HEMICONVULSION-HEMIPLEGIA-EPILEPSY SYNDROME (HHE SYNDROME) (A LECTURE)

Abstract

Hemiconvulsion-hemiplegia-epilepsy syndrome (HHE syndrome) — polyetiologic disease, with onset in childhood, characterized by the triad of symptoms: 1) prolonged convulsive seizures (usually on background of fever), involving one half of the body (hemiconvulsions); 2) acute hemiparesis occurring immediately after seizures (on the side of convul­sions); 3) symptomatic focal epilepsy, occurring in the sequel. The authors discuss in detail different aspects of the disease, including etiology, pathogenesis, diagnostic approaches, differential diagnosis, and approaches to treatment (including prevention and therapy of the disease) and outcome