Primary Perivascular Epithelioid Cell Tumor (PEComa) of the Bladder: A Case Report With 2-Years of Follow-Up and Review of Current Literature

Primary perivascular epithelioid cell tumors (PECo- mas) are a variety of rare mesenchymal neoplasm about which very little is known. Due to the small number of cases reported in the literature, there is no consensus about a classi fi cation of this disease that might in fl uence clinical practice and disease management. This article describes a primary PEComa of the bladder in which surgical strategy has been adopted. This strategy has shown good results, showing no local or distant relapse after 2 years of follow-up, without the need of adjuvant therapy. This might be the correct strategy in the treatment of urinary PEComas