A 23-year-old Malay female patient presented with a history of pain and swelling over right maxilla. Imaging showed a well-defined unilocular radiolucency with areas of radiopacity in the right maxilla. The lesion was initially thought to be a unicystic ameloblastoma. However, histopathology of the excised lesion proved otherwise with a final diagnosis given as dentinogenic ghost cell tumour. The clinical presentation of the case, subtypes of DGCT, similarities with ameloblastoma, and treatment modalities are discussed in this paper
