Congenital aortic valve atresia is usually part of a developmental anomaly usually called
‘hypoplastic left-heart syndrome’. To the best of our knowledge, most reported cases of aortic
atresia have been associated with hypoplasia of the ascending aorta, of the left ventricle, and of
the mitral valve. We report a patient presenting with aortic atresia with a ventricular septal
defect and a normally sized left ventricle. (Cardiol J 2011; 18, 3: 304–306
