Abrikossoff tumor is an uncommon neoplasm of soft tissue, mostly benign but cases of aggressive malignant form with metastases were also reported. GCT can occur at any area of the body (head and neck are the most common but also limbs and vulva). Local surgical excision with wide margin is a treatment of choice but possibility of recurrence, multiple location and malignancy in time must be considered. This report presents a rare pediatric case with Abrikossoff tumor.Abrikossoff tumor is an uncommon neoplasm of soft tissue, mostly benign but cases of aggressive malignant form with metastases were also reported. GCT can occur at any area of the body (head and neck are the most common but also limbs and vulva). Local surgical excision with wide margin is a treatment of choice but possibility of recurrence, multiple location and malignancy in time must be considered. This report presents a rare pediatric case with Abrikossoff tumor
