Carcinoma ex-pleomorphic nonmalignant tumour (Ca ex PA, CXPA) is a rare, aggressive, poorly understood malignancy of the exocrine gland. The clinical findings typical of this neoplasm embrace history of a slow growing, ulcerated, painless mass that enlarges speedily. The current definition of Ca ex PA became widely accepted in the second half of the twentieth century. It is uncommon, having a prevalence rate of 5.6 cases per 100,000 malignant neoplasms and a yearly incidence rate of 0.17 tumours per 1 million persons in the world. The cancer is found predominantly in the sixth to eighth decades of life and is slight female predilection. 
