5 research outputs found
The Primary Folding Defect and Rescue of ÎF508 CFTR Emerge during Translation of the Mutant Domain
- Author
- AC DeCarvalho
- Andre Schmidt
- AW Serohijos
- B Kleizen
- Bertrand Kleizen
- BH Qu
- BH Qu
- CL Ward
- CR Brown
- CS Rogers
- E Strickland
- EM Schwiebert
- F Sun
- F Zhang
- GC Meacham
- GC Meacham
- GM Denning
- HA Lewis
- HA Lewis
- HA Lewis
- Hanneke Hoelen
- I Braakman
- Ineke Braakman
- J Buchner
- JH van Doorninck
- JL Mendoza
- JM Younger
- JM Younger
- John Richardson
- JP Mornon
- JR Riordan
- K Du
- K Du
- L Cui
- L He
- LG Johnson
- LS Ostedgaard
- M Roxo-Rosa
- MP Anderson
- MR Picciotto
- P Vergani
- Paraskevi Charitou
- PH Thibodeau
- PH Thibodeau
- Philip J. Thomas
- R Wilson
- RJ Dawson
- S Atwell
- S Sato
- S Sato
- SH Cheng
- TJ Jensen
- TW Loo
- V Kanelis
- Vladimir N. Uversky
- X Sun
- X Wang
- XM Zhang
- Publication venue
- Public Library of Science
- Publication date
- 01/01/2010
- Field of study
In the vast majority of cystic fibrosis (CF) patients, deletion of residue F508 from CFTR is the cause of disease. F508 resides in the first nucleotide binding domain (NBD1) and its absence leads to CFTR misfolding and degradation. We show here that the primary folding defect arises during synthesis, as soon as NBD1 is translated. Introduction of either the I539T or G550E suppressor mutation in NBD1 partially rescues ÎF508 CFTR to the cell surface, but only I539T repaired ÎF508 NBD1. We demonstrated rescue of folding and stability of NBD1 from full-length ÎF508 CFTR expressed in cells to isolated purified domain. The co-translational rescue of ÎF508 NBD1 misfolding in CFTR by I539T advocates this domain as the most important drug target for cystic fibrosis
A Heterologous Multiepitope DNA Prime/Recombinant Protein Boost Immunisation Strategy for the Development of an Antiserum against Micrurus corallinus (Coral Snake) Venom
- Author
- A Calmette
- AM Moura-da-Silva
- AR de Roodt
- AR Prieto da Silva
- BA Jameson
- CA Schneider
- Carlos Chavez-Olortegui
- Clara Guerra Duarte
- CR Lewis-Younger
- CR Ramos
- D Laune
- DA Warrell
- DM Feltquate
- EO Serapicos
- F Bucaretchi
- G Azofeifa-Cordero
- GD Tanaka
- GN Ramachandran
- HA Reid
- Henrique Roman Ramos
- I Fernandes
- I Fernandes
- I Raw
- InĂĄcio de Loiola M. Junqueira-de-Azevedo
- J Kyte
- J Silveira de Oliveira
- JA Roze
- JLC Cardoso
- JP Chippaux
- Juliana Branco Novo
- K Arnold
- Karen Castro
- KE Hooper-McGrevy
- KL Castro
- LI Leao
- M Biasini
- N Guex
- P Benkert
- P Benkert
- Paulo Lee Ho
- PL Ho
- PR Widders
- R Frank
- R Mannel
- RA Harrison
- RA Harrison
- RA Harrison
- RB Yang
- RC Weir
- Ricardo A. Machado-de-Ăvila
- RL Norris
- Robert A Harrison
- SC Wagstaff
- V Arce-Estrada
- Y Nakamura
- Publication venue
- 'Public Library of Science (PLoS)'
- Publication date
- Field of study
Optimizations of SiRNA Design for the Activation of Gene Transcription by Targeting the TATA-Box Motif
- Author
- A Khvorova
- A Mantei
- A Nykanen
- A Reynolds
- A Sandelin
- AA Beg
- AH Hall
- AJ Whitmarsh
- AL Jackson
- AZ Ansari
- AZ Ansari
- B Haley
- B Jagla
- B Liu
- BA Janowski
- BA Janowski
- BA Janowski
- BP Lewis
- BP Monia
- C Wilson
- CD Jeffries
- CD Novina
- CR Allerson
- CY Majmudar
- D Yu
- DH Kim
- DR Corey
- DS Schwarz
- DS Schwarz
- FJ van Werven
- G Tang
- H Herweijer
- Haihua Luo
- HL Pahl
- Hui Zhang
- HW Hwang
- J Moses
- J Soutschek
- J Vollmer
- JB Bramsen
- JC Schwartz
- JM Jacque
- JM Layzer
- Jun Liu
- JW Engels
- JY Liao
- K Nishi
- K Suzuki
- K Ui-Tei
- K Ui-Tei
- KR Blake
- L Gitlin
- Laszlo Tora
- LC Li
- LL Cummins
- M Amarzguioui
- M Jinek
- M Kane
- M Kulkarni
- M Manoharan
- M Yamagishi
- ME Gleave
- Miaomiao Fan
- N Sugimoto
- NS Lee
- PD Cook
- PS Arora
- PS Miller
- R Dreos
- RC Wilson
- RF Place
- S Bagga
- S Guang
- S Li
- SA Shabalina
- SM Elbashir
- SM Elbashir
- SM Elbashir
- SM Hammond
- ST Younger
- T Juven-Gershon
- TM Rana
- TP Prakash
- V Huang
- WF Lima
- WY Hu
- Xuemin Guo
- Y Chu
- Y Kwon
- Y Zhang
- Yijun Zhang
- YL Chiu
- Zhuoqiong Huang
- Publication venue
- 'Public Library of Science (PLoS)'
- Publication date
- Field of study
Horticultural Scienceâs Role in Meeting the Need of Urban Populations
- Author
- A Santini
- A Stigarll
- A Troy
- A Zezza
- AA Alvey
- AG McDonald
- AH Roy
- AL Shigo
- AM Townsend
- AP Davis
- B Baumgartner
- B Behe
- B Cimprich
- BS Kweon
- BY Kim
- C Cammack
- C Cammack
- C Haynes
- C McGuinn
- C MĂŒller
- C Potter
- CA Lewis
- CA Shoemaker
- CA Shoemaker
- CC Collins
- CC Marcus
- CL Wilson
- CM Gigliotti
- CM Morton
- CP Loughner
- CR Finch
- CR Hall
- D Hope
- D Kendal
- D Pimentel
- D Relf
- D Relf
- D Relf
- den Berg AE Van
- DJ Cotter
- DJ Nowak
- DR Brogan
- E Alexandri
- E Ng
- E Rappe
- EAK Justen
- EG McPherson
- FE Kuo
- FE Kuo
- FR Gouin
- G McPherson
- GA Dahle
- GH Donovan
- GH Donovan
- GS Lovasi
- H Akbari
- H Akbari
- H Frumkin
- H Masuya
- H-J LĂŒdecke
- HD Bon
- HH Kim
- HN Morzaria-Luna
- I KĂŒhn
- J Barton
- J Cornelis
- J DeWolfe
- J Fenger
- J Flagler
- J Hassink
- J Kerrigan
- J L Crompton
- J Lelieveld
- J Maas
- J Smit
- J Yang
- J-D Duh
- J-H Mok
- JAL Mougeot
- JB Kirkpatrick
- JC Berndtsson
- JD Thomsen
- JF Bell
- JL Kidd
- JM Dixon
- JM Hall
- K Dobbs
- K Ikin
- K Lachowycz
- K Stagoll
- KL Dylewski
- KL Wolf
- KL Wolf
- KL Wolf
- KP Beckett
- L TyrvÀinen
- LA Simons
- LM Anderson
- LW DeMarco
- M Cohen
- M Francis
- M Predny
- M Wichrowski
- M Younger
- MA Pedlowski
- ME Dietz
- MG Berman
- ML McKinney
- MS OâNeill
- N Gandelman
- OM Aguilar
- P Dadvand
- PD Relf
- PD Relf
- PD Relf
- PF Mooney
- PG Whitehead
- PM Cozens
- Q Xie
- QF Xiao
- QF Xiao
- R Bakys
- R Ewing
- R Maleike
- R Mitchell
- R Popek
- R Wittig
- RJ Slater
- RP Culp
- S Bell
- SA Park
- SB Warner Jr
- T Bringslimark
- T Fjeld
- T Gregor
- T Ranney
- T-T-H Pham
- TM Poland
- TM Waliczek
- TM Waliczek
- VC Coats
- VI Lohr
- VI Lohr
- VI Lohr
- VI Lohr
- VI Lohr
- VI Lohr
- VI Lohr
- W Gen-Song
- Y Rydin
- YJ Huang
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Parasitic Infections of the Genito-urinary Tract
- Author
- A Abdullah
- A Alexieff
- A Andeh
- A Araventinos
- A Castellani
- A Castellani
- A Castellani
- A Castellani
- A Cioffi
- A Cornell
- A Custem-Franco
- A Donné
- A Donosainfante
- A Elliot
- A Gambier
- A Grassi
- A Grimaldi
- A Hagen
- A Ibrahim
- A LibbĂŽa
- A Lichtenstein
- A Lightstone
- A Longo
- A Loos
- A Massimino
- A Mattei
- A Nogueira
- A Panayotatou
- A Panayotatou
- A Panayotatou
- A Pasma
- A Pena
- A Pijper
- A Pulido-Martin
- A Rauber
- A Riley
- A Schmidt
- A Trabucco
- A Travella
- A Westphal
- A. E. Woodhead
- A. E. Woodhead
- A. E. Woodhead
- A. R. Ferguson
- AA Diaz Colodrero
- AA Grimaldi
- AA Pacheco
- AB Sarewitz
- AC Chandler
- AC Chandler
- AC Chandler
- AC Curtis
- AC Drummond
- AC Lovett-Campbell
- AC Pipkin
- AD Armbrust
- AD Cisneros
- AE Giirsel
- AE Mcculloch
- AE Palmer
- AE Sitzen
- AE Woodhead
- AF Oritz
- AG Atwell
- AG Martynyuk
- AH Burr
- AH Schroeder
- AJ Bearup
- AJ Chalmers
- AJ Chalmers
- AJ Haddow
- AJ Hinkelmann
- AL Chute
- Alves
- AM Atakan
- AM Elwr
- AR Ferguson
- AR Santaella
- AR Stevens
- AS Mohammed
- AS Warthin
- AV Machado
- B Klinger
- B Lewis
- B Meillon
- B. J. Boucin
- BF Pecherskii
- BG Triay
- BH Kean
- BH Kean
- Biccheler
- Biccheler
- C Baumeister
- C Dobell
- C Farmakidis
- C Krakower
- C Marks
- C Romiti
- C Wegelin
- C Younger
- C. H. Venkateswaren
- Cassoute
- CC Hewitt
- CE Hercus
- CE Towne
- CF Craig
- CF Cropper
- CF Engelhard
- CH Barlow
- CH Barlow
- CH Kellaway
- CH Mattei
- CL Deming
- CL Straith
- CM Africa
- CM Greenslade
- Compstok
- Coneglio
- CR Lopez-Neyra
- CV Zerbini
- CW Anderson
- D Antonio Jr.
- D Givrer
- D Jeremié
- D Jeremié
- D Kirsch
- D Soubignon
- D Turner
- D Turner
- D Valle
- D Zanalda
- Dahl
- DB Rosenthal
- DD Albers
- DE Murray
- Desage
- DH Wenrich
- DH Wenrich
- DK Edwards
- DS Ridley
- Dzhavan
- Dztiandznag-Azou
- DâHaennens
- E Baelz
- E Billings
- E Bonnecarrere
- E Castano
- E Colombo
- E Dias
- E Grance
- E Knight
- E Leduc
- E Massal
- E Navahette
- E Nocard
- E Ortiz-Rivas
- E Piraaii
- E Ruggieri
- E Savitsch
- E Truc
- E. A. King
- EA Mills
- EA Rivas
- EB Rogers
- EC Mekie
- ED Casco
- ED Greig
- EF King
- EG Carillo
- EH Cluver
- EJ Shreson
- EK Markell
- EL Cornell
- EL Vila
- EL Vila
- Elsdon-Dew
- EM Fisher
- EP Mumford
- ER Brygoo
- ER Eastman-Nagle
- ER Reay
- ER Riay
- ER Riay
- ES Oliviera
- ES Patton
- ES Pomeroy
- ES Sayegh
- ES Sayegh
- ET Willans
- EW Beach
- EW Masterman
- EW Stunkard
- F Balsamelli
- F Bilger
- F Conant
- F Cozza
- F Dily
- F Dily
- F Graziani
- F Hawking
- F KĂŒchenmeister
- F Lanoeley
- F Lanoeley
- F Lanoeley
- F Loesch
- F Marchand
- F Meersseman
- F Narabayashi
- F Ouzilleau
- F Ronnike
- F Santacruz
- F Smith
- F Yatsenko
- F Yatsenko
- F Zini
- F Zumpt
- F Zumpt
- F. B. Hartley
- F. T. Crossling
- FD Thomas
- FG Cawston
- FG Cawston
- FH Redewill
- FL Nino
- FO Dobritz
- FW Davis
- G Ambomim
- G Armitage
- G Aronica
- G Blanc
- G Bucco
- G Chevalier
- G Cocco
- G Craig
- G Derrico
- G Desusclade
- G Dock
- G Fiorito
- G Francini
- G Franohini
- G Franohini
- G Franohini
- G Franohini
- G Franohini
- G Iacapraro
- G Maclean
- G Millul
- G Olivieri
- G Penso
- G Penso
- G Perl
- G Placitelli
- G Ravasini
- G Rintelen
- G Rossi
- G Sesia
- G Spanu
- G Zedda
- G. B. Bartlett
- GC Allison
- GC Rocca
- GC Thooris
- Gowea
- GW Moor-House
- H Bauer
- H Berner
- H Galliard
- H Galliard
- H Grove
- H Held
- H Jungrans
- H Legrand
- H Leonhardt
- H Odland
- H Sharaf
- H. W. Brown
- HA Baylis
- HA Neves
- Halawani
- Halawani
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- HJ Keutel
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- HL Kretschmer
- HL Liu
- HM Weyrauch
- HO Mönnig
- Houzel
- HR Dew
- HR Sauer
- HW Plaggemeyer
- HW Shik
- I Bennie
- I Bennie
- I Carneri
- I Maisels
- I Maisels
- I. S. Hilmy
- IL Imazappratie
- IR Berger
- J Aleixo
- J Aulong
- J Azzena
- J Bartlakowski
- J Ciurea
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- J Frunikin
- J Gutart
- J Howship
- J Israel
- J Jua
- J Khouri
- J Khouri
- J Khouri
- J Kozlowski
- J Krejci
- J Mackenzie
- J Mackenzie
- J Puig-Syreda
- J Rementeria
- J Rivoir
- J Schwetz
- J Serfling
- J Tanaka
- J Tenenbaum
- J Vergez
- J Walkiers
- J. E. R. Mcdonagh
- J. T. Lewis
- JA Davies
- JA Huarte
- JA Kieser
- JA Ross
- JA Ross
- JB Bernstine
- JB Muir
- JC Ferrer
- JD Baistrocchi
- JD Caeiro
- JE Glen Jr.
- JF Kessel
- JF Kessel
- JF Murray
- JG Feinberg
- JG Rohn
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- JJ Diaz
- JJ Pereda
- JL Pawan
- JM Allende
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- JM Watson
- JM Watson
- JM Watson
- JM Watson
- JM Watson
- JN Lucena
- JR Goyena
- JR Rossell
- JS Gilliam
- JW Bisher
- JW Draper
- JW Macfie
- JW Peabody Jr.
- JW Visiter
- K Matsuda
- K Uhlir
- K. O. Manohar
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- KD Fairley
- KD Fairley
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- KS Shah
- KĂŒlz
- L Alcay
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- L DĂ©jou
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- L Morenas
- L Nevill
- L Oller
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- L Sabadini
- L Sabadini
- L Veau
- L Visnjouski
- L. J. Davis
- L. P. Gabrod
- LA Jankovski
- LA Sanjurjo
- LA Surraco
- LB Goldschmidt
- LC Venturi
- LD ArrĂșes
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- LĂ©ger
- M Bottou
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- M Casile
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- M Erfan
- M Fernandez
- M Gelfand
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- M Gelfand
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- M Girolami
- M Hartmann-Keppel
- M Imbert
- M Imbert
- M Khalil
- M Koller
- M Leclerq
- M Llanos
- M Moore
- M Parent
- M Pesqueira
- M Petzetakis
- M Petzetakis
- M Petzetakis
- M Petzetakis
- M Rodecurt
- M Rodecurt
- M Saujeon
- M Schubert
- M Segurola
- M Sorrentino
- M Straub
- M Touzl
- M. A. Haseeb
- M. H. Sinz
- M. J. Wiittingdon
- MA Afifi
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- O Bollinger
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- P Alvaro
- P Barbellion
- P Brunelli
- P Bruni
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- P Grracd
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- P Holm
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- P Jordan
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- PS Mtganwa
- PW Aschner
- R Bachrach
- R Bernardi
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- R Leuckart
- R Onorata
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- R Santos
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- R. R. Willcok
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- RA RubĂ
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- RL Young
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- RS Hawes
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- S Alzahawi
- S Annecke
- S Annecke
- S Burkert
- S Cerqua
- S Davidovic
- S Ferrandu
- S Gorman
- S Hirst
- S Ishikawa
- S Kamalou
- S Kitamura
- S Markowski
- S Spadaro
- S. A. Seligman
- SG Cowper
- SK Dastidar
- SL Brim
- SR Bushby
- SS Rao
- Surraco
- SV Humphries
- T Bilharz
- T Gerritsen
- TB Menon
- TC Allbutt
- TG Mcdougall
- Trumbull
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- U Cesarono
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- V Compan
- V Compan
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- V Giuduceandrea
- V Nicaise
- V Vermooten
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- VZ Cope
- W Alves
- W Alves
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- WD Winter Jr.
- WE Coutts
- WE Coutts
- WE Coutts
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- WE Erich
- WG Hayward
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- WJ Latham
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- WL Barton
- WL Barton
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- WP Dakin
- WT Cummins
- WV Macfarlane
- WV Macfarlane
- WW Cort
- YM Elgort
- ZD Hahine
- ZT Bercovitz
- ZT Martin
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- 01/01/1959
- Field of study