9 research outputs found
Summary of worldwide pediatric malignancies reported after exposure to etanercept
- Author
- Publication venue
- BioMed Central
- Publication date
- 01/01/2010
- Field of study
Agrin Binds BMP2, BMP4 and TGFβ1
- Author
- A Hrus
- A Nagy
- B Zhang
- Bostjan Kobe
- DV Tortoriello
- E Porten
- G Bezakova
- H Wu
- I Ksiazek
- J Harrow
- JI Moon
- JJ Hill
- JJ Hill
- JL Bixby
- K Baerwald-de la Torre
- K Kondás
- K Matsumoto-Miyai
- K Tsuchida
- L Nieba
- L Patthy
- L Patthy
- L Zilberberg
- László Bányai
- László Patthy
- M Abe
- M Annies
- M Srivastava
- MA Larkin
- N Kim
- P Bork
- P Scotton
- P Sonderegger
- Peter Sonderegger
- R Reif
- S McCroskery
- S McCroskery
- SJ Lee
- T Nakamura
- TT Kummer
- Y Sidis
- Z Feng
- Publication venue
- Public Library of Science
- Publication date
- 01/01/2010
- Field of study
The C-terminal 95 kDa fragment of some isoforms of vertebrate agrins is sufficient to induce clustering of acetylcholine receptors but despite two decades of intense agrin research very little is known about the function of the other isoforms and the function of the larger, N-terminal part of agrins that is common to all isoforms. Since the N-terminal part of agrins contains several follistatin-domains, a domain type that is frequently implicated in binding TGFβs, we have explored the interaction of the N-terminal part of rat agrin (Agrin-Nterm) with members of the TGFβ family using surface plasmon resonance spectroscopy and reporter assays. Here we show that agrin binds BMP2, BMP4 and TGFβ1 with relatively high affinity, the KD values of the interactions calculated from SPR experiments fall in the 10−8 M–10−7 M range. In reporter assays Agrin-Nterm inhibited the activities of BMP2 and BMP4, half maximal inhibition being achieved at ∼5×10−7 M. Paradoxically, in the case of TGFβ1 Agrin N-term caused a slight increase in activity in reporter assays. Our finding that agrin binds members of the TGFβ family may have important implications for the role of these growth factors in the regulation of synaptogenesis as well as for the role of agrin isoforms that are unable to induce clustering of acetylcholine receptors. We suggest that binding of these TGFβ family members to agrin may have a dual function: agrin may serve as a reservoir for these growth factors and may also inhibit their growth promoting activity. Based on analysis of the evolutionary history of agrin we suggest that agrin's growth factor binding function is more ancient than its involvement in acetylcholine receptor clustering
Association between drug intake and incidence of malignancies in patients with Juvenile Idiopathic Arthritis: a nested case–control study
- Author
- A Klein
- A Mantovani
- Betty Bisdorff
- BL Nordstrom
- Boris Hügle
- E Baecklund
- F Wolfe
- FH Prince
- GR Burmester
- GT Ostring
- Hartmut Michels
- J Klotsche
- Jenny Schlichtiger
- JF Simard
- Johannes-Peter Haas
- K Minden
- Katja Radon
- M Galanski
- M Hooper
- ML Mannion
- N Ruperto
- P Diak
- P McCroskery
- PJ Hashkes
- S Bernatsky
- Swaantje Barth
- T Beukelman
- V Ivancevic
- Y Dincer
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Cutaneous Adverse Events in the Randomized, Double-Blind, Active-Comparator DECIDE Study of Daclizumab High-Yield Process Versus Intramuscular Interferon Beta-1a in Relapsing-Remitting Multiple Sclerosis
- Author
- A Menter
- AB Gottlieb
- Adam Friedman
- B Bielekova
- B Bielekova
- CH Polman
- DJ Huss
- DY Leung
- E Guttman-Yassky
- EJ Freyschmidt
- Firas Hougeir
- H Wiendl
- I Cortese
- J Elkins
- J Oh
- Jacob Elkins
- James G. Krueger
- JM Hanifin
- JS Margolis
- JW Rose
- L Kappos
- L McEwan
- Leon Kircik
- LF Eichenfield
- LJ Edwards
- M Girardi
- MA Lowes
- Marianne Sweetser
- Nisha Lucas
- Peter McCroskery
- R Gold
- R Sidbury
- RA Clark
- RB Nussenblatt
- RJ Hay
- SH Kardaun
- Steven J. Greenberg
- SV Ramagopalan
- T Bieber
- TA Waldmann
- U Oh
- Wanda Castro-Borrero
- Xiaojun You
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Stimulation of procollagenase synthesis in human rheumatoid synovial fibroblasts by mononuclear cell factor/interleukin 1
- Author
- Publication venue
- 'Elsevier BV'
- Publication date
- Field of study
Impact of repeated bouts of eccentric exercise on myogenic gene expression
- Author
- A Mauro
- AC McPherron
- AC McPherron
- Andreas Costa
- Armand Anne-Sophie
- AZ Jamurtas
- B Langley
- BM Wentworth
- CS Bickel
- CS Bickel
- D Joulia
- D Peters
- DJ Mahoney
- DS Willoughby
- E Endl
- E Endl
- F Haddad
- H Li
- H Lin
- Hargita Hegyesi
- Hicham Dalloul
- J Hill
- J Kim
- JE Dominique
- Jozsef Tihanyi
- K Nosaka
- L Mendler
- LA Megeny
- Levente Racz
- M Hameed
- M Shibata
- Mark Vaczi
- N Psilander
- Peter Apor
- S Bogdanovich
- S McCroskery
- S McCroskery
- SBP Charge
- SM Roth
- T Launay
- T Scholzen
- TC Chen
- TC Chen
- U Proske
- WS Bullough
- Y Yang
- Z Yan
- Zsolt Csende
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Dual exon skipping in myostatin and dystrophin for Duchenne muscular dystrophy
- Author
- A Aartsma-Rus
- A Aartsma-Rus
- A Aartsma-Rus
- A Aartsma-Rus
- A Aartsma-Rus
- A Aartsma-Rus
- A Aartsma-Rus
- A Clop
- A Matsakas
- A Rebbapragada
- AC McPherron
- AC McPherron
- Annemieke Aartsma-Rus
- AP Monaco
- AY Manzur
- B Langley
- B Zhao
- C McFarlane
- C Qiao
- C Trollet
- CH Zhu
- CJ Mann
- CM Liu
- David JJ de Gorter
- Dwi U Kemaladewi
- GD Shelton
- Gert Jan B van Ommen
- GJ van Ommen
- H Amthor
- HA Heemskerk
- HM Blau
- J Dumonceaux
- JC van Deutekom
- JK Kang
- Johan T den Dunnen
- KR Wagner
- LS Krivickas
- M Bremmer-Bout
- M Kinali
- M Schuelke
- M Thomas
- N Yoshida
- Peter AC 't Hoen
- Peter ten Dijke
- R Rios
- RF Le
- S Bogdanovich
- S Bogdanovich
- S McCroskery
- Samuel Terlouw
- Sandra H van Heiningen
- SJ Lee
- SJ Lee
- TA Souza
- TJ Hawke
- TR Magee
- WE Taylor
- Willem MH Hoogaars
- Y Tang
- ZB Li
- Publication venue
- BMC
- Publication date
- 01/01/2011
- Field of study
<p>Abstract</p> <p>Background</p> <p>Myostatin is a potent muscle growth inhibitor that belongs to the Transforming Growth Factor-β (TGF-β) family. Mutations leading to non functional myostatin have been associated with hypermuscularity in several organisms. By contrast, Duchenne muscular dystrophy (DMD) is characterized by a loss of muscle fibers and impaired regeneration. In this study, we aim to knockdown myostatin by means of exon skipping, a technique which has been successfully applied to reframe the genetic defect of dystrophin gene in DMD patients.</p> <p>Methods</p> <p>We targeted myostatin exon 2 using antisense oligonucleotides (AON) in healthy and DMD-derived myotubes cultures. We assessed the exon skipping level, transcriptional expression of myostatin and its target genes, and combined myostatin and several dystrophin AONs. These AONs were also applied in the <it>mdx </it>mice models via intramuscular injections.</p> <p>Results</p> <p>Myostatin AON induced exon 2 skipping in cell cultures and to a lower extent in the <it>mdx </it>mice. It was accompanied by decrease in myostatin mRNA and enhanced <it>MYOG </it>and <it>MYF5 </it>expression. Furthermore, combination of myostatin and dystrophin AONs induced simultaneous skipping of both genes.</p> <p>Conclusions</p> <p>We conclude that two AONs can be used to target two different genes, <it>MSTN </it>and <it>DMD</it>, in a straightforward manner. Targeting multiple ligands of TGF-beta family will be more promising as adjuvant therapies for DMD.</p
Myostatin is a direct regulator of osteoclast differentiation and its inhibition reduces inflammatory joint destruction in mice
- Author
- A Korb-Pap
- AC McPherron
- Adelheid Korb-Pap
- Athanasios Stratis
- Berno Dankbar
- Christina Koers-Wunrau
- Corinna Wehmeyer
- CT Ritchlin
- Daniela Brunert
- Denise Beckmann
- DL Scott
- DR Bertolini
- E Kellum
- EK Nicholson
- EL Holzbaur
- G Schett
- GJ Inman
- GJ Martinez
- H Kaneto
- H Machida
- H Tsuboi
- J Keffer
- J Lam
- J Lin
- Jessica Bertrand
- K Fuller
- K Polzer
- K Redlich
- KR Wagner
- Kurt Redlich
- L Bradley
- Michelle Fennen
- MW Hamrick
- MW Hamrick
- MW Hamrick
- N Tani-Ishii
- NC Walsh
- P Bialek
- P Li
- PA Monach
- Peter Paruzel
- S McCroskery
- SE Lee
- Silvia Hayer
- SR Goldring
- SR Goldring
- Svetlana Frank
- T Sugatani
- Thomas Pap
- X Li
- Y Omata
- Y Suzuki
- Z Huang
- ZB Li
- ZH Lee
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Enzyme Handbook
- Author
- 339-349
- [10]Siffert O., Emöd, I.
- [11] Fricker L.D., Snyder, S.H.
- [11] Taylor A., Volz, K.W., Lipscomb, W.N., Takemoto, L. J.
- [3] Schmidt U., Weller, D., Holder, A.
- [9]Fujiwara K., Tsuru, D.
- [hie J.N., Dure, L.S.
- A Amory
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- A Marquet
- A Melo
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- A Moreno
- A Moriyama
- A Moriyama
- A Murai
- A Nicholson-Weller
- A Nordwig
- A Nordwig
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- A Ota
- A Pierre
- A Pähler
- A Radzicka
- A Reboul
- A Reboul
- A Rinne
- A Ritonja
- A Rosenberg
- A Sancar
- A Sharma
- A Soumarmon
- A Stockell
- A Storer
- A Suhar
- A Suzuki
- A Suzuki
- A Szewczuk
- A Szewczuk
- A Taylor
- A Taylor
- A Thomson
- A Traverso-Cori
- A Wolos
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- A Wolos
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- A Yaron
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- A Yaron
- A Yawetz
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- ATP Skrabanja
- AV Hoffbrand
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- B Asgeirsson
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- BY Hiraoka
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- C Nolan
- C Oliver
- C Pavoine
- C Rodriguez
- C Sampaio
- C Shing-Yang
- C Tetu
- C Tiruppathi
- C Torp-Pedersen
- C Vita
- C Watts
- C Wells
- C Yoshida
- C Zevaco
- C Zwizinski
- C Zwizinski
- C-H Wong
- C-M Lee
- C-S Chiu
- C-T Chang
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- CG Miller
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- CH Miller
- Chan. S.A.T., Jones, T.H.D., Sweeney, J.P., Toursarkissian, K.
- Chih-Min Kam Fujikawa, K.
- CJ Brandl
- CJ Chern
- CJ Decedue
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- T-C Wun
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- Xin-Ii Lin Wong, R.N.S., Tang, J.
- Y Agrawal
- Y Agrawal
- Y Atsumi
- Y Bai
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- Y Ethoh
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- Y Hojima
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- Y Kido
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- Y Nagai
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- Y Tsujita
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- “ (Turk V., Neville, M.
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- 01/01/1991
- Field of study