The scalp tumor - turban tumor syndrome: case study

Abstract

Pojava multiplih tumora kožnih adnexa prvi puta je opisana krajem devetnaestoga stoljeća i danas je poznata pod imenom Turban tumor sindrom, ili po autorima koji su ga opisali Brooke-Spieglerov sindrom. Dva puta češće se javlja kod žena, obično u prvom ili drugom deseteljeću života, u obliku kožnih čvorića lokaliziranih uglavnom na koži vlasišta. Punu veličinu tumori postignu nakon pedesete godine života kada se bolesnici najčešće i javljaju liječniku. Dugo rastu, ne stvarajući poteškoće. Turban tumori pokazuju tipičnu histološku sliku, a liječenje im je isključivo kirurško. U radu smo prikazali slučaj bolesnice koja je imala više kožnih tumora u vlastištu, od koji je najveći bio promjera 23 cm, a težio je 2200 grama. Patohistološki nalaz odgovarao je proliferirajućoj pilarnoj-trihilemalnoj cisti.The appearance of multiple tumors of the skin adnexa was first described in the late nineteenth century and today is known as the Turban Tumor Syndrome, or by authors who described it, the Brooke-Spiegler Syndrome. It is twice more common in women, usually in the first or second decade of life in the form of skin nodules localized mainly in the skin of the scalp. The tumors reach their full size after fifty years of age, when patients are most likely to visit their doctor. They grow for a long period of time without creating difficulties. Turban tumors show typical histology and their treatment is exclusively surgical. In this paper, we present a case of a patient who had multiple skin tumors in the skin adnexa, with the largest one being 23 cm in diameter and weighing 2200 grams. Pathohistological morphological features: proliferating pilar-trichilemmal cyst

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