Introduction: Doose syndrome, also known as myoclonus-astatic syndrome, is a rare form of epilepsy that usually presents in childhood and is characterized by myoclonic and drop or startled seizures, along with delayed psychomotor development. Dental management in patients with Doose syndrome requires a comprehensive approach, taking into account both the medical and psychological and social implications of the patient. This can influence the patient\u27s ability to maintain postural stability, which could increase the risk of falls or accidents during dental treatment, as well as anticonvulsant treatment, which is common in these patients, since many of these drugs can have side effects related to oral health, such as xerostomia (dry mouth), which can predispose to dental caries and oral infections. Clinical Case: a four-year-old male patient, diagnosed with Doose syndrome, presents to the pediatric dentist\u27s office with the purpose of receiving dental treatment and rehabilitation. The patient was seen after being previously referred to a neurology specialist, and a comprehensive treatment plan encompassing various strategies was implemented. This approach consisted of performing necessary surgical procedures and providing continuous follow-up for a period of 12 months, taking into account both his physical health and his psychological and social status. Thanks to this collaborative effort, the factors that could trigger seizure episodes were significantly reduced. As a result, a notable decrease in plaque accumulation was observed, the patient\u27s oral cavity remained caries-free, and he better adapted to dental visits. Conclusion: the patient\u27s rehabilitation was successful without any complications throughout the process. The procedure related to his management was subjected to further analysis, in which behavioral control measures were implemented, and was performed under local anesthesia. A notable improvement in both the patient\u27s oral and general health was observed, evidenced by the increase in his weight and height during the follow-up visit, which took place six months after the initial evaluation
