13 research outputs found
Diagnóstico de doenças metabólicas do sistema nervoso da infância por exame ultra-estrutural de tecido não cerebral
International meta-analysis of stated preference studies of transportation noise nuisance
The final publication is available at Springer via http://dx.doi.org/10.1007/s11116-014-9527-4This paper reports the first meta-analysis and most extensive review of stated preference studies of transportation noise nuisance. The meta-analysis is based on a newly compiled data set of 258 values from 49 studies and 23 countries and spanning more than 40 years. Contrast this with the most extensive meta-analysis of the more conventional hedonic pricing approach which includes 53 noise valuations. Moreover, the sample compares favourably with the 444 observations from the very first meta-analysis of the value of travel time savings which is by far the most widely examined parameter in transport planning.
A particularly significant finding of the study is that the intertemporal income elasticity is close to one, somewhat larger than the cross-sectional income elasticity typically obtained from individual studies. This demonstrates the importance of distinguishing the effects of
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income variations that occur over time, which tend to drive policy, from variations across
individuals at one point in time, and such findings are typical of those observed in other
markets. Importantly, the values derived are transferable across countries and may be used
to benchmark existing evidence and provide values in contexts where none exist.
Other key results are that values for aircraft noise exceed those for other modes, whilst
those exposed to higher noise levels and those who are highly annoyed also have higher
values in line with expectations. A wide range of design effects were tested but few were
significant and these included the consumer surplus measure, the representation of noise
and the context
NEUROAXONAL DYSTROPHY IN CHILDHOOD Report of Two Second Cousins with Hallerworden-Spatz Disease, and a Case of Seitelberger's Disease
Late Infantile Neuronal Ceroid Lipofuscinosis : Abnormalities in the Polyunsaturated Fatty Acid Profiles of Phospholipids in Cultured Skin Fibroblasts
Lipofuscinose ceróide neuronal: relato de quatro casos com estudo por histoquímica retal, microscopia eletrônica de conjuntiva e necrópsia
Os autores relatam os achados neuropatológicos e clínicos de quatro casos de lipofuscinose ceróide ou doença de Batten. Dois casos foram estudados por necrópsia: o encéfalo mostrou atrofia e neurônios contendo pigmento citoplasmático com características tintoriais de lipofuscina. Um caso foi diagnosticado por estudo histoquímico de biópsia retal, em material congelado em nitrogênio líquido demonstrando-se células ganglionares mioentéricas contendo acúmulo citoplasmático de material granular fosfatase ácida positivo, bem como em grande número de macrófagos do córion. O quarto caso foi diagnosticado por microscopia eletrônica de biópsia de conjuntiva, com identificação de inclusões curvelíneas membranáceas e tipo impressão digital