2 research outputs found
Segmental anhidrosis with hyporeflexia associated with congenital spinal deformity: A Ross's syndrome variant or inverse Horner's syndrome?
A 39-year-old soldier presented with anhidrosis affecting both upper
extremities below the shoulders, the right side of the trunk below the
third rib in front and the third vertebra on the back, and the left
lower extremity below the inguinal ligament since 1992. Ten years later
in 2002, he was also found to have bilateral absence of Achilles reflex
and decreased right knee jerk. In addition, the patient was found to
have congenital spinal abnormalities in the form of block of vertebrae
C3-C4; decreased disc space C4-C5; and break in pars interarticularis
L5-S1 with decreased disc space. A total of seven cases of Ross
syndrome, Holmes-Adie syndrome (tonic pupil with lost tendon jerks)
with segmental anhidrosis, have been described in the literature. Our
case, however, did not have any pupillary abnormality. A case of
progressive isolated segmental anhidrosis has also been described. The
association of congenital spinal abnormality, which may be
pathognomonic in the causation of this progressive sudomotor
degeneration, is quite interesting in our case. The distribution of
anhidrosis on the right side is just below the level of sweating loss
sometimes described in lesions of superior sympathetic cervical
ganglion in Horner's syndrome