Binder's Syndrome also known as Maxillo-Nasal Dysplasia is a developmental disorder primarily affecting the anterior part of the maxilla and nasal complex (nose and jaw). It is a rare disorder and the causes are unclear. It is an uncommon condition characterized by a retruded mid-face with an extremely flat nose. Hereditary factors and vitamin D deficiency during embryonic growth have been researched as possible causes. Morphological characteristics of the syndrome are of fundamental importance for the correct diagnosis and treatment planning of these patients. We hereby report to you a rare case of Binder's syndrome with clinical, radiographic features and discussed the treatment options