Introdution. Limb-Body Wall Complex (LBWC) is a congenital defect which includes at least two of the following characteristics:
abdominal and/or thoracic body wall defects, exencephaly or encephalocoele with or without craniofacial defects
(56%) and spinal defects associated with marked vertebral or sacral defects (95%).
Case Report. We present a case report of an infant with LBWC, borned by diamniotic twin pregnancy. A prenatal ultrasound
reported an healthy fetus and a fetus with multiple malformations. At birth we found a big abdominal wall defect, absence
of scrotal sac and testicles, asymmetric chest and no major deformities in craniofacial region. At 2 hours of life, we removed
the amniotic sac, we put the stomach and the spleen in the abdominal cavity, which is virtual, and positioned a spring-loaded
silo. At 15th day of life we had complete reduction of the intestinal loops and liver and we closed the wall defect with a
prosthesis and a cryopreserved skin. The general conditions of the patient, very severe since birth, became progressively
worse and he died in the 21st day of life.
Discussion. Once the diagnosis is done the physician should offer the parents a therapeutic abortion, and above all, in case
they want to carry the pregnancy to term, we need to prepare them to the severity of the malformation and the high probability
of death