DP Judge

HR Weiss

M Werkmann

R Savini

English

PubMed

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Brace treatment in an infantile/juvenile patient with progressive scoliosis due to Marfan’s syndrome

POSTER PRESENTATION Open Access
Brace treatment in an infantile/juvenile patient
with progressive scoliosis due to Marfan’s
syndrome
HR Weiss*, M Werkmann
From 8th International Conference on Conservative Management of Spinal Deformities and SOSORT 2011
Annual Meeting
Barcelona, Spain. 19-21 May 2011
Background
Little information exists about successful brace treatment
of progressive early onset scoliosis. Even less information
is available about the early treatment of scoliosis patients
with Marfan’s syndrome at age < 6 years. Purpose of this
case report is to demonstrate the possibility of successful
brace treatment in a patient with early onset scoliosis due
to Marfan’s syndrome [1,2].
Case report
A two year old girl diagnosed with Marfan’s syndrome
presented with a double major scoliosis of 20°. After a
follow-up of 6 months she showed a rapid progression
to 46° (November 2008) and was braced immediately.
In-brace correction in the first brace (RSC) was moder-
ate due to the stiffness mainly of the lumbar curve. A
new brace was made after significant growth (Gensingen
brace in October 2009). An in-brace correction to 12°
thoracic and 12° lumbar has been achieved. In October
2010 she also has outgrown her second brace to some
extent. Due to clinical overcorrection (ATR lumbar -5°)
brace wearing time has been reduced to 12 hrs. / day at
first. In January 2011 at the age of 4 and a half she pre-
sented again with an ATR lumbar of -6° and thoracic 2°,
lumbar still overcorrected, so we decided to leave off
the brace for 3 months time.
Conclusions
(1) Successful brace treatment in infantile / juvenile
patients with scoliosis is possible. (2) When treated dur-
ing periods of rapid growth corrections can be achieved
with high correction braces. (3) Before early surgery is
performed high quality conservative management seems
indicated.
Published: 27 January 2012
References
1. Judge DP, Dietz HC: Marfan’s syndrome. Lancet 2005, 366(9501):1965-76.
2. Savini R, Cervellati S, Beroaldo E: Spinal deformities in Marfan’s syndrome.
Ital J Orthop Traumatol 1980, 6(1):19-40.
doi:10.1186/1748-7161-7-S1-P5
Cite this article as: Weiss and Werkmann: Brace treatment in an
infantile/juvenile patient with progressive scoliosis due to Marfan’s
syndrome. Scoliosis 2012 7(Suppl 1):P5.
Submit your next manuscript to BioMed Central
and take full advantage of: 
• Convenient online submission
• Thorough peer review
• No space constraints or color figure charges
• Immediate publication on acceptance
• Inclusion in PubMed, CAS, Scopus and Google Scholar
• Research which is freely available for redistribution
Submit your manuscript at 
www.biomedcentral.com/submit
Orthopedic Rehabilitation Services, Gensingen, Germany
Weiss and Werkmann Scoliosis 2012, 7(Suppl 1):P5
http://www.scoliosisjournal.com/content/7/S1/P5
© 2012 Weiss and Werkmann; licensee BioMed Central Ltd. This is an open access article distributed under the terms of the Creative
Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and
reproduction in any medium, provided the original work is properly cited.


Crossref

POSTER PRESENTATION Open AccessBrace treatment in an infantile/juvenile patientwith progressive scoliosis due to Marfan’ssyndromeHR Weiss*, M WerkmannFrom 8th International Conference on Conservative Management of Spinal Deformities and SOSORT 2011Annual MeetingBarcelona, Spain. 19-21 May 2011BackgroundLittle information exists about successful brace treatmentof progressive early onset scoliosis. Even less informationis available about the early treatment of scoliosis patientswith Marfan’s syndrome at age < 6 years. Purpose of thiscase report is to demonstrate the possibility of successfulbrace treatment in a patient with early onset scoliosis dueto Marfan’s syndrome [1,2].Case reportA two year old girl diagnosed with Marfan’s syndromepresented with a double major scoliosis of 20°. After afollow-up of 6 months she showed a rapid progressionto 46° (November 2008) and was braced immediately.In-brace correction in the first brace (RSC) was moder-ate due to the stiffness mainly of the lumbar curve. Anew brace was made after significant growth (Gensingenbrace in October 2009). An in-brace correction to 12°thoracic and 12° lumbar has been achieved. In October2010 she also has outgrown her second brace to someextent. Due to clinical overcorrection (ATR lumbar -5°)brace wearing time has been reduced to 12 hrs. / day atfirst. In January 2011 at the age of 4 and a half she pre-sented again with an ATR lumbar of -6° and thoracic 2°,lumbar still overcorrected, so we decided to leave offthe brace for 3 months time.Conclusions(1) Successful brace treatment in infantile / juvenilepatients with scoliosis is possible. (2) When treated dur-ing periods of rapid growth corrections can be achievedwith high correction braces. (3) Before early surgery isperformed high quality conservative management seemsindicated.Published: 27 January 2012References1. Judge DP, Dietz HC: Marfan’s syndrome. Lancet 2005, 366(9501):1965-76.2. Savini R, Cervellati S, Beroaldo E: Spinal deformities in Marfan’s syndrome.Ital J Orthop Traumatol 1980, 6(1):19-40.doi:10.1186/1748-7161-7-S1-P5Cite this article as: Weiss and Werkmann: Brace treatment in aninfantile/juvenile patient with progressive scoliosis due to Marfan’ssyndrome. Scoliosis 2012 7(Suppl 1):P5.Submit your next manuscript to BioMed Centraland take full advantage of: • Convenient online submission• Thorough peer review• No space constraints or color figure charges• Immediate publication on acceptance• Inclusion in PubMed, CAS, Scopus and Google Scholar• Research which is freely available for redistributionSubmit your manuscript at www.biomedcentral.com/submitOrthopedic Rehabilitation Services, Gensingen, GermanyWeiss and Werkmann Scoliosis 2012, 7(Suppl 1):P5http://www.scoliosisjournal.com/content/7/S1/P5© 2012 Weiss and Werkmann; licensee BioMed Central Ltd. This is an open access article distributed under the terms of the CreativeCommons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, andreproduction in any medium, provided the original work is properly cited.

Scoliosis

HC: Marfan’s syndrome. Lancet

Orthop Traumatol

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Brace treatment in an infantile/juvenile patient with progressive scoliosis due to Marfan’s syndrome

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