Apikal Hipertrofik Kardiyomyopati

Abstract

Apical hypertrophic cardiomyopathy (AHCM) is one form of hypertrophic cardiomy¬opathy that is the most common hereditary cardiac disease and the most frequently found cardiomyopathy. AHCM has typical findings on electrocardiography, echocardiography and ventricu¬lography. The electrocardiographic changes and symptoms associated with AHCM often mimic acute coronary syndromes and coronary angiogram can be performed with pre-diagnosis of coronary artery disease several times. Physicians should consider AHCM in case of patients who have similar electrocardiographic changes and symptoms with coronary artery disease.Apikal hipertrofik kardiyomyopati (AHCM), en sık gözlenen kalıtsal kalp hastalığı ve kardiyomyopati olan hipertrofik kardiyomyopatinin bir formudur. AHCM elektrokardiyografi, ekokardiyografi ve ventrikülografide tipik bulgulara sahiptir. Elektrokardiyografik bulgular ve semptomlar akut koroner sendromları taklit edebilir ve koroner arter hastalığı ön tanısı ile koroner anjiyografi birkaç kez yapılabilir. Koroner arter hastalığı semptom ve elektrografik değişiklikle başvuran hastalarda AHCM tanısı akla gelmelidir

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