The Russian version of the Juvenile Arthritis Multidimensional Assessment Report (JAMAR)

The Juvenile Arthritis Multidimensional Assessment Report (JAMAR) is a new parent/patient-reported outcome measure that enables a thorough assessment of the disease status in children with juvenile idiopathic arthritis (JIA). We report the results of the cross-cultural adaptation and validation of the parent and patient versions of the JAMAR in the Russian language. The reading comprehension of the questionnaire was tested in 10 JIA parents and patients. Each participating centre was asked to collect demographic, clinical data and the JAMAR in 100 consecutive JIA patients or all consecutive patients seen in a 6-month period and to administer the JAMAR to 100 healthy children and their parents. The statistical validation phase explored descriptive statistics and the psychometric issues of the JAMAR: the three Likert assumptions, floor/ceiling effects, internal consistency, Cronbach\u2019s alpha, interscale correlations, test\u2013retest reliability, and construct validity (convergent and discriminant validity). A total of 100 JIA patients (25% systemic, 19% oligoarticular, 38% RF-negative polyarthritis, 18% other categories) and 198 healthy children, were enrolled in two centres. The JAMAR components discriminated healthy subjects from JIA patients. All JAMAR components revealed good psychometric performances. In conclusion, the Russian version of the JAMAR is a valid tool for the assessment of children with JIA and is suitable for use both in routine clinical practice and clinical research

ІННОВАЦІЙНІ НАПРЯМКИ РОЗВИТКУ ХІМІЧНОЇ І ХАРЧОВОЇ ІНЖЕНЕРІЇ

The materials are presented to inform about the XVIII International Scientific and Practical Conference Integrated Technologies and Energy Saving "ITE-2018", Ukraine, in November 2018, which was initiated by representatives of the European Federation of Chemical Engineering (EFCE) and the Ukrainian Association of Chemical and Food Engineering (CFE-UA ) and is dedicated to the 85th anniversary of the establishment of the department of integrated technologies, processes and devices (ITPA) NTU «KhPI». A unique opportunity is provided for companies, organizations, teachers, researchers, members of EFCE and CFE-UA to contribute to the development and solution of modern and progressive scientific and technical issues related to chemical and food technology, as well as chemical engineering, in order to solve global tasks of modernity. The materials of the innovative developments of the department (ITPA) NTU «KhPI» are presented in the form of a unique interactive software package that allows you to design flow diagrams of complex heat exchange systems with energy consumption close to the thermodynamically reasonable minimum. The use of the developed methods also makes it possible to estimate the energy-saving potential and the potential to reduce harmful emissions not only from enterprises, but also from large industrial complexes.В статье приведена информация о ХVIII международной научно-практической конференции Интегрированные технологии и энергосбережение «ИТЭ-2018», Украина, в ноябре 2018, которая проведена по инициативе представителей Европейской федерации химической инженерии (EFCE) и Украинской ассоциации химической и пищевой инженерии (CFE -UA) и посвящена 85 годовщине со дня образования кафедры интегрированных технологий, процессов и аппаратов (ИТПА) НТУ «ХПИ». Предоставлена уникальная возможность для компаний, организаций, преподавателей, научных сотрудников, членов EFCE и CFE -UA внести свой вклад в развитие и решение современных и прогрессивных научных и технических вопросов, связанных с химической и пищевой технологии, а также химическим машиностроением, с целью решения глобальных задач современности. Представлены материалы инновационных разработок кафедры (ИТПА) НТУ «ХПИ» в виде уникального пакета интерактивного математического обеспечения, который позволяет проектировать технологические схемы сложных теплообменных систем с потреблением энергии, близкой к термодинамически обоснованному минимуму.У статті наведено інформацію про ХVIII міжнародну науково-практичну конференцію Інтегровані технології та енергозбереження «ІТЕ-2018», Україна, в листопаді 2018 року, яка проведена за ініціативою представників Європейської федерації хімічної інженерії (EFCE) і Української асоціації хімічної та харчової інженерії (CFE-UA) та присвячена 85 річниці з дня утворення кафедри інтегрованих технологій, процесів та апаратів (ІТПА) НТУ «ХПІ». Надана унікальна можливість для компаній, організацій, викладачів, науковців, членів EFCE  та CFE -UA внести свій вклад в розвиток і рішення сучасних і прогресивних наукових та технічних питань, пов'язаних з хімічною та харчовою технологіями, а також хімічним машинобудуванням, з метою вирішення глобальних завдань сьогодення. Представлено матеріали інноваційних розробок кафедри (ІТПА) НТУ «ХПІ» у вигляді унікального пакету інтерактивного математичного забезпечення, який дозволяє проектувати технологічні схеми складних теплообмінних систем зі споживанням енергії, що близька до термодинамічно-обґрунтованого мінімуму

EARLY CONGENITAL SYPHILITIC PSEUDOPARALYSIS (PARROT’S DISEASE): A CLINICAL CASE

Background. Congenital syphilis is a severe intrauterine infection which, affecting most of the organs and systems of a child, can lead to his disability. However, it is extremely difficult to suspect congenital syphilis in a child in the absence of information about prior syphilis in his mother. The article presents a case of a monosymptomatic clinical picture of early congenital syphilis.Description of the Clinical Case. At the age of 1 month, the child had hyperemia, isolated edema of the right forearm, and restriction of limb movements. He was examined by a pediatrician who suspected a fracture of the forearm bones. X-ray did not show any fracture. The situation was regarded as an allergic reaction; desensitizing therapy was prescribed during which the range of movements in the right arm slightly increased. At the age of 2 months, there was a decrease in the range of movements in the left arm. On admission, the condition was regarded as moderate one. No fever; no signs of intoxication. Skin and visible mucous membranes were not changed. Cardiopulmonary activity was satisfactory. The abdomen was palpable in all compartments, painless. The liver was enlarged 6 cm, of dense consistency. The spleen was enlarged 5 cm. Bowel and bladder functions were normal. Neurological status: the reaction to examination was adequate, emotional cry. Cranial nerves without pathology. Can see and hear. Restricted range of movements in the arms; passive movements were painful. Muscle tone in the arms was low, in the legs — closer to physiological one. Equal and brisk tendon reflexes from the arms and legs. Large fontanel 1.5[1]1.5 cm, not protruded. X-ray examination of the forearm bones showed a change in the structure of the epiphyses of both forearm bones that was common to syphilitic osteochondritis.Conclusion. The article describes the complexity of diagnosis of early congenital syphilis in a child aged 2 months in the absence of a corresponding anamnesis in his mother. The need to rule out syphilitic infection in infants with motor impairments, born from unexamined mothers, has been emphasized

Proceedings Of The 23Rd Paediatric Rheumatology European Society Congress: Part Two

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