Cistični limfangiom mezenterija jejunuma koji oponaša akutni apendicitis: prikaz slučaja

Abstract

Cystic lymphangiomas of the small bowel mesentery are rare manifestations of intra-abdominal tumors. Usually, they are discovered incidentally during examination for an unrelated abdominal illness. We present a case of a 4-year-old boy who was admitted to our hospital because of the right lower quadrant acute abdominal pain suspect of acute appendicitis. At laparotomy, a giant, cystic, encapsulated and lipomatous mesenterial mass was found, 15x15x10 cm in size, infiltrating the jejunum. The tumor was located 70 cm from Treitz’s ligament. Extirpation of tumor mass with intestinal resection of the involved loops was necessary. Pathologic examination confirmed the diagnosis of mesenteric cystic lymphangioma. Although they are rare, cystic mesenteric lymphangiomas should be considered as a possible cause of acute abdomen and treated with surgical resection. Prognosis after surgical removal is excellent.Cistični limfangiomi mezenterija tankog crijeva pripadaju rijetkim intraabdominalnim tumorima. Obično se nađu slučajno tijekom obrade zbog neodređene trbušne boli. Prikazuje se slučaj četverogodišnjeg dječaka hospitaliziranog zbog bolova u donjem desnom abdominalnom kvadrantu sumnjivih na akutnu upalu crvuljka. Nakon učinjene laparotomije našla se velika, cistična, inkapsulirana, lipomatozna mezenterijska masa veličine 15x15x10 cm koja je infiltrirala jejunum. Tumor je bio smješten oko 70 cm aboralno od Treitzova ligamenta. Učinjena je ekstirpacija tumora s infiltriranom jejunalnom vijugom. Patohistološki nalaz je potvrdio dijagnozu mezenterijskog cističnog limfangioma. Iako rijetki, cistični mezenterijski limfangiomi se mogu smatrati mogućim uzrokom akutne abdominalne boli i liječiti kirurškom resekcijom. Prognoza je nakon kirurškog odstranjenja odlična

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