A young woman affected by Turner syndrome undergoes periodic cardiac monitoring. Her last ECG documented QT prolongation. QT prolongation is reported in patients with Turner syndrome. This electrophysiological abnormality is probably due to an intrinsic defect in the regulation of the cardiovascular system. Although a long QT is more likely to be found in these patients, no severe life-threatening tachyarrhythmias have been described so far. Paediatricians should reassure Turner patients about the prognosis of this electrophysiological abnormality while recommending the cardiologic follow up
