Congenital agenesis of pubis and bilateral cryptorchidism: A case report

AbstractINTRODUCTIONAgenesis of the pubic bone, as evidenced in the world literature, is a very rare clinical and congenital abnormality. Several disorders may occur with hypoplasia of the pubis.PRESENTATION OF CASEHere, we report a rare longer follow-up case of the congenital unilateral agenesis of the superior ramus of pubic bone with bilateral undescended testes, osteoporosis, cranial malformations, acetabular dysplasia, unilateral shortening of the lower extremity and an abnormal gait pattern.DISCUSSIONSomatic mutations may responsible for developmental abnormalities of the mesoderm from which the pubic bones and urogenital structures develop.CONCLUSIONAn isolated x-ray finding of ramus pubis agenesis may associate with cryptorchidism or several other urogenital malformations

Idiopathic hypertonicity as a cause of stiffness after surgery for developmental dysplasia of the hip

INTRODUCTION: There are various complications reported with surgical treatment of DDH. Most studied complication is avascular necrosis of the femoral head and hip stiffness. The purpose of this report was to describe a case with severe stiffness of the hip due to hypertonicity in periarticular muscles after it was treated for developmental dysplasia of the hip (DDH)

Cystic transphyseal bone tuberculosis: a report of two cases

We present two cases of tuberculosis osteomyelitis mimicking subacute osteomyelitis and treated without extensive debridement. Tuberculous osteomyelitis should be considered in the differential diagnosis of proximal tibial infections in children and early diagnosis and treatment is possible without extensive debridement

Bone mineral density in children with neurofibromatosis 1

Aim: Our aim was to detect the status of bone mineral density (BMD) in children with NF1, and thus to help the management of the skeletal complications of NF1

Factors affecting adherence with foot abduction orthosis following Ponseti method

Objective: The Ponseti method is an effective protocol for treatment of congenital idiopathic clubfoot. Foot abduction orthosis (FAO) is sometimes necessary to preserve the correction achieved with the serial casting and tenotomy. Patient and family adherence to brace use is a common problem, as nonadherence is directly related to relapse. The aim of this study was to investigate patient and parent characteristics related to relapse

Radiological results of modified Dega osteotomy in Tonnis grade 3 and 4 developmental dysplasia of the hip

Dega acetabuloplasty at the time of open reduction is effective in improving the acetabular coverage of the femoral head, hence improving the stability of reduction and preventing possible surgery in the future for residual acetabular dysplasia in older children with Tonnis grade 3 and 4 developmental dysplasia of the hip (DDH). The aim of this study was to assess the radiological results of open reduction combined with Dega osteotomy in DDH. Twenty-two children's 26 hips were operated on at a mean age of 38 +/- 20.4 SD months and followed up for an average of 42 (range 24-108) months. Thirteen hips (50%) were operated on with concomitant open reduction and capsulorrhaphy, and 13 hips (50%) were treated with concomitant open reduction, capsulorrhaphy and femoral shortening osteotomy. Radiological examination included acetabular index (AI) and centre edge angle measurements. The mean preoperative AI was 39.4 +/- 6.9 degrees SD, which improved to 18.3 +/- 4.5 degrees SD postoperatively, and AI was measured as 15 +/- 3.5 degrees SD at the latest follow-up. There was a significant difference in the mean AI values between the last follow-up and the preoperative measurements (P < 0.05). The mean centre edge angle was 31 +/- 5.6 degrees SD postoperatively, and it was 31 +/- 6.2 degrees SD at follow-up. There was no significant difference between the two values. Two hips were noted to have lateralization of the femoral head due to coxa valga anteverta. One of them was operated with a femoral varus osteotomy. The Dega osteotomy combined with anterior open reduction and femoral osteotomies is a safe and effective acetabular osteotomy for surgical treatment of severe DDH such as Tonnis grade 3 and 4 dislocations. (C) 2014 Wolters Kluwer Health vertical bar Lippincott Williams & Wilkins