7 research outputs found
Dilated cardiomyopathy mutations in alpha-tropomyosin inhibit its movement during the ATPase cycle.
- Publication venue
- 'Elsevier BV'
- Publication date
- 01/01/2009
- Field of study
The Glu40Lys and Glu54Lys mutations in alpha-tropomyosin cause dilated cardiomyopathy (DCM). Functional analysis has demonstrated that both mutations decrease thin filament Ca2+-sensitivity and that Glu40Lys reduces maximum activation. To understand the molecular mechanism underlying these changes, we labeled wild type alpha-tropomyosin and both mutants at Cys190 with 5-iodoacetamide-fluorescein and incorporated the labeled proteins into ghost muscle fibers. Using the polarized fluorimetry, the position of the labeled tropomyosins on the thin filament and their affinity for actin were measured and the change in these parameters at different stages of the ATPase cycle determined. Both DCM mutations were found to shift tropomyosin towards the periphery of thin filament and to change the affinity of tropomyosin for actin; during the ATPase cycle the amplitude of tropomyosin movement was reduced and at some stages of the cycle even reversed. The correlation of these structural changes with the observed function effects is discussed
Alpha-tropomyosin mutations in inherited cardiomyopathies
- Author
- A Karibe
- AA Geisterfer-Lowrance
- AD McLachlan
- AD McLachlan
- AM Gordon
- AN Chang
- B Chang
- BJ Maron
- C Nakajima-Taniguchi
- Charles Redwood
- CK Loong
- D Wernicke
- DE Michele
- DE Michele
- DE Michele
- DE Michele
- E Behrmann
- E Kremneva
- E Oechslin
- EM McNally
- EM Schulz
- EM Schulz
- EM Schulz
- F Bai
- F Bai
- G Frisso
- G Jagatheesan
- GA Smith
- H Ashrafian
- H Morita
- H Otsuka
- H Ribolow
- H Watkins
- H Watkins
- I Olivotto
- J Heineke
- J Mogensen
- JB Meerakker van de
- K Murakami
- K Yamauchi-Takihara
- KY Spaendonck-Zwarts van
- L Thierfelder
- LM Holthauzen
- LS Tobacman
- M Arad
- M Janco
- M Johnson
- M Kawai
- M Memo
- M Mirza
- M Mirza
- M Muthuchamy
- MJ Heller
- N Golitsina
- NA Rysev
- NK Lakdawala
- NK Lakdawala
- P Richard
- P Robinson
- P Teekakirikul
- Paul Robinson
- PB Monteiro
- PH Pak
- R Bottinelli
- R Prabhakar
- RE Hershberger
- RJ Jongbloed
- S Fokstuen
- S Klaassen
- S Ly
- S Probst
- S Rajan
- SB Marston
- SL Driest Van
- SL Driest Van
- SV Perry
- SV Perry
- T Schober
- TM Olson
- V Regitz-Zagrosek
- V Sequeira
- W Bing
- W Bing
- XE Li
- XE Li
- YM Hoedemaekers
- YS Borovikov
- YS Borovikov
- YS Borovikov
- YS Borovikov
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Calcium Ion in Skeletal Muscle: Its Crucial Role for Muscle Function, Plasticity, and Disease
- Author
- ACSADI G
- BARNARD RJ
- BOBE R
- BOROVIKOV YU S
- DANIELI GA
- DE SMEDT H
- DIAZ-MUNOZ M
- DOWNES M
- DUDLEY GA
- DUDLEY GA
- FARAH CS
- FLORINI JR
- GARCIN R
- GERDAY C
- GRĂśTZNER P
- GUO W
- HALL-CRAGGS EC
- HAWKINS C
- Heinrich Brinkmeier
- HELBLING-LECLERC A
- HERZBERG O
- HIKIDA RS
- HOFMANN SL
- HUGHES SM
- INESI G
- JAYARAMAN T
- KHAN MA
- KIM CK
- KLEE CB
- KOBAYASHI T
- KOBAYASHI T
- KRĂ„MER R
- KRĂśGER P
- KRĂśGER P
- LEHMANN-HORN F
- LEHOTSKY J
- LEXELL J
- LYTTON J
- MacKRILL JJ
- Markus MĂĽntener
- Martin W. Berchtold
- McPHERSON PS
- McPHERSON PS
- MELICHNA J
- MENKE A
- MICKELSON JR
- MITCHELL RD
- MURRAY BE
- MĂśNTENER M
- NEGELE JC
- NEMETH PM
- NORI SL
- OSTWALD TJ
- PETTE D
- POTTER JD
- PULLEN AH
- PULLEN AH
- RANVIER L
- SCHIAFFINO S
- SCOTT BT
- SEILER S
- SELBERT S
- SIRCA A
- SORIMACHI H
- SUDBRAK R
- SUH JG
- SUNADA Y
- SUZUKI K
- TIDBALL JG
- TIMERMAN AP
- TOYOFUKU T
- VANDERVOORT AA
- VITADELLO M
- WATTERSON JG
- WUYTACK F
- XU A
- Publication venue
- 'American Physiological Society'
- Publication date
- Field of study
Wave Propagation in a Range Dependent Waveguide
- Author
- A Bamberger
- A Bamberger
- A Stevenson
- A Stevenson
- A Tolstoy
- AB Coppens
- AB Coppens
- AB Valyaev
- AD Avdeev
- AD Avdeev
- AD Pierce
- AD Pierce
- AD Pierce
- AD Pierce
- AE Kondo
- AF Gladenko
- AF Gladenko
- AF Gladenko
- AG Voronovich
- AG Voronovich
- AG Voronovich
- AH Nayfeh
- AI Neishtadt
- AL Gutman
- AL Virovlyanskii
- AL Virovlyansky
- AP Prudnikov
- AP Prudnikov
- AS Starkov
- AS Starkov
- AS Starkov
- AS Starkov
- AS Starkov
- AS Starkov
- AT Abawi
- AV Gurevich
- AV Gurevich
- AV Popov
- Avilov
- B.J. Orchard
- B.Ye. Kinber N.Ye. Mal’tsev, V.I. Tokatly
- BE Mcdonald
- BE Mcdonald
- BE Mcdonald
- BE Mcdonald
- BI Klyachin
- BL Kennett
- BL Kennett
- BL Kennett
- BR Mace
- BT Wetton
- BY Kinber
- BY Kinber
- BY Kinber
- BZ Katsenelenbaum
- BZ Katsenelenbaum
- C Wunsch
- CA Boyles
- CH Harrison
- CS Chiu
- CS Chiu
- CT Tindle
- D Chu
- D Huang
- D Lee
- D Lee
- D Lee
- D Lee
- D Lee
- D Lee
- D Wurmser
- D Yevick
- D.R. Palmer
- DE Weston
- DE Weston
- DE Weston
- DH Berman
- DI Darovskikh
- DI Darovskikh
- DJ Thomson
- DJ Thomson
- DJ Tomson
- DM Milder
- DP Knobles
- DR Jackson
- DR Palmer
- DR Palmer
- DS Ko
- DY Mikhin
- E Kamke
- E Smith
- E Topuz
- E.A. Polyanskii
- EA Polyanskii
- EA Polyanskii
- EA Polyanskii
- EA Polyanskii
- EA Polyanskii
- EA Polyanskii
- EC Shang
- EC Shang
- EC Shang
- EH Vefring
- EK Westwood
- ER Robinson
- ER Robinson
- F Natterer
- FA Milinazzo
- FB Bretherton
- FB Jensen
- FB Jensen
- FB Jensen
- FD Tappert
- FD Tappert
- FD Tappert
- FD Tappert
- FD Tappert
- FD Tappert
- FG Bass
- FP Bretherton
- FR Dinapoli
- FS Chwieroth
- G Gillette
- GA Korn
- GA Kriegsmann
- GB Deane
- GD Malyuzhinets
- GD Malyuzhinets
- GD Malyuzhinets
- GH Knightly
- GH Knightly
- GJ Orris
- GV Frisk
- GV Kisunko
- GY Lyubarskii
- H Bremmer
- H Bremmer
- H Levine
- H Primack
- H Weinberg
- HK Brock
- I Karasalo
- IA Molotkov
- IA Molotkov
- IA Molotkov
- IJ Thompson
- IT Lu
- IV Mukhina
- IW Schurman
- J Corones
- J Simmen
- J Tromp
- J.S. Robertson
- JA Fawcett
- JA Fawcett
- JA Hudson
- JA Santo
- JA Santo
- JA Santo
- JB Keller
- JC Miller
- JE Murphy
- JF Claerbout
- JF Claerbout
- JF Miller
- JH Marburger
- JH Woodhouse
- JJ Mccoy
- JJ Mccoy
- JM Arnold
- JM Arnold
- JM Arnold
- JM Arnold
- JP Corones
- JS Papadakis
- JS Perkins
- JS Robertson
- JS Robertson
- JS Robertson
- JS Robertson
- JT Goh
- JT Warfield
- K Dysthe
- K Taylor
- K.R. Smith
- KD Heaney
- KE Gilbert
- KE Gilbert
- KV Avilov
- L Fishman
- L Fishman
- L Fishman
- L Halpern
- L Nghiem-Phu
- L Nghiem-Phu
- L.M. Brekhovskikh
- LA Vainshtein
- LB Dozier
- LB Dozier
- LB Felsen
- LD Landau
- LD Landau
- LL Vaksman
- LL Vaksman
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Campos
- LR Bragg
- LR Bragg
- LS Wang
- M Park
- M Wiercigroch
- M.A. Leontovich
- MA Biot
- MA Leontovich
- MA Leontovich
- MB Porter
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Collins
- MD Feit
- MG Bostock
- MG Brown
- MI Yavor
- MI Yavor
- MJ Buckingham
- MJ Buckingham
- MJ Buckingham
- MK Myers
- MK Myers
- MV Hall
- MV Tinin
- N.S. Grigor’eva
- NN Komissarova
- NN Komissarova
- NN Komissarova
- NN Komissarova
- NN Zernov
- NN Zernov
- NS Grigoreva
- NY Maltzev
- O.A. Godin
- O.A. Godin
- O.A. Godin
- O.A. Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- OA Godin
- P. Gamiz
- PH Lim
- PW Smith
- R Burridge
- R Doolittle
- R Snieder
- R Snieder
- R Snieder
- RC Shockley
- RC Shockley
- RF Gragg
- RF Henrick
- RH Hardin
- RI Brent
- RI Brent
- RI Odom
- RI Odom
- RI Odom
- RJ Cederberg
- RM Fitzgerald
- RR Greene
- S Schelkunoff
- S.A.L. Glegg
- S.M. Grudskii
- SE Dosso
- SJ Maurer
- SK Jeng
- SL Sobolev
- SM Candel
- SM Flatte
- SM Grudskiy
- Solov’ev
- SP Aksenov
- SR Rutherford
- SS Abdullaev
- SS Abdullaev
- SS Davis
- ST Mcdaniel
- ST Mcdaniel
- ST Mcdaniel
- SV Burenkov
- SV Burenkov
- T Landers
- TN Bichutskaya
- TN Bichutskaya
- transl. English
- V Maupin
- V Maupin
- V Maupin
- V.S. Buldyrev
- V.S. Buldyrev
- V.S. Buldyrev
- VA Baranov
- VA Borovikov
- VA Borovikov
- VA Borovikov
- VA Borovikov
- VA Borovikov
- VA Borovikov
- VA Borovikov
- VA Fock
- VE Zakharov
- VE Zakharov
- VI Il’ichev
- VI Karpman
- VK Kuznetsov
- VK Kuznetsov
- VM Babic
- VM Babich
- VM Babich
- VM Babich
- VM Babich
- VN Melekhin
- VP Maslov
- VS Buldyrev
- VS Buldyrev
- VS Buldyrev
- VS Buldyrev
- VS Buslaev
- VV Goncharov
- VV Shevchenko
- VV Shevchenko
- VV Shevchenko
- VV Shevchenko
- VY Zavadskii
- VY Zavadskii
- W Eversman
- W Kohler
- W Munk
- W Munk
- W Möhring
- WA Kuperman
- WL Kath
- WL Siegmann
- WL Siegmann
- Y Cho
- Y Desaubies
- Y Desaubies
- YA Kravtsov
- YL Li
- YN Demkov
- YS Kryukov
- YV Petukhov
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- 01/01/1999
- Field of study
The Field at and near a Caustic
- Author
- A Silbiger
- AH Kamel
- AN Barkhatov
- AO Williams
- AP Kachalov
- Arnold
- AS Kryukovskiy
- AS Kryukovskiy
- AS Kryukovskiy
- BG Lucas
- BY Kinber
- C Chester
- CH Chapman
- D Ludwig
- D Ludwig
- DA Gorman
- DA Sachs
- DH Peregrine
- DH Wood
- DS Ahluwalia
- DW White
- E Zauderer
- ED Gazazyan
- FB Jensen
- FD Tappert
- FG Friedlander
- GA Korn
- GB Airy
- GL James
- H Ăśberall
- I Tolstoy
- IF Dronov
- II Volkov
- JA Santo
- JF Nye
- JG Watson
- JN Connor
- JN Connor
- JN Connor
- KW Ford
- L Levey
- L Levey
- LB Felsen
- LD Landau
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- LM Brekhovskikh
- M.A. Leontovich
- MA Leontovich
- MA Pedersen
- MA Pedersen
- MB Porter
- MG Brown
- MG Brown
- MG Brown
- MJ Mezzino
- MJ Yedlin
- MM Popov
- MV Berry
- MV Berry
- MV Berry
- MV Fedoryuk
- MV Fedoryuk
- MV Fedoryuk
- NC Nicholas
- NY Kirpichnikova
- O.A. Godin
- OA Godin
- OA Godin
- PL Marston
- PM Bakker
- R Gilmore
- R Lynn
- RE Langer
- RM Levis
- RN Buchal
- RW Boyd
- T Brocker
- T Pearcey
- V Arnold
- V Arnold
- V. Cerveny
- VA Borovikov
- VA Fock
- VD Azhotkin
- VD Azhotkin
- VE Grikurov
- VI Arnold
- VK Kiriakov
- VM Babic
- VM Babic
- VM Babic
- VM Babic
- VM Babich
- VM Babk
- VM Kudryashov
- VP Maslov
- VP Maslov
- VS Buldyrev
- VS Buldyrev
- VS Buldyrev
- VS Buldyrev
- VV Klimov
- VV Klimov
- VY Groshev
- WA Kinney
- YA Kravtsov
- YA Kravtsov
- YA Kravtsov
- YA Kravtsov
- YA Kravtsov
- YI Orlov
- YI Orlov
- YI Orlov
- YI Orlov
- YI Orlov
- YL Gazaryan
- Yu.I. Orlov
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- 01/01/1999
- Field of study
Late Middle Cambrian trilobites from St Valentines Peak and Native Track Tier, northwestern Tasmania
- Author
- Baillie P.W.
- Bao J.-S.
- Bordonaro O.L.
- Borovikov L.E.
- Brock GA.
- Brongniart A.
- Brögger W.C.
- Butts C.
- Chang W.T.
- Cooper R.A.
- Ergaliev G.K.
- Holm G.
- Howell B.F.
- Jago J.B.
- Jago J.B.
- Jago J.B.
- Jago J.B.
- Jago J.B.
- Jago J.B.
- Jago J.B.
- Jago J.B.
- Jago J.B.
- Jago J.B.
- James B. Jago
- Jell P.A.
- Jell P.A.
- Jell P.A.
- Jin-Song Bao
- Khalfin L.L.
- Kobayashi T.
- Kobayashi T.
- Kobayashi T.
- Laurie J.R.
- Lazarenko N.P.
- Linnarsson J.G.O.
- Lisogor K.A.
- Lorenz T.
- Lu Y.-H.
- Lu Y.-H.
- M'coy F.
- Meek F.G.
- Moberg J.C.
- Palmer A.R.
- Palmer A.R.
- Peng S.-C.
- Peng S.-C.
- Peng S.-H.
- Peng S.-H.
- Peter W. Baillie
- Pokrovskaya N.V.
- Poulsen C.
- Pratt B.R.
- Qian Y.-Y.
- Resser C.E.
- Robison R.A.
- Robison R.A.
- Robison R.A.
- Romanenko E.V.
- Romanenko E.V.
- Rusconi C.
- Rusconi C.
- Rushton A.W.A.
- Seymour D.B.
- Shergold J.H.
- Shergold J.H.
- Tortello M.F.
- Walcott C.D.
- Walcott C.D.
- Walcott C.D.
- WestergĂĄrd A.H.
- WestergĂĄrd A.H.
- Whitehouse F.W.
- Whitehouse F.W.
- Whittington H.B.
- Whittington H.B.
- Xiang L.-W.
- Yang J.-L.
- Zhang T.-R
- Ă–pik A.A.
- Ă–pik A.A.
- Ă–pik A.A.
- Ă–pik A.A.
- Ă–pik A.A.
- Publication venue
- 'Informa UK Limited'
- Publication date
- Field of study
Polarity and gradients in plants: A survey
- Author
- A Hagemann
- A Lang
- A Max
- A Pascher
- A TrÉcul
- A Weide
- AB Wardrop
- AC Leopold
- Agricola G.
- ATH Czaja
- Axmx S.
- B Cholnoky
- Baldovinos DE LA Pena G.
- Beiträge zur Morphologie der ungeschlechtlichen und geschlechtlichen Vermehrung der Gattung Chlamydomonas
- Bv Cholnoky
- C Wetter
- CM Chud
- CM Chud
- Correns
- CW Wardlaw
- DL Freeman
- DM Whitaker
- DM Whitaker
- DR Bartoo
- E Ball
- E Ball
- E BĂśNning
- E BĂśNning
- E BĂśNning
- E BĂśWung
- E Herrz
- E Knapp
- E KĂśSter
- E KĂśSter
- E Libbert
- E Running
- E Running
- E Running
- E Wildeman
- E Zepf
- EA Reed
- EJ Lund
- EJ Lund
- EJ Lund
- EW Sinnott
- EW Sinnott
- EW Sinnott
- EW Sinnott
- EW Sinnott
- F Bergann
- F Neeff
- F Noll
- F Oehlkers
- F Steinecke
- F Wettstein
- FC Steward
- Frey-WYSSLIvG A.
- FW Went
- FW Went
- FW Went
- FW Went
- G Camus
- G Klees
- G Kostrun
- G Morel
- G Mosebach
- G Rothe
- G Werz
- G Werz
- G Werz
- GA Borovikov
- GJ Allman
- Goebel K.
- Goebel K.
- Gratzy-Wardengg S. A. E.
- GS Avery
- H Beyrich
- H Bornhagen
- H Drawert
- H Miene
- H Miene
- H Moar
- H Prat
- H Timmel
- H VĂ–Chting
- H VĂ–Chting
- H VĂ–Chting
- H VĂ–Chting
- H VĂ–Chting
- H Wanner
- H Wanner
- H Wanner
- H Winkler
- HC Row
- HE Warmke
- HF Rosene
- HF Rosene
- HF Rosene
- HG Alraum
- HG Alraum
- HL Duiiamel
- Hurd-Carrer A. M.
- I Igura
- J Dore
- J HĂ„Mmerling
- J HĂ„Nmierling
- J HĂ„Nmierling
- J HĂ„Nmierling
- J HĂ„Nmierling
- J LefÙVre
- J Loeb
- J Loeb
- J Massart
- J Moutschen
- J Needham
- J Reinert
- J Reinert
- J Sachs
- J Terby
- J Weir
- J Westerdijk
- JB Thomas
- JE Ellengorn
- JM Janse
- JM Oppenheimer
- JR Reeder
- JT Bonner
- JT Bonner
- JW Pont
- K Behre
- K Goebel
- K HĂ–Fler
- K Loawag
- K Loawag
- K Ramshorn
- KB Raper
- KE Maltzaax
- Klees
- L Bauer
- L Eliasson
- L Jaffe
- L Kny
- L Stange
- LF Jaffe
- LH Macdaniels
- LJ Berry
- LJ Berry
- M Abeloos
- M Raciborski
- MA Tingley
- Moutschen
- MP Both
- MW Bannan
- MĂśLler-Stoll W. R.
- Nahazawa
- Nahazawa
- Nahazawa
- Nahazawa
- Nahazawa
- Nahazawa
- Nahazawa
- Neeff
- Neilson-Jones W.
- NG Cholodny
- NIC MĂśLler
- Noll
- Noll
- O Rathfelder
- P Jaccard
- P Maaesawarr
- PA Hicks
- PE Pilet
- PE Pilet
- PL Redfearn
- R Beyerle
- R Bloch
- R Bloch
- R Bloch
- R Bloch
- R Bloch
- R Bloch
- R Bloch
- R Castan
- R Dostal
- R Dostal
- R Harrison
- Reu-Ter L.
- Reu-Ter L.
- RG Harrison
- RG Harrison
- RJ Gautheret
- RJ Gautheret
- RJ Gautheret
- RJD Graham
- RM Sachs
- RM Tupper-Carey
- S Nahazawa
- S Nahazawa
- S Nahazawa
- Sachs
- Sachs R. M., C. F. Bretz and A. Lang
- Schechter V.
- Schechter V.
- Schober G.
- Schrank A. R.
- Schratz E.
- Schumacher W.
- Schumacher W.
- Seifriz W.
- Silberschmidt K.
- Simon S. V.
- Sinnott E. W.
- Sinnott E. W., and R. Bloch
- SL Meyer
- Sohoutedenwery I.
- SS Wilkes
- ST Hales
- TT Colquhoun
- W Benecke
- W Haupt
- W Haupt
- W Keen
- W Nienburg
- W Pfeffer
- W Plant
- W Plett
- W Zimmermann
- W Zimmermann
- W Zimmermann
- W Zimmermann
- WA Beceer
- WG Clark
- WG Clark
- WP Jacobs
- WP Jacobs
- WS Rehm
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- 01/01/1965
- Field of study