8 research outputs found
A diagnosis of lymphangioleiomyomatosis in a pregnant woman presenting with a retroperitoneal mass
- Author
- Publication venue
- 'Wiley'
- Publication date
- Field of study
Pulmonary Lymphangioleiomyomatosis (LAM): Examining Oral Contraceptive Pills and the Onset of Disease
- Author
- Publication venue
- 'Mary Ann Liebert Inc'
- Publication date
- 01/01/2003
- Field of study
Lymphomatoide Granulomatose mit primÀrer Manifestation in der Skelettmuskulatur
- Author
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Polymorphic reticulosis (lethal midline granuloma) and lymphomatoid granulomatosis: Identical or distinct entities?
- Author
- AA Liebow
- AA Liebow
- AC Douglas
- ALA Katzenstein
- AR Gibbs
- AS Fauci
- BS Eichel
- CC Yockey
- CE Pena
- DM MacKinnon
- GR Allison
- I Damjanov
- I Friedman
- IM Weisbrodt
- Ivan Stamenkovic
- JD Crissman
- JM Anderson
- JP Stewart
- KTK Chen
- L Michaels
- Marie -Franïżœoise Toccanier
- MJ Saldana
- RA DeRemee
- S Kay
- SC Lee
- SH Kassel
- TJ McDonald
- WF McGuirt
- YS Fu
- Yusuf Kapanci
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Linfangioleiomiomatose pulmonar Pulmonary Lymphangioleiomyomatosis
- Author
- Aubry MC
- Avilla NA
- Baldi S
- Bernstein SM
- Bionetti F
- Brentani MM
- Carlos Roberto Ribeiro Carvalho
- Chu SC
- Colley MH
- Cornog JL
- Corrin B
- Costello LC
- De la Fuente J
- Desurmont S
- Eliasson AII
- Enterline HT
- Flores-Delgado G
- Fukuda Y
- Graham ML 2nd
- Hayashi T
- Johnson SR
- Kambe A
- Kang HW
- Kelly J
- Kerr LA
- Kitaichi M
- Kreisman H
- Lieberman J
- Matsui K
- Matsui K
- Maziak DE
- McCarthy KS Jr
- Nussbaun E
- OâBrien JD
- Pedro Medeiros Junior
- Radermecker M
- Roach ES
- Rosendal P.
- Rossi GA
- Shen A
- Smolarek TA
- Sobonya RE
- StĂĄvale MLS
- Sullivan EJ
- Taylor JR
- Urban T
- Urban T
- Usuki J
- Von Stössel E.
- Wahedna I
- Yockey CC
- Zahner J
- Zanella A
- Publication venue
- Sociedade Brasileira de Pneumologia e Tisiologia
- Publication date
- 01/02/2004
- Field of study
Linfangioleiomiomatose pulmonar (LAM) Ă© uma doença rara, de etiologia desconhecida, que basicamente afeta mulheres jovens no perĂodo fĂ©rtil de sua vida. Clinicamente, manifesta-se atravĂ©s de dispnĂ©ia progressiva, pneumotĂłrax de repetição, tosse seca e, menos freqĂŒentemente, por quilotĂłrax e escarros hemoptĂłicos. Essas alteraçÔes surgem devido Ă proliferação anormal de cĂ©lulas de mĂșsculo liso no parĂȘnquima pulmonar, linfonodos e em outros tecidos. Mais recentemente, estudos citogenĂ©ticos verificaram a presença de mutaçÔes do gene TSC-2 em cĂ©lulas de angiomiolipoma renal e linfonodos abdominais de pacientes com LAM, indicando uma possĂvel origem para as lesĂ”es hamartomatosas da doença. Radiologicamente, caracteriza-se pela presença de infiltrado intersticial reticulonodular e sinais de hiperinsuflação ao radiografia de tĂłrax. Na tomografia computadorizada de alta resolução, cistos de paredes finas, localizados centralmente, sĂŁo visibilizados por todo o parĂȘnquima do pulmĂŁo. O ultrassom e a tomografia de abdome podem revelar angiomiolipomas renais e linfonodomegalias retroperitoneais. Meningeomas tambĂ©m podem estar associados, porĂ©m a sua presença deve sempre levar Ă pesquisa de esclerose tuberosa. Funcionalmente, a doença caracteriza-se por um distĂșrbio ventilatĂłrio obstrutivo, de carĂĄter progressivo, com hiperinsuflação pulmonar e diminuição da difusĂŁo de monĂłxido de carbono. Apesar da ausĂȘncia de comprovação quanto Ă eficĂĄcia, o principal tratamento utilizado ainda Ă© o anti-estrogĂȘnico e constitui-se de oofarectomia, progesterona contĂnua, tamoxifeno e anĂĄlogos de GnRH. AlĂ©m desse, a realização de transplantes pulmonares tem elevado para alĂ©m de dez anos a sobrevida mĂ©dia das pacientes.<br>Lymphangioleiomyomatosis (LAM) is a rare lung disease of unkwnon etiology that frequently affects women in childbearing age. Clinically it manifests itself by and pneumothorax. Chylous pleural effusions and hemoptisis occur less frenquently. All these fenomena results from the abnormal smooth muscle proliferation in the lung parenchima. Lymph-nodes, small airways and blood vessels. More recently cytogenetic studies disclosed mutations of the TSC-2 gene in cells of renal angiomyolipoma and/or abdominal lymph nodes, pointing towards a possible origin of the hamartomatous lesions. Chest radiography may appear normal or yield reticulonodular infiltrates and signs of hyperinsuflation. At HRCT scans, multiple thin-walled cysts can be seen over the lung parenchyma. Abdominal imaging by either ultrasound or CT may show renal angiomyolipomas and retroperitoneal lymph node enlargement. Meningeomas may also be associated but their presence requires testing for tuberous sclerosis complex. Physiologically LAM is characterized by progressive airflow obstruction, air trapping and gastransfer impairment. Estrogenic suppression with either oophorectomy, deposit progestogens, tamoxifen and GnRh analogs, is still the main treatment. In addition to this therapy lung transplantations have increased patients median survival rates by more than ten years
Pathologie und Radiologie der Lungenfibrosen
- Author
- A Brunner
- A Burkhardt
- A Burkhardt
- A Cantin
- A Hany
- AA Liebow
- AA Liebow
- AA Liebow
- AG HĂšppleston
- AH Niden
- AP Fishman
- AU Desjardins
- B Felson
- BA Keogh
- BR Line
- C Kuhn
- C Mittermayer
- C Parkinson
- CB Carrington
- CB Carrington
- CB Carrington
- CC Yockey
- CM BĂŒsing
- CT Lee
- CV Strimlan
- D Heath
- DE Bennet
- DE Niewochner
- DH Bowden
- DM Gould
- DP Penney
- DS Klein
- E Uehlinger
- EA Gaensler
- EA Gaensler
- EJ Campbell
- ER Weibel
- F Basset
- FF Collins
- FL Jennings
- G Fischer
- G Fruhman
- G Könn
- GA Lillington
- GA Lillington
- GG Pietra
- GL Snider
- GM Turino
- GR Epler
- GS Davis
- GW Hunninghake
- H Benzer
- H Cottier
- H Eisenberg
- H Kappus
- H Kitamura
- H Matthys
- H Meessen
- H Pinkerton
- H Spencer
- H Spencer
- H-G Lasch
- HS Stender
- HW Knipping
- HY Reynolds
- HY Reynolds
- IH Kerr
- IYR Adamson
- IYR Adamson
- IYR Adamson
- IYR Adamson
- J Bignon
- J Bignon
- J Freyschmidt
- J-O Gebbers
- JD Fulmer
- JD Fulmer
- JF Ray
- JG Scadding
- JG Scadding
- JG Scadding
- JG Scadding
- JG Scadding
- JH Robertson
- JJ Coalson
- JM Lauweryns
- K Wurm
- KFW Hinson
- KL Pinsker
- KM Reiser
- L Hamman
- L Hamman
- L Kreel
- LC Dearden
- LC Watters
- LE Hines
- LK Jackson
- LM Parvinen
- M Amthor
- M Bachofen
- M Bachofen
- M Lamotte
- M Turner-Warwick
- M Turner-Warwick
- M Turner-Warwick
- M Turner-Warwick
- M Turner-Warwick
- MG Mustafa
- N Vetter
- NJ Gross
- NL MĂŒller
- P Dalquen
- P Gross
- P Thomas
- P Wichert von
- P Wichert von
- P Wiehert von
- P Wiehert von
- P Wiehert von
- PH Wright
- PH Wright
- PHG Gell
- R Catane
- R Rubin
- R Rubin
- RB Engelstad
- RB Engelstad
- RB Weiss
- RC Bone
- RC Rosan
- RF Bils
- RG Crystal
- RG Crystal
- RG Fraser
- RME Seal
- RP Daniele
- RR Tubbs
- RW Spann
- S MönkÀre
- S Sutinen
- SF Ryan
- SP Hammar
- T Mc Loud
- TC Medici
- TV Colba
- U Bleyl
- U Bleyl
- U Bleyl
- U Costabel
- U Costabel
- U MĂŒller
- UH Cegla
- UN Riede
- V Hecht
- W Eger
- W Giese
- W Haas
- W Hartung
- W Sandritter
- W Schermuly
- WD Reinbold
- WJ Sibbald
- WM Rumansik
- WS Rau
- WS Rau
- WS Rau
- WS Rau
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- 01/01/1989
- Field of study
Treatment of Acute Respiratory Distress Syndrome in the Poisoned Patient
- Author
- A Aghabiklooei
- A Chela
- A Combes
- A Dushianthan
- A Emad
- A Esteban
- A Harris
- A Marruchella
- A Mercat
- A Pirjavec
- A Smith
- A Walubo
- AB Bille
- AE Mulberg
- AE Wolters
- AF Hernandez
- AJ Greenspon
- AJ Kansagra
- AJ Scalzo
- AM Goetz
- AS Slutsky
- AS Slutsky
- B Feingold
- B MĂ©garbane
- B MĂ©garbane
- B Nemery
- B Sangster
- B Walder
- BC Friedman
- BJ Woelke
- BM Tang
- C Delclaux
- C Guérin
- CA Lindsay
- CC Yockey
- CE Mapp
- CF Chian
- CJ Hauser
- CN Schmickl
- CT Bolliger
- CY Wang
- D Bracco
- D Brodie
- D Gruson
- D Henzler
- D Jiang
- D Leduc
- D Talmor
- DA Tanen
- DE Gossman
- DG Ashbaugh
- DM Cohen
- DP Bansal
- DR Varma
- DW Lange de
- DW Lange de
- E Azoulay
- E Damiani
- E HjortsĂž
- E Jonge de
- EL Costa
- F Liu
- F Urdaneta
- FA Herbert
- FL Rock
- FR Sidell
- G Ainslie
- G Eastwood
- G Eshel
- G MacLaren
- G Vanzetto
- GB Zuckerman
- GJ Peek
- GJ Peek
- GK Bysani
- GM Thomas
- GU Meduri
- GU Meduri
- H Ashrafian
- H Buscher
- HE Lim
- HT Le
- I VadĂĄsz
- IB Seidenschwanz
- IW Soliman
- J Borak
- J Petersson
- J Phua
- J Villar
- J Villar
- JA Nightingale
- JB Cole
- JC Chevrolet
- JC Jackson
- JC Möller
- JD Hill
- JF Murray
- JF Pittet
- JG Chen
- JJ Howard
- JM Byers
- JM Niehoff
- JM Samet
- JP Kehrer
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- JR Bennion
- JV Peter
- JY Fagon
- K Doi
- K Kono
- K Kunimasa
- K Lee
- K Miller
- K Modelska
- KA Barsness
- KE Marciniak
- L Brochard
- L Burry
- L Franchi
- L Gattinoni
- L Papazian
- L Szinicz
- L Tsonis
- L Xu
- LB Ware
- LJ Smith
- LK Garrettson
- M Boussarsar
- M Licker
- M Luis
- M Martin
- M Piagnerelli
- M Rahman
- M Serinken
- M St-Onge
- M Suarez
- M Tenenbein
- MA Taylor
- MB Amato
- MB Amato
- MJ Harvey
- MJ Knapp
- ML Hernandez
- MO Meade
- MR Suchyta
- MS Dai
- MW Lai
- N Batchelor
- N Cohen
- N Tanaka
- ND Ferguson
- NE Alexis
- NJ McKeown
- NK Baban
- NR Aggarwal
- OJ Bienvenu
- P Blankman
- P Mecca
- P Pelosi
- P Pentel
- P Terragni
- PA Chyka
- PA Mazzeo
- PB Bitterman
- PJ Barnes
- PJ Foley
- PM Suter
- PP Terragni
- PR Powell-Jackson
- R Agarwal
- R Brandenburg
- R Brandenburg
- R Brandenburg
- R Kass
- R Magazine
- R Masson
- R Ochiai
- R Tio
- R Tiruvoipati
- R Wenstone
- RA Promisloff
- RE Rendall
- RG Brower
- RG Brower
- RH Poe
- RK Linskens
- RM Aris
- RM Varnell
- S Brinkman
- S Brinkman
- S Han
- S Jeyaseelan
- S Kamholz
- S Rabinovitch
- S Sun
- S-C Lim
- SC Donnelly
- SG Moreno
- SH Abid
- SH Lee
- SK Gupta
- SL Hu
- SN Chugh
- SR Guharoy
- SS Wahba
- T Dolinay
- T Kawai
- T Mahmood
- T Muders
- T Okumura
- T Rhen
- T Yamada
- TE Stewart
- The Australia and New Zealand Extracorporeal Membrane Oxygenation (ANZ ECMO) Influenza Investigators
- TJ Lemoine
- TJ Toward
- TJ Whitmore
- TR Martin
- TR Weber
- TT Catchings
- U Trumpener
- V Lindén
- V PettilÀ
- VL Serebruany
- VM Ranieri
- W Alhazzani
- WB Frierson
- WE Thornton
- WH Lyle
- WN Burton
- Y Finkelstein
- Y Kamijo
- YL Lee
- Publication venue
- Publication date
- 07/10/2015
- Field of study
Search for Higgs boson and observation of Z boson through their decay into a charm quark-antiquark pair in boosted topologies in proton-proton collisions at âs=13 TeV
- Author
- Aarrestad T
- Abbaneo D
- Abbiendi G
- Abbott M
- Abbrescia M
- Abdullin S
- Abreu A
- Acharya H
- Acosta D
- Acosta HE
- Adam W
- Adamidis K
- Adams E
- Adams M
- Adams T
- Addesa F
- Adloff C
- Adzic P
- AdĂĄn DP
- Afanasiev S
- Agapitos A
- Agarwal G
- Agram J
- Aguilar-Benitez M
- Agyel D
- Ahmad A
- Ahmad M
- Ahmad WH
- Ahmed A
- AimĂš C
- Akchurin N
- Akgun B
- Akpinar A
- Al-Mashad MA
- Albert A
- Albrecht A
- Albrecht S
- Albrow M
- Alcerro LA
- Aleksandrov A
- Alexander J
- Alhusseini M
- Alimena J
- Alison J
- Allmond B
- Almond J
- Alonso AG
- Alpana A
- Alvarez JR
- Alverson G
- Alves BFS
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- Aly R
- Alyari M
- Amapane N
- Amaral SSD
- Amarilo KM
- Ambrozas M
- Amendola C
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- Amsler C
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- Saltzberg D
- Salur S
- Salvatico R
- Salvi G
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- Samalan A
- Sanchez A
- Sanchez MCDLB
- Sandeep K
- Sanders S
- Santanastasio F
- Santocchia A
- Santoro A
- Santos AZC
- Saoulidou N
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- Savitskyi M
- Savoiu D
- Savoy-Navarro A
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- Schnake S
- Schnetzer S
- Schonbeck N
- Schroeder N
- Schröder M
- Schuh T
- Schuler S
- Schulte J
- Schwandt J
- Schwanenberger C
- Schwarz D
- Schweiger K
- Schöfbeck R
- SchĂŒtze P
- Sciacca C
- Scodellaro L
- Scott E
- Scribano A
- Sculac T
- Seez C
- Sehrawat A
- Seidel M
- Seidita R
- Seixas J
- Sekhar S
- Sekmen S
- Selivanova D
- Selvaggi G
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- Sen S
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- Seo H
- Setti F
- Sexton-Kennedy E
- Sfar HR
- Sguazzoni G
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- Shang V
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- Shumka E
- Shvetsov I
- Si W
- Siado J
- Siddireddy P
- Siikonen H
- Sikdar A
- Sikler F
- Silva GC
- Silva P
- Silvestris L
- Simkina P
- Simone F
- Simonetto F
- Simonis H
- Simpson F
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- Simsek C
- Singh J
- Singla A
- Sirois Y
- Siroli G
- Siviero F
- Skinnari L
- Skovpen K
- Skovpen Y
- Slabospitskii S
- Smirnov V
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- Smith N
- Smith V
- Smith W
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- Sola V
- Solano A
- Soldi D
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- Sommerhalder M
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- Sorrentino G
- Sosnov D
- Sousa VDS
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- Spanier S
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- Spitzbart D
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- Staiano A
- Stakia A
- Stamerra A
- Starodumov A
- Steen A
- Steggemann J
- Stein A
- SteinbrĂŒck G
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- Stephans G
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- Strologas J
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- Suarez I
- Sulimov V
- Sultanov G
- Summers S
- Sun X
- Suryadevara P
- SurĂĄnyi O
- Susa T
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- Swain S
- Swartz M
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- Szleper M
- Sznajder A
- Sözbilir Ă
- Tabb W
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- Takahashi Y
- Tali B
- Taliercio A
- Tamulaitis G
- Tani L
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- Tcherniaev E
- Teague D
- Tedeschi T
- Tekten S
- Teles PR
- Templ S
- Tenchini R
- Terkulov A
- Teroerde M
- Terrill W
- Teryaev O
- Tews A
- Teyssier D
- Thachayath A
- Thakur S
- Thayil S
- Theofilatos K
- Thiel M
- Thieman J
- Thom J
- Thomas L
- Thomas S
- Thomas-Wilsker J
- Tiras E
- Tishelman-Charny A
- Titov M
- Tiwari P
- Tkaczyk S
- Tlisova I
- Tok U
- Tomalin I
- Tomei TRFP
- Toms M
- Tonelli G
- Tonjes M
- Tonon N
- Topaksu AK
- Tornago M
- Toropin A
- Torterotot L
- Tosi M
- Tosi S
- Townsend A
- Tramontano R
- Tran N
- Tran T
- Trapote A
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- Trevisani N
- Tricomi A
- Trocino D
- Tropea P
- Trujillo DB
- Tsamalaidze Z
- Tsatsos A
- Tsipolitis G
- Tsirou A
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- Tully C
- Tumasyan A
- Tuo S
- Tuominen E
- Tuominiemi J
- Turini N
- Turkcapar S
- Tuuva T
- Tuve C
- Tytgat M
- Tziaferi E
- Uchida K
- Ujvari B
- Ulmer K
- Ulrich R
- Umoret G
- Uniyal R
- Uplegger L
- Usai E
- Uslan E
- Uttley G
- Uvarov L
- Uzunian A
- Vaandering E
- Vage L
- Vagnerini A
- Vai I
- Valencia FV
- Valsecchi D
- Valuev V
- Van De Klundert M
- Van Den Bossche N
- van der Linden J
- Van Doninck W
- Van Hove P
- Van Mechelen P
- Van Onsem G
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- Vander Donckt M
- Vander Velde C
- Vanlaer P
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- Villalba CV
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- Volobouev I
- Von Cube R
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- Vourliotis E
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- Wachirapusitanand V
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- Watson I
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- Wickramarathna D
- Wiedenbeck S
- Wieland S
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- Wissing C
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- WĂŒrthwein F
- Xiang Y
- Xiao J
- Xiao M
- Xiao R
- Xie S
- Xie W
- Yagil A
- Yalvac M
- Yan F
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- Yao Y
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- Yohay R
- Yoo H
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- Yoon I
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- Yu D
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- Yumiceva F
- Yusuff I
- Yzquierdo AP
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- Zaleski S
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- Zarubin A
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- Zecchinelli A
- Zeid SA
- Zeinali M
- Zeuner W
- Zghiche A
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- Zhizhin I
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- Ziemons T
- Zilizi G
- Zipper N
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- Zoi I
- Zolkapli Z
- Zorbakir I
- Zotto P
- Zotz A
- Zou R
- Zucchetta A
- Zumerle G
- Zuo X
- Zuolo D
- Zygala L
- Ălvarez CR
- Publication venue
- Publication date
- 01/01/2023
- Field of study