Congenital infiltrating lipomatosis of the face, first described by Beck in 1836, is a rare condition
of unknown etiology, characterized by widespread infiltration of mature fat cells in the context of tissues
softening of the face, with associated consequent bone deformities. It is presented as an isolated or associated condition
hemimegalencephaly and neurocutaneous syndromes. We describe the case of a 10-year-old patient with known lipomatosis
congenital of the face, arrived at our structure for follow up with Computed Tomography (CT) and Resonance
Magnetic (RM) .
