Sacrococcygeal teratoma (SCT) is the most common neoplasm in neonates and the most common germ cell tumor in
children. SCT with malignant elements is very rare in infants. Prenatal diagnosis is of exceptional importance for the adequate
fetal intervention, evaluation of perinatal complications and the selection of the optimal treatment. The treatment
of choice is complete surgical resection. Postsurgical approach for immature teratoma with malignant elements is not well
established. Considering the risk for tumor recurrence, long term follow-up is mandatory. We report clinical, laboratory,
radiological and histological findings, surgical procedure, and follow-up in the preterm female neonate with immature SCT
with malignant elements