A Rare Case Report of Eight Syndrome Secondary to Syringomyelia Associated with Type I Chiari Malformation

Eight syndrome is defined as the combination of a unilateral conjugate gaze palsy and ipsilateral seventh cranial nerve palsy. It may occur as a result of demyelinating, vascular, infectious, or compressive lesions of the brainstem localized to the caudal pontine tegmentum. A 43-year-old woman was admitted to our clinic with complaints of headache, inability to look to the left, and weakness on the left side of her face. The complaints had begun abruptly about a month before her admission. Suboccipital decompression surgery for type I Chiari malformation had been performed 10 years earlier. Neuro-ophthalmological examination revealed left-sided horizontal gaze palsy and anisocoria. Cranial and cervical magnetic resonance images revealed cerebellar tonsillar herniation and syringomyelia, the latter of which was considered to be the cause of eight syndrome. No interventions were performed, and periodic follow-up was advised on neurosurgical consultation. Left gaze palsy and facial palsy recovered almost completely in three months, while the anisocoria persisted. Syringomyelia should be considered among the causes of horizontal gaze palsy plus ipsilateral seventh nerve palsy, termed as eight syndrome. Clinical suspicion and appropriate radiological examination can aid in the diagnosis

A rare complication of Ramsey Hunt Syndrome: Sınus vein thrombosis

Ramsay-Hunt Syndrome (RHS) is a rare affection characterized by peripheral facial paralysis (PFP), skin eruption in the auricular canal and cochleovestibular symptoms. It is produced by varicella-zoster virus(VZV) reactivation at the geniculate ganglia. In elderly and immunocompromised individuals, the virus may reactivate to produce shingles (zoster). After zoster resolves, many elderly patients experience postherpetic neuralgia. Uncommonly, VZV can spread to large cerebral arteries to cause a spectrum of large-vessel vascular damage, ranging from vasculopathy to vasculitis, with stroke. In immunocompromised individuals, especially those with cancer or acquired immunodeficiency syndrome, deeper tissue penetration of the virus may occur (as compared with immunocompetent individuals), with resultant myelitis, small-vessel vasculopathy, ventriculitis, and meningoencephalitis. The polymerase chain reaction (PCR) analysis of cerebrospinal fluid remains the mainstay for diagnosing the neurologic complications of VZV during life. We report a case of Ramsay Hunt syndrome complicated with cerebral venous thrombosis. Patient received treatment with acyclovir and anticoagulation. Early treatment with acyclovir therapy and anticoagulation could improve the recovery rate of facial nerve palsy and sinus vein thrombosis

Ramsay Hunt Sendromunun Nadir Bir Komplikasyonu: Sinüs Ven Trombozu

Ramsay Hunt syndrome is a rare affection characterized by peripheral facial paralysis, skin eruption in the auricular canal and cochleovestibular symptoms. It is produced by varicella zoster virus (VZV) reactivation in the geniculate ganglia. In elderly and immunocompromised individuals, the virus may reactivate to produce shingles (zoster). After zoster resolves, many elderly patients experience postherpetic neuralgia. Uncommonly, VZV can spread to large cerebral arteries to cause a spectrum of large-vessel vascular damage, ranging from vasculopathy to vasculitis, with stroke. In immunocompromised individuals, especially those with cancer or acquired immunodeficiency syndrome, deeper tissue penetration of the virus may occur (as compared with immunocompetent individuals), with resultant myelitis, small-vessel vasculopathy, ventriculitis, and meningoencephalitis. Polymerase chain reaction analysis of cerebrospinal fluid remains the mainstay for diagnosing the neurologic complications of VZV during over a patient;amp;#8217;s lifetime. We report a case of Ramsay Hunt syndrome complicated with cerebral venous thrombosis. The patient received treatment with acyclovir and anticoagulation. Early treatment with acyclovir therapy and anticoagulation could improve the recovery rate of facial nerve palsy and sinus vein thrombosis.Ramsay Hunt sendromu akut olarak gelişen fasiyal felç ve buna neden olan varisella zoster virüsü (VZV)’ne bağlı dış kulak kanalının ve kulak derisinin veziküler lezyon birlikteliğidir. Bell felci gibi %50 spontan iyileşme sıklığı olmasına rağmen Ramsay Hunt sendromu nun morbiditesi daha yüksek, komplikasyonları daha tehlikelidir. VZV birkaç 10 yıllık latans devrinden sonra, özellikle yaşlılarda ve im münyetmezliği olan kişilerde, genikulat gangliyonunda herpes zoster veya Ramsay Hunt sendromu şeklinde reaktivasyon gösterebilir. Nadir olarak, VZV büyük serebral arterlere yayılarak vaskülopati ya da vaskülite neden olarak strokla sonuçlanabilir. Kanser, immünyet mezlik sendromu gibi immünyetmezliği olan kişilerde virüs daha derin dokulara penetre olabilir. Ender olarak miyelit, küçük damar vaskülopatisi, sinüs ven trombozu, serebellit, ensefalit, ventrikülit, kalıcı işitme kaybı gibi komplikasyonlar gelişebilir. VZV için kan ve beyin omurilik sıvısında yapılan çalışmalar arasında en hızlı ve sensitif test polimeraz zincir reaksiyonudur. Biz serebral sinüs ven trom bozu ile komplike olan Ramsay Hunt sendromu olan bir olgu sunduk. Hastaya antikoagülasyon ve asiklovir tedavisi verildi. Erken te davi ile fasiyal sinir felci ve sinüs ven trombozu düzelebilir

Rarebit perimetry in the evaluation of visual field defects in idiopathic intracranial hypertension

PURPOSE. Rarebit perimetry (RBP) is a new perimetric technique that has been reported as a sensitive test for the evaluation of the neural structure of the visual system. The aim of this study was to compare RBP with standard automated perimetry in detecting the visual field defects of patients with idiopathic intracranial hypertension (IIH)