Cutaneous lesions of the nose

Skin diseases on the nose are seen in a variety of medical disciplines. Dermatologists, otorhinolaryngologists, general practitioners and general plastic and dermatologic surgeons are regularly consulted regarding cutaneous lesions on the nose. This article is the second part of a review series dealing with cutaneous lesions on the head and face, which are frequently seen in daily practice by a dermatologic surgeon. In this review, we focus on those skin diseases on the nose where surgery or laser therapy is considered a possible treatment option or that can be surgically evaluated

The Cutaneous Features Of Tuberous Sclerosis : A Hospital Based Study In South India

Tuberous sclerosis is now frequently designated as the tuberous sclerosis complex (TSC) Its inheritance is autosomal dominant, but upto 70% of the cases are new mutations. Its prevalence was found to be 4.50 per 10.000 cases attending our dermatology outpatient department. A total of 9 patients attended the out patient department between August 1998 to June 2000. Five were males and 4 females. Eight cases were having definite TSC, whereas a single had suspect TSC. The age of our patients ranged from 10 months to 50 years. A positive family history was available in 4 cases. Most common cutaneous manifestation of TSC was adenoma sebaceum (8 cases) followed by shagreen patches (7 cases) and Koenenâ€s tumour (6 cases). Ash leaf macules and forehead plaques were seen in 5 cases each. Other findings were skin tags (3 cases), café-au-lait macules(2 cases), enamel pits (2 cases), portwine stain (1 case) and subconjunctival naevus (1 case). Classical triad of epilepsy, mental retardation and adenoma sebaceum was seen in one case only

Bilateral Giant Plexiform Neurofibromas In Neurofibromatosis Type 1

A single plexiform neurofibroma or two of any type are considered diagnostic of neurofibromatosis type 1 (NF). Plexiform neurofibromas are congenital and pathognomonic for NF-1. It is uncommon for an individual with NF-1 to have more than one plexiform neurofibroma. We, herewith, report a 38 year old man with NF-1, having exceptionally large bilateral plexiform neurofibromas involving both lower limbs

Kindler Syndrome With Squamous Cell Carcinoma Of The LEG

We report a 26 year old female patient of Kindler syndrome associated with squamous cell carcinoma of the leg. This syndrome is a rare inherited disorder characterized by trauma induced acral blistering, photosensitivity, poikiloderma and cutaneous atrophy. Occurrence of overt cutaneous malignancy on glabrous skin in this syndrome has not been reported before