Prosthodontic Management of Papillon –Lefevre syndrome – A case report

Abstract

Papillon-Lefevre syndrome is a rare autosomal recessive condition in nature. It manifests as hyperkeratosis of the palms and soles along with destruction of the periodontal support of both the primary and secondary dentition. Periodontal destruction may be seen soon after the beginning of eruption of primary teeth resulting in loss of teeth at the age of 4-5 yrs and loss of permanent teeth at the age of 13-15 yrs. The third molars may be protected from the periodontal destruction and bone loss. An 18 year old male patient diagnosed with Papillon-Lefevre syndrome was referred to the Department of Prosthodontics, Rural Dental College and Hospital, Loni,for prosthetic rehabilitation. The extra-oral findings resembled the characteristic features of Papillon-Lefevre syndrome like palmar and plantar hyperkeratosis. Intra-oral examination revealed upper and lower edentulous arches except the fully erupted third molars in both the arches. A case report of such a rare condition occurring in a teenage patient and its prosthetic management for restoring the patient’s functional needs and social well being is presented in this article.Key Words: Papillon-Lefevre Syndrome, Prosthetic rehabilitation, Telescopic Dentur