Objective: Anaplastic liposarcoma of the head is an extremely rare entity. Seventy-seven cases of head and neck liposarcomas have been reported in the world literature since 1911. Radical surgery is the form of treatment advised.Clinical presentation: Authors report the case of a 62 years old female patient admitted in our institution for a giant extracranial tumor (122/88 mm), developed insidious over a period of 3 years and neglected. The patient agreed surgery only for the epicranial tumor. The lesion was completely removed. Postoperatory outcome was excellent concerning this tumor, although the histopathological result was not that great: high anaplastic liposarcoma.Conclusion: Liposarcoma of the scalp is rare. Diagnosis is made histologically. The histopathologic variant influences clinical behavior and prognosis. The treatment of choice is wide surgical excision. 
