Bilateral renal artery stenosis and epidermal nevus syndrome in a child

Epidermal nevus syndrome is a rare congenital sporadic neuro-ectodermic disorder, characterized by the presence of epidermal nevi in association with various developmental abnormalities of the skin, eyes, nervous, skeletal, cardiovascular and urogenital systems. We describe a 5-year-old boy with conjunctival lipodermoid, cervical and facial sebaceous nevi who presented at 3 years of age with hypertension due to bilateral renal artery stenosis together with multiple vascular anomalies (aorta, celiac trunk, superior mesenteric artery) as shown by magnetic resonance angiography. Systemic arterial hypertension was difficult to control despite combined anti-hypertensive drugs and the surgical repair of the aortic coarctation

Le Cystadénome mucineux ovarien géant (une cause rare de masse abdominale chez l'enfant : à propos de trois observations)

LYON1-BU Santé (693882101) / SudocPARIS-BIUM (751062103) / SudocSudocFranceF

Traitement percutané par Ethilbloc de kystes osseux anévrysmaux (série de 25 cas)

LYON1-BU Santé (693882101) / SudocSudocFranceF

Etude IRM des infections ostéo-articulaires de l'enfant à Kingella kingae

LYON1-BU Santé (693882101) / SudocPARIS-BIUM (751062103) / SudocSudocFranceF

APPORT DE L'IMAGERIE DANS LA PRISE EN CHARGE DES INVAGINATIONS INTESTINALES AIGUES SECONDAIRES CHEZ L'ENFANT (A PROPOS DE 43 CAS, EXPERIENCE A TORONTO)

LYON1-BU Santé (693882101) / SudocPARIS-BIUM (751062103) / SudocSudocFranceF

Safety of gadoterate meglumine in over 1600 children included in the prospective observational SECURE study

Background To date, few data on the safety profile of gadoterate meglumine in pediatric patients are available. Purpose To assess the safety profile of gadoterate meglumine in routine practice, to detect any case of nephrogenic systemic fibrosis (NSF) suspicion and to collect efficacy data. Material and Methods The pediatric population of the observational SECURE study comprised 1631 patients scheduled for contrast-enhanced magnetic resonance imaging (MRI) with gadoterate meglumine (dose: 0.1 mmol/kg). Risk factors, MRI types and immediate adverse events (AEs) were systematically recorded. Patients with moderate to severe renal impairment were followed up for at least 3 months for detection of any NSF suspicion. Efficacy was assessed by the on-site radiologist in terms of image quality and ability to come to diagnosis. Results The population included 106 children (6.5%) aged <2 years, 815 (50.0%) aged 2 to <12 years and 710 (43.5%) aged 12 to <18 years, with a mean (+/- SD) age of 10.2 (+/- 4.9) years. Central nervous system exploration was the most frequent MRI type (80.4%) and main risk factors were any stage of renal insufficiency (9.8%) and allergies (5.2%). Only one AE (vomiting) that was deemed doubtfully related to gadoterate meglumine was observed. No suspicions of NSF were reported. Good to very good image quality was obtained for 98.4% of pediatric patients and diagnosis was established in 99.6% of cases. Conclusion This study confirmed the good safety profile of gadoterate meglumine in routine practice in a large pediatric population. The study is registered on with the identifier NCT01523873

Apport de l'IRM dans le diagnostic d'appendicite aiguë chez l'enfant (une étude rétrospective à propos de 20 cas présentant une échographie non contributive)

LYON1-BU Santé (693882101) / SudocPARIS-BIUM (751062103) / SudocSudocFranceF

Modified technique of meso-Rex shunt in case of insufficient length of the jugular vein graft

Meso-Rex shunt (MRS) can relieve portal hypertension and restore a physiological portal flow in patients with portal vein thrombosis. We describe a technical variant where the autologous internal jugular vein (IJV) was too short to bridge the superior mesenteric vein (SMV) and the Rex recessus