Thrombosis in BehÇet's disease (BD) is not uncommon and venous occlussions affecting the venae cavae and their tributaries may result in during the course of the disease. Pseudo-Kaposi's sarcoma is characterized with a nodule or plaque which may lead to a painful ulceration. The development of the Mali's syndrome, an entity of Pseudo-Kaposi's sarcoma, usually follows stasis dermatitis and occurs on the lower extremities. In this report, we present a Pseudo-Kaposi's sarcoma case a 25-year-old male during the fourth year of the diagnosis with BD. The association of Pseudo Kaposi's sarcoma and BehÇet's disease has never- to our knowledge- been reported before.Thrombosis in BehÇet's disease (BD) is not uncommon and venous occlussions affecting the venae cavae and their tributaries may result in during the course of the disease. Pseudo-Kaposi's sarcoma is characterized with a nodule or plaque which may lead to a painful ulceration. The development of the Mali's syndrome, an entity of Pseudo-Kaposi's sarcoma, usually follows stasis dermatitis and occurs on the lower extremities. In this report, we present a Pseudo-Kaposi's sarcoma case a 25-year-old male during the fourth year of the diagnosis with BD. The association of Pseudo Kaposi's sarcoma and BehÇet's disease has never- to our knowledge- been reported before