Ectodermal dysplasia is a hereditary disorder that occurs as a consequence of disturbances in
the ectoderm of the developing embryo. The triad of nail dystrophy, alopecia or hypotrichosis and palmoplantar
hyperkeratosis is usually accompanied by a lack of sweat glands and a partial or complete absence of primary and/
or permanent dentition. A case report illustrating the prosthetic rehabilitation of a seven year old boy with hypohidrotic ectodermal dysplasia associated with total anodontia is presented
