Lafora Disease Masquerading as Hepatic Dysfunction

Lafora disease is fatal intractable progressive myoclonic epilepsy. It is frequently characterized by epileptic seizures, difficulty walking, muscle spasms, and dementia in late childhood or adolescence. We chronicle here an unusual case of an asymptomatic young male soccer player who presented with elevated liver enzymes. Neurological examination was unremarkable. The diagnostic workup for hepatitis, infectious etiologies, autoimmune disorders, hemochromatosis, Wilson\u27s disease, alpha-1 antitrypsin deficiency, and other related diseases was inconclusive. He subsequently underwent an uneventful percutaneous liver biopsy. Based on the pathognomonic histopathological findings, Lafora disease was considered the likely etiology. The present study is a unique illustration of this rare disorder initially manifesting with abnormal liver enzymes. It underscores the importance of clinical suspicion of Lafora disease in cases with unexplained hepatic dysfunction. Prompt liver biopsy and genetic testing should be performed to antedate the onset of symptoms in these patients

Construction and measurements of a vacuum-swing-adsorption radon-mitigation system

Long-lived alpha and beta emitters in the $^{222}$Rn decay chain on (and near) detector surfaces may be the limiting background in many experiments attempting to detect dark matter or neutrinoless double-beta decay, and in screening detectors. In order to reduce backgrounds from radon-daughter plate-out onto the wires of the BetaCage during its assembly, an ultra-low-radon cleanroom is being commissioned at Syracuse University using a vacuum-swing-adsorption radon-mitigation system. The radon filter shows ~20$\times$ reduction at its output, from 7.47$\pm$0.56 to 0.37$\pm$0.12 Bq/m$^3$, and the cleanroom radon activity meets project requirements, with a lowest achieved value consistent with that of the filter, and levels consistently < 2 Bq/m$^3$.Comment: 5 pages, 3 figures, Proceedings of Low Radioactivity Techniques (LRT) 2013, Gran Sasso, Italy, April 10-12, 201

Penerapan Metode Electrical Resistivity Tomography (Ert) Untuk Mengetahui Bidang Longsor Pada Model Lereng

Longsoran yang terjadi pada lereng merupakan salah satu permasalahan utama di bidang geoteknik. Untuk melakukan perbaikan maupun perkuatan pada lereng perlunya dilakukan penyelidikan tanah guna memprediksi bidang longsor pada lereng tersebut sehingga perbaikan dan perkuatan yang dilakukan dapat dilakukan secara efektif. Salah satu alternatif metode yang dapat dipakai adalah penggunan metode geofisika, seperti geolistrik khususnya Electrical Resistivity Tomography (ERT). Penyelidikan ini diwujudkan dengan dembuatan suatu model fisik lereng dengan variasi keretakan dan diberikan pembebanan sebanyak 5 macam pembebanan. Tujuan utama dari penelitian ini adalah untuk mengetahui penggunaan metode penyelidikan geolistrik untuk mengetahui bidang longsor. Berdasarkan penelitian ini bidang longsor ataupun retakan terdapat pada lapisan dengan nilai resistivitas yang memiliki nilai resistivitas berbeda cukup signifikan

Trends in the availability and usage of electrophysical agents in physiotherapy practices from 1990 to 2010: A review

This is the Pre-print version of the Article. The official published version can be accessed from the link below - Copyright @ 2012 Maney PublishingBackground: The use of electrophysical agents has a historically important role in physiotherapy practice. There are anecdotal reports that the availability and usage of electrotherapy modalities are declining, which may have implications for physiotherapy practice. The aim of this literature review was to provide scientific evidence on electrotherapy usage in the last 20 years by identifying trends in availability, use, and non-use of nine electrotherapeutic modalities in physiotherapy practices during 1990s and 2000s. Methods: Review of empirical studies published in the English language from 1990 to 2010 and identified through searching online bibliographic databases, which included: Medline/OvidSP, PubMed Central, CINAHL/EBSCOhost, ScienceDirect, Scopus, ISI Web of Science, and Google Scholar. Findings: In the last 20 years, ultrasound availability and usage show increasing trends in several countries. The availability and use of pulsed shortwave diathermy and laser have shown steady trends. Transcutaneous electrical nerve stimulation, interferential, and biofeedback availability and usage have shown increasing trends in the UK and decreasing trends in Australia and the Republic of Ireland. Trends of continuous shortwave diathermy availability and use are declining irrespective of the country of the study. The availability and usage of microwave diathermy and H-wave show steeply declining trends, while there is a sharp rise in their non-availability over the last several years. Conclusions: The availability and use of electrophysical agents have greatly changed in the last 20 years. Declining trends in the availability and usage along with increasing trend of non-availability of electrotherapy modalities may have implications for electrotherapy education, training, and practice in the coming years.This study was funded by Health & Safety Executive, UK (grant no. 4371/R47.022)

Geographical Concentration of Rural Poverty in Bangladesh

This paper was presented at the dialogue on Mapping Poverty for Rural Bangladesh: Implications for Pro-poor Development. The dialogue was organised as part of CPD's ongoing agricultural policy research and advocacy activities with IRRI under the PETRRA project. The study reported geographical concentration of rural poverty in Bangladesh for 425 upazilas in 2000-01. The study measured and mapped incidence of poverty (using Headcount Index), intensity of poverty (using Poverty Gap Index) and severity of poverty (using Squared Poverty Gap Index). It has analyzed factors contributing to the spatial concentration of poverty. It is hoped that the findings of the study would be helpful in identifying target areas and priorities for agricultural R&D interventions and poverty reduction programmes.Poverty, Rural Poverty, Bangladesh

Proper Weyl Collineations in Kantowski-Sachs and Bianchi Type III Space-Times

A study of proper Weyl collineations in Kantowski-Sachs and Bianchi type III space-times is given by using the rank of the 6X6 Weyl matrix and direct integration techniques. Studying proper Weyl collineations in each of the above space-times, it is shown that there exists no such possibility when the above space-times admit proper Weyl collineations.Comment: 5 page

Effect of Food Quality on Customer Perceived Satisfaction Level and Mediating Effect of Food Safety on Them

Purpose:We done a study to knownnbsp impact of food safety on food quality and customerrsquos satisfaction and the purpose of our study to know how much people are concerned about safety of food what they eat in their routine life. We used questionnaire to get results and our target group is students of UET. Findings:We got to know that food safety has mediating effect on food quality and customerrsquos satisfaction and people are concerned about what they eat is either safe or not and pay attention to what adds up in their food and what they engulf in eating. Food producers and restaurants must pay attention to their food processing procedures and home cooking persons should make sure about healthy food items. Limitations:All respondents are belong to one institution. Other researcher can add respondents of many demographics.nbsp nbs

INDIGO : better geomagnetic observatories where we need them

The INDIGO project aims to improve the global coverage of digital observatories by deploying digital magnetometer systems in: i) Observatories where existing analog recording equipment is in need of upgrading. ii) Newly established digital observatories. iii) Existing digital observatories for the purpose of quality control and redundancy. In implementing the project and selecting suitable sites, special attention is paid to parts of the Earth devoid of magnetic observatories, increasing the reliability and long-term operation of existing observatories and cost-effective use of local resources. The Poster reviews the current status of the project. We examine the different steps and initiatives taken since the initiation of INDIGO in 2004 and assess their effectiveness in achieving progress towards our aims of improving global coverage and enhanced data quality