5 research outputs found
ΠΠ΅Π»ΡΠ΄ΠΎΡΠΊΠΎΠ²Π°Ρ ΡΠΊΡΡΡΠ°ΡΠΈΡΡΠΎΠ»ΠΈΡ Ρ Π΄Π΅ΡΠ΅ΠΉ
The article presents updated data on the problem of premature ventricular contractions in children based on the clinical guidelines of the Russian Society of Cardiology and the Union of Pediatricians of Russia for the diagnosis, treatment and management of pediatric patients with premature ventricular contraction. The issues of diagnosis and treatment based on the principles of evidence-based medicine as well as important aspects of prevention of exacerbations and follow-up have been clarified in detail. The criteria for assessing the quality of care for patients with premature ventricular contractions have been presented.CONFLICT OF INTEREST. Not declared.Π ΡΡΠ°ΡΡΠ΅ ΠΈΠ·Π»ΠΎΠΆΠ΅Π½Ρ ΠΎΠ±Π½ΠΎΠ²Π»Π΅Π½Π½ΡΠ΅ Π΄Π°Π½Π½ΡΠ΅ ΠΎ ΠΏΡΠΎΠ±Π»Π΅ΠΌΠ΅ ΠΆΠ΅Π»ΡΠ΄ΠΎΡΠΊΠΎΠ²ΡΡ
ΡΠΊΡΡΡΠ°ΡΠΈΡΡΠΎΠ»ΠΈΠΉ Ρ Π΄Π΅ΡΠ΅ΠΉ, ΠΎΡΠ½ΠΎΠ²Π°Π½Π½ΡΠ΅ Π½Π° ΠΊΠ»ΠΈΠ½ΠΈΡΠ΅ΡΠΊΠΈΡ
ΡΠ΅ΠΊΠΎΠΌΠ΅Π½Π΄Π°ΡΠΈΡΡ
ΠΡΡΠΎΡΠΈΠ°ΡΠΈΠΈ Π΄Π΅ΡΡΠΊΠΈΡ
ΠΊΠ°ΡΠ΄ΠΈΠΎΠ»ΠΎΠ³ΠΎΠ² Π ΠΎΡΡΠΈΠΈ ΠΈ Π‘ΠΎΡΠ·Π° ΠΏΠ΅Π΄ΠΈΠ°ΡΡΠΎΠ² Π ΠΎΡΡΠΈΠΈ ΠΏΠΎ Π΄ΠΈΠ°Π³Π½ΠΎΡΡΠΈΠΊΠ΅, Π»Π΅ΡΠ΅Π½ΠΈΡ ΠΈ Π²Π΅Π΄Π΅Π½ΠΈΡ ΠΏΠ°ΡΠΈΠ΅Π½ΡΠΎΠ² Π΄Π΅ΡΡΠΊΠΎΠ³ΠΎ Π²ΠΎΠ·ΡΠ°ΡΡΠ° Ρ ΠΆΠ΅Π»ΡΠ΄ΠΎΡΠΊΠΎΠ²ΠΎΠΉ ΡΠΊΡΡΡΠ°ΡΠΈΡΡΠΎΠ»ΠΈΠ΅ΠΉ. ΠΠΎΠ΄ΡΠΎΠ±Π½ΠΎ ΠΎΡΠ²Π΅ΡΠ΅Π½Ρ Π²ΠΎΠΏΡΠΎΡΡ Π΄ΠΈΠ°Π³Π½ΠΎΡΡΠΈΠΊΠΈ, Π»Π΅ΡΠ΅Π½ΠΈΡ, ΠΎΡΠ½ΠΎΠ²Π°Π½Π½ΡΠ΅ Π½Π° ΠΏΡΠΈΠ½ΡΠΈΠΏΠ°Ρ
Π΄ΠΎΠΊΠ°Π·Π°ΡΠ΅Π»ΡΠ½ΠΎΠΉ ΠΌΠ΅Π΄ΠΈΡΠΈΠ½Ρ, Π° ΡΠ°ΠΊΠΆΠ΅ Π²Π°ΠΆΠ½ΡΠ΅ Π°ΡΠΏΠ΅ΠΊΡΡ ΠΏΡΠΎΡΠΈΠ»Π°ΠΊΡΠΈΠΊΠΈ ΠΎΠ±ΠΎΡΡΡΠ΅Π½ΠΈΠΉ Π±ΠΎΠ»Π΅Π·Π½ΠΈ ΠΈ Π΄ΠΈΡΠΏΠ°Π½ΡΠ΅ΡΠ½ΠΎΠ³ΠΎ Π½Π°Π±Π»ΡΠ΄Π΅Π½ΠΈΡ. ΠΡΠΎΠ±ΡΠ°ΠΆΠ΅Π½Ρ ΠΊΡΠΈΡΠ΅ΡΠΈΠΈ ΠΎΡΠ΅Π½ΠΊΠΈ ΠΊΠ°ΡΠ΅ΡΡΠ²Π° ΠΌΠ΅Π΄ΠΈΡΠΈΠ½ΡΠΊΠΎΠΉ ΠΏΠΎΠΌΠΎΡΠΈ ΠΏΠ°ΡΠΈΠ΅Π½ΡΠ°ΠΌ Ρ ΠΆΠ΅Π»ΡΠ΄ΠΎΡΠΊΠΎΠ²ΡΠΌΠΈ ΡΠΊΡΡΡΠ°ΡΠΈΡΡΠΎΠ»ΠΈΡΠΌΠΈ.ΠΡΠ±Π»ΠΈΠΊΠ°ΡΠΈΡ ΡΠ²Π»ΡΠ΅ΡΡΡ ΠΎΠ±Π½ΠΎΠ²Π»Π΅Π½Π½ΡΠΌ Π²Π°ΡΠΈΠ°Π½ΡΠΎΠΌ ΠΊΠ»ΠΈΠ½ΠΈΡΠ΅ΡΠΊΠΈΡ
ΡΠ΅ΠΊΠΎΠΌΠ΅Π½Π΄Π°ΡΠΈΠΉ ΠΡΡΠΎΡΠΈΠ°ΡΠΈΠΈ Π΄Π΅ΡΡΠΊΠΈΡ
ΠΊΠ°ΡΠ΄ΠΈΠΎΠ»ΠΎΠ³ΠΎΠ² Π ΠΎΡΡΠΈΠΈ ΠΈ Π‘ΠΎΡΠ·Π° ΠΏΠ΅Π΄ΠΈΠ°ΡΡΠΎΠ² Π ΠΎΡΡΠΈΠΈ ΠΏΠΎ Π΄ΠΈΠ°Π³Π½ΠΎΡΡΠΈΠΊΠ΅, Π»Π΅ΡΠ΅Π½ΠΈΡ ΠΈ Π²Π΅Π΄Π΅Π½ΠΈΡ ΠΏΠ°ΡΠΈΠ΅Π½ΡΠΎΠ² Π΄Π΅ΡΡΠΊΠΎΠ³ΠΎ Π²ΠΎΠ·ΡΠ°ΡΡΠ° Ρ ΠΆΠ΅Π»ΡΠ΄ΠΎΡΠΊΠΎΠ²ΠΎΠΉ ΡΠΊΡΡΡΠ°ΡΠΈΡΡΠΎΠ»ΠΈΠ΅ΠΉ, ΠΎΠΏΡΠ±Π»ΠΈΠΊΠΎΠ²Π°Π½Π½ΡΡ
Π½Π° ΡΠ°ΠΉΡΠ΅ https://medi.ru/klinicheskie-rekomendatsii/zheludochkovaya-ekstrasistoliya-u-detej_14366/ΠΠ²ΡΠΎΡΡ ΠΏΠΎΠ΄ΡΠ²Π΅ΡΠΆΠ΄Π°ΡΡ ΠΎΡΡΡΡΡΡΠ²ΠΈΠ΅ ΠΊΠΎΠ½ΡΠ»ΠΈΠΊΡΠ° ΠΈΠ½ΡΠ΅ΡΠ΅ΡΠΎΠ², ΠΊΠΎΡΠΎΡΡΠΉ Π½Π΅ΠΎΠ±Ρ
ΠΎΠ΄ΠΈΠΌΠΎ ΠΎΠ±Π½Π°ΡΠΎΠ΄ΠΎΠ²Π°ΡΡ
Damages of Cardiovascular System at Mucopolysaccharidosis Type I: Clinical Cases
Background. Cardiac involvement in patients with mucopolysaccharidosis (MPS) type I, or Hurler syndrome, has various phenotypes.Clinical Case Description. In the first case symptoms were indicative of acute severe heart failure which was confirmed by laboratory and instrumental diagnostic methods. Left heart chambers dilatation and left ventricular hypocontractility were revealed on echocardiography. Atypical disease course with no improvement on multicomponent therapy of heart failure let us to think about metabolic disease, so we confirmed it with tandem mass spectrometry and molecular genetic testing. Therefore this led to timely enzyme replacement therapy onset and allogeneic bone marrow transplantation that positively affect the disease outcome. The second case showed classic course of MPS I. Its clinical signs such as musculoskeletal and ENT-organ manifestations allowed us to diagnosis and later confirm it by tandem mass spectrometry and molecular genetic testing at the age of 3. The cardiac pathology presented by mitral valve leaflets thickening and 2nd degree regurgitation has been diagnosed later. In our view, early treatment onset should slow down the progression of heart damage.Conclusion. Several clinical variants of cardiac pathology at MPS I are presented. The need of constant cardiovascular system monitoring in children with MPS I is shown. It is also mentioned that cardiac pathology can be the first manifestation of the disease
Premature Ventricular Contraction in Children
The article presents updated data on the problem of premature ventricular contractions in children based on the clinical guidelines of the Russian Society of Cardiology and the Union of Pediatricians of Russia for the diagnosis, treatment and management of pediatric patients with premature ventricular contraction. The issues of diagnosis and treatment based on the principles of evidence-based medicine as well as important aspects of prevention of exacerbations and follow-up have been clarified in detail. The criteria for assessing the quality of care for patients with premature ventricular contractions have been presented.CONFLICT OF INTEREST. Not declared