). Various SiPM and MPPC parameters, such as dark noise, gain, direct
crosstalk, correlated avalanches and photon detection efficiency were measured
as a function of the applied over voltage and wavelength at liquid xenon
temperature (163~K). The results from this study are used to provide updated
estimates of the achievable energy resolution at the decay -value for the
nEXO design
Hypophosphatasia in children. Three faces of one disease
S.A. Boykov1, I.Yu. Chernyak1, N.S. Shatokhina1, E.Yu. Gurkina2, N.A. Borodina3, E.F. Chelabova3, S.A. Epoeva3
1Children’s Regional City Hospital, Krasnodar, Russian Federation
2V.A. Almazov National Medical Research Center, St. Petersburg, Russian Federation
3Children’s Hospital of the city of Armavir, Armavir, Russian Federation
Hypophosphatasia (HPP) is a rare multisystem inherited metabolic disorder caused by mutations in ALPL gene that encodes tissue nonspecific alkaline phosphatase responsible for bone mineralization. HPP is characterized by impaired bone mineralization, skeletal abnormalities, and systemic manifestations which result in significant morbidity and mortality. Clinical presentations of HPP vary greatly. Early (perinatal and infantile) HPP is characterized by the most severe symptoms, i.e., respiratory and neurological disorders are of crucial importance being the leading causes of death. Progressive skeletal impairment, rickets-like deformities, reduced mobility, and severe disability are typical of childhood-onset HPP. The biochemical hallmark of HPP is low alkaline phosphatase (ALP) activity. HPP diagnosis is verified by clinical symptoms in combination with persistently low ALP activity (adjusted for age and sex). Molecular genetic test to identify ALPL gene mutation is performed as needed. Three case reports addresses authors’ experience with the diagnosis and treatment for HPP.
Keywords: hypophosphatasia, case series, alkaline phosphatase, impaired bone mineralization, asfotase alfa.
For citation: Boykov S.A., Chernyak I.Yu., Shatokhina N.S. et al. Hypophosphatasia in children. Three faces of one disease. Russian Journal of Woman and Child Health. 2020;3(2):136–141. DOI: 10.32364/2618-8430-2020-3-2-136-141.
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Measurements of thermophoretic velocities of aerosol particles in microgravity conditions in different carrier gases
Measurements of the thermophoretic velocities of aerosol particles (paraffin) in different carrier gases (helium, nitrogen, argon, xenon) were performed in microgravity conditions (the drop tower facility, in Bremen). The experiments permitted the study of thermophoresis in conditions which minimize the impact of gravity.
Monodisperse aerosol particles were observed through a digital holographic velocimeter, a device allowing the determination of 3-D coordinates of particles in the viewing volume. Particle trajectories, and consequently particle velocities, were reconstructed by analysing the sequence of particle positions. We successfully observed thermophoretic velocities in low-gravity conditions. The experiments show that the thermophorefic velocity decreases from helium (He) to nitrogen (N-2), argon (At), and xenon (Xe)
Evolution of Oxygen–Ion and Proton Conductivity in Ca-Doped Ln2Zr2O7 (Ln = Sm, Gd), Located Near Pyrochlore–Fluorite Phase Boundary
Sm2−xCaxZr2O7−x/2 (x = 0, 0.05, 0.1) and Gd2−xCaxZr2O7−x/2 (x = 0.05, 0.1) mixed oxides in a pyrochlore–fluorite morphotropic phase region were prepared via the mechanical activation of oxide mixtures, followed by annealing at 1600 °C. The structure of the solid solutions was studied by X-ray diffraction and refined by the Rietveld method, water content was determined by thermogravimetry (TG), their bulk and grain-boundary conductivity was determined by impedance spectroscopy in dry and wet air (100–900 °C), and their total conductivity was measured as a function of oxygen partial pressure in the temperature range: 700–950 °C. The Sm2−xCaxZr2O7−x/2 (x = 0.05, 0.1) pyrochlore solid solutions, lying near the morphotropic phase boundary, have proton conductivity contribution both in the grain bulk and on grain boundaries below 600 °C, and pure oxygen–ion conductivity above 700 °C. The 500 °C proton conductivity contribution of Sm2−xCaxZr2O7−x/2 (x = 0.05, 0.1) is ~ 1 × 10−4 S/cm. The fluorite-like Gd2−xCaxZr2O7−x/2 (x = 0.1) solid solution has oxygen-ion bulk conductivity in entire temperature range studied, whereas proton transport contributes to its grain-boundary conductivity below 700 °C. As a result, of the morphotropic phase transition from pyrochlore Sm2−xCaxZr2O7−x/2 (x = 0.05, 0.1) to fluorite-like Gd2−xCaxZr2O7−x/2 (x = 0.05, 0.1), the bulk proton conductivity disappears and oxygen-ion conductivity decreases. The loss of bulk proton conductivity of Gd2−xCaxZr2O7−x/2 (x = 0.05, 0.1) can be associated with the fluorite structure formation. It is important to note that the degree of Ca substitution in such solid solutions (Ln2−xCax)Zr2O7−δ (Ln = Sm, Gd) is low, x < 0.1. In both series, grain-boundary conductivity usually exceeds bulk conductivity. The high grain-boundary proton conductivity of Ln2−xCaxZr2O7−x/2 (Ln = Sm, Gd; x = 0.1) is attributable to the formation of an intergranular CaZrO3-based cubic perovskite phase doped with Sm or Gd in Zr sublattice