Complete heart block in thalassemia major: A case report

PubMedID: 12405443Cardiac complications of iron overload are the most common cause of death in patients with thalassemia major. These complications include recurrent pericarditis, refractory congestive heart failure and rhythm disorders. The usual rhythm disturbances are supraventricular or ventricular premature contractions and first-or second-degree heart block. Complete heart block is a very rare complication of thalassemia major. Herein, we report a case of complete heart block with thalassemia major. The patient also had serious congestive heart failure. Management of the heart block with pacemaker brought no clinical improvement, and she died in the second month of hospitalization

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Temporary atrioventricular complete block that develops following the transcatheter closure of ventricular septal defect

PubMedID: 22397051Atrioventricular (AV) block is a potential risk after transcatheter closure of perimembranous ventricular septal defect (VSD) with the Amplatzer perimembranous device. We present herein a case of a 6.5-year-old female patient who developed complete AV block six days after closure of VSD and recovered with steroid and salicylate treatment. It is important to be alert to the development of AV block after transcatheter perimembranous VSD closure. Very careful monitoring of rhythm is mandatory during the short- and long-term follow-up

Successful medical treatment of fetal supraventricular tachycardia that cause hydrops fetalis [Hidrops fetalise neden olan fetal supraventriküler taşikardinin başarılı medikal tedavisi]

Supraventricular tachycardia (SVT) is the most frequent fetal tachyarrhythmia. Diagnosis is established with M-mode ultrasound and/or Doppler investigation. Untreated cases may develop fetal heart failure and hydrops. Even these cases should not be left untreated - maternal administration of antiarrhythmic drugs should be undertaken. In this manuscript, we describe a successful treatment with maternal administration of sotalol and digoxin in a fetus that developed hydrops because of SVT. © 2014 Turkish Society of Obstetrics and Gynecology. All rights reserved

Transcatheter closure of post-myocardial infarction muscular ventricular septal rupture: Case report [Miyokard infarktüsü sonrasi geli?en musküler ventriküler septal rüptürün transkateter yöntemle kapatilmasi]

Muscular ventricular septal rupture (VSR) is a serious and life threatening complica tion of acute myocardial infarction. It is usually occurs within the first one week after infarction. Today, the recommended treatment is surgical closure. Another treatment option is transcatheter closure method. In this report, we present a patient who is applied transcatheter closure due to post myocardial infarction muscular VSR associated with refractory heart failure. Copyright © 2013 by Türkiye Klinik leri

Left Ventricular Thrombosis Due to Acquired Protein C Deficiency Diagnosed by Two-Dimensional Echocardiography

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Long-term follow-up of 799 children with isolated ventricular septal defects [İzole ventriküler septal defektli 799 çocugun uzun süreli takibi]

PubMedID: 22395370Objectives: We evaluated long-term follow-up results and prognosis of pediatric patients with isolated ventricular septal defects (VSD). Study design: The study included 799 patients (368 girls, 431 boys; mean age at diagnosis 24.3±37.4 months; median 6 months) who were monitored by the pediatric cardiology department for VSD. The mean follow-up period was 32.8±30.3 months (median 20 months). Results: The VSDs were classified as perimembranous (n=610, 76.4%), muscular (n=171, 21.4%), doubly committed subarterial (n=10, 1.3%), and multiple (n=8, 1%). Spontaneous closure rates were 42.7%, 13.1%, and 25% in muscular, perimembranous, and multiple VSDs, respectively, which corresponded to a mean age of 18.6±19.9 months (median 12 months) in muscular and 30.2±33.7 months (median 14.5 months) in perimembranous VSDs. Before 2 years of age, 78.1% of muscular and 58.6% of perimembranous VSDs underwent spontaneous closure. Of 256 defects (32%) that required surgical closure, 91.4% were of perimembranous location. The mean age at surgery was 38.8±49.1 months (median 11 months) for muscular, and 43.7±40.9 months (median 24 months) for perimembranous defects. During the follow-up period, the following complications were noted: aortic valve prolapse (0.7%), aortic regurgitation (0.6%), left ventricle-to-right atrium shunt (2.6%), subaortic ridge (3.7%), and infundibular stenosis (1.2%). Aortic regurgitation developed in eight patients (3.7%) after surgical closure. Conclusion: Our data on the natural course and prognosis of VSDs may be of relevance with respect to patients'age, defect type, and complications encountered in the follow-up period. © 2012 Türk Kardiyoloji Dernegi

Power spectral analysis of heart rate variability in children with aortic stenosis

PubMedID: 12026197Aortic stenosis is a progressive disorder and can be the cause of serious arrhythmias and possibly sudden death. Evaluation and follow-up of the autonomic nervous system may provide some useful information for management of the disease. Our study aimed to examine heart rate variability in children with aortic stenosis in the supine position and to detect the changes in autonomic activity during head-up tilt testing. Sixteen patients and 11 healthy controls participated in the study. In the supine position, seven minutes of continuous echocardiographic (ECG) recording was performed, followed by four consecutive ECG recordings, each consisting of seven minutes in 70° tilt position. To obtain power spectrums, the tachograms were taken on the autoregressive mode. The mean RR interval duration, standard deviation of RR interval, central frequencies of low and high frequency oscillations, their powers, total power and percents of normalized low and high frequency powers were accepted for statistics. There were no significant differences between the groups in the supine position. In tilt position, mean RR interval and its standard deviation were decreased in both groups. The central frequency of low freuquency power significantly (p < 0.05) shifted to left, normalized low frequency power increased and normalized high frequency power decreased in the control group at the beginning of tilt position, but at the second phase of tilt position in the patient group. We conclude from the results that children with mild-to-moderate aortic stenosis reflect delayed response to sympathetic provocation

Ortner's Syndrome caused by ductus arteriosus aneurysm

PubMedID: 27372626[No abstract available

The right ventricular outflow tract reconstruction with "Contegra™ VenPro" heterologous conduit in the ross procedure [Ross Prosedüründe "Contegra™ VenPro" Kapakli Heterogreft Konduit Kullanilarak Sag Ventrikül Çikim Yolu Rekonstrüksiyonu]

PubMedID: 15033624[No abstract available