6 research outputs found
Fixed subaortic stenosis revisited - Congenital abnormalities in 72 new cases and review of the literature
Seventy-two patients aged 2-65 years (mean 20.2) with fixed subaortic
stenosis (FSS) are reported. All patients underwent echocardiography and
angiography prior to surgical intervention, Sixty-four (89%) had
discrete subaortic stenosis (DSS) and 8 (11%) tunnel type stenosis
(TSS). Patients with DSS aged 2-65 years (mean 29) while patients with
TSS aged 10-34 years (mean 19) and had a distinct female preponderance
(7:1). Twenty-five patients (39%) with DSS had other congenital
abnormalities of which aortic stenosis associated with bicuspid aortic
valve was slightly more common than ventricular septal defect (7:6),
Five patients with TSS had a small aortic annulus and hypoplastic aorta.
Our data and those in the literature indicate that TSS although related
to DSS has certain features that may set it apart as a distinct entity.
In addition DSS appears to be associated with aortic stenosis and
bicuspid aortic valve as frequently as with ventricular septal defect.
Copyright (C) 2000 S. Karger AG, Basel