Atypical Neuroimaging Manifestations of Linear Scleroderma “en coup de sabre”

How to Cite This Article: Allmendinger AM, Ricci JA, Desai NS, Viswanadhan N, Rodriguez D. Atypical Neuroimaging Manifestations of Linear Scleroderma “en coup de sabre”. Iran J Child Neurol. Summer 2015;9(3):62-68.AbstractLinear scleroderma “en coup de sabre” is a subset of localized sclerodermawith band-like sclerotic lesions typically involving the fronto-parietal regionsof the scalp. Patients often present with neurologic symptoms. On imaging,patients may have lesions in the cerebrum ipsilateral to the scalp abnormality.Infratentorial lesions and other lesions not closely associated with the overlyingscalp abnormality, such as those found in the cerebellum, have been reported,but are extremely uncommon. We present a case of an 8-year-old boy with a left fronto-parietal “en coup de sabre” scalp lesion and describe the neuroimaging findings of a progressively enlarging left cerebellar lesion discovered incidentally on routine magnetic resonance imaging. Interestingly, the patient had no neurologic symptoms given the size of the mass identified

Affordability targets: Implications for Housing Supply

This report presents the results of an econometric modelling project, concerned with regional housing affordability, conducted for the ODPM between November 2004 and April 2005. The key outputs of the project are not just this report, but the model itself, the details of which are set out in the accompanying Technical Appendix, available via the ODPM website: www.odpm.gov.uk/housing. The team for the project was large, including fifteen individuals from nine organisations. The project was directed from the University of Reading. In addition to the team, the work was improved by help from an advisory group and a user group, consisting of members drawn from both central government and from the wider academic and policy communities

CT and MR imaging of Susac syndrome in a young male presenting with acute disorientation.

Susac syndrome is a rare neurologic disorder first described by Susac et al. in 1979. Clinically, Susac syndrome consists of a triad including encephalopathy, branch retinal artery occlusion, and sensorineural hearing loss. Microinfarction is believed to be the basic histologic feature and MR is considered the best imaging modality. This case documents the typical imaging findings of Susac syndrome, as well as the unique MR imaging finding of cranial nerve enhancement

Atypical spine involvement of Erdheim-Chester disease in an elderly male.

Erdheim-Chester disease is a rare form of non-Langerhans histiocytosis presenting in the 5th through 7th decades of life. Osseous manifestations include symmetrical sclerosis of the long bones and, rarely, the spine. Central nervous system disease commonly affects the white matter tracts as well as the orbits, but epidural disease is rare. To the best of the authors\u27 knowledge, simultaneous epidural and skeletal spine disease has not been reported. The MR imaging characteristics of skeletal spine disease have also not been reported. The authors describe the case of an 87-year-old man with both epidural and skeletal spine disease. The clinical characteristics, imaging manifestations, and the histological features are discussed

Imaging manifestations of malignant neoplasia mimicking pyogenic osteodiscitis.

Malignant neoplasia involving contiguous vertebrae and the corresponding intervertebral discs is a rare occurrence that has similar imaging manifestations as pyogenic osteodiscitis. The authors describe the imaging manifestations of two cases of malignant neoplasia mimicking pyogenic osteodiscitis. We present a case of an 83-year-old male with metastatic non-small cell lung carcinoma and an 82-year-old female with a plasmacytoma, both within the thoracic spine. These cases illustrate how the imaging features of pyogenic osteodiscitis may parallel those of malignant neoplasia

Approaches to ultra-low radiation dose coronary artery calcium scoring based on 3rd generation dual-source CT: A phantom study

Objectives: To investigate to what extent 3rd generation dual-source computed tomography (DSCT) can reduce radiation dose in coronary artery calcium scoring. Methods: Image acquisition was performed using a stationary calcification phantom. Prospectively electrocardiogram (ECG)-triggered 120 kV sequential, and 120 and Sn100 kV ultra-high pitch (UHP) acquisitions were performed with different tube currents (80, 60, 40, 20 mA). Images were reconstructed using filtered back projection (FBP) and 3rd generation iterative reconstruction (IR). Contrast-to-noise ratio (CNR), Agatston score, calcium volume, and radiation dose were assessed. For statistical analysis Friedman tests and Wilcoxon rank sum tests were used. Results: Even at reduced tube currents, the three acquisition techniques did not show significant differences in Agatston score (p = 0.4) or calcium volume (p = 0.08) with FBP reconstruction. Calcium volumes were significantly lower for 3rd generation IR compared to FBP reconstructions (p <0.01). CTDIvol for the 120 kV sequential, 120 and Sn100 kV UHP acquisitions at 80 and 20 mA were 1.2-0.37, 0.48-0.17, and 0.07-0.02 mGy, respectively. Conclusion: 3rd generation DSCT enabled a reduction of tube current in both the sequential and UHP acquisitions without significantly affecting coronary calcium scoring. Tin filtered 100 kV scanning may allow accurate quantification of calcium score without correction of the HU threshold. (C) 2015 Elsevier Ireland Ltd. All rights reserved

Power and Politics in Marine Spatial Planning

There is growing concern that MSP is not facilitating a paradigm shift towards democratic marine management and that it may simply repackage old power dynamics in the rhetoric of participation. MSP has been advanced using the logic of 'rationality' and 'post-political' forms of planning that emphasise consensus and managerial-technological apparatuses for the governance of socio-political natural spaces. MSP has been described as the rational organization of the use of marine space. Rationality is, however, context dependent and the context of rationality is power. MSP processes are, therefore, arenas where specific and multiple instances of power manifests itself. MSP is also an inherently political (sensu Mouffee, 2005) process. Rather than acknowledging debate and dissensus, MSP is advanced as a neutral, participatory process that can develop win-win outcomes. The result is a choreographed form of governance and participation, with clearly defined roles, processes and acceptable outcomes, which renders invisible the politics of disagreement and legitimises the agendas of dominant actors. This chapter argues that to recapture its democratising potential, MSP requires explicit engagement with power and politics. Document type: Part of book or chapter of boo