Acute intermittent porphyria (AIP) is caused by the
deficiency of porphobilinogen deaminase, a haem synthesis
enzyme, giving rise to crises characterized by abdominal pain,
tachyarrythmias and psychiatric features. Anaesthesia in AIP
is challenging because it has to avoid precipitating an attack.
We report a case of a lady with AIP who underwent total
abdominal hysterctomy whose anaesthesia was uneventful.peer-reviewe